MONDO:0009871 |
OMIM:261990 |
Orphanet:2891 |
pili torti-developmental delay-neurological abnormalities syndrome |
MONDO:0010155 |
OMIM:275630 |
Orphanet:98907 |
Dorfman-Chanarin disease |
MONDO:0012161 |
OMIM:608957 |
Orphanet:169085 |
susceptibility to respiratory infections associated with CD8alpha chain mutation |
MONDO:0010275 |
OMIM:300232 |
Orphanet:168448 |
spondyloepimetaphyseal dysplasia, Bieganski type |
MONDO:0009192 |
OMIM:226980 |
Orphanet:1667 |
Wolcott-Rallison syndrome |
MONDO:0012248 |
OMIM:609308 |
Orphanet:86812 |
autosomal recessive limb-girdle muscular dystrophy type 2K |
MONDO:0011532 |
OMIM:605280 |
Orphanet:100994 |
hereditary spastic paraplegia 13 |
MONDO:0018794 |
OMIM:618372 |
Orphanet:477787 |
cytosolic phospholipase-A2 alpha deficiency associated bleeding disorder |
MONDO:0008959 |
OMIM:214350 |
Orphanet:1401 |
CHAND syndrome |
MONDO:0007088 |
- |
Orphanet:1020 |
Alzheimer disease type 1 |
MONDO:0010438 |
OMIM:300818 |
Orphanet:447 |
paroxysmal nocturnal hemoglobinuria 1 |
MONDO:0014124 |
OMIM:615297 |
Orphanet:974 |
Adams-Oliver syndrome 4 |
MONDO:0009514 |
OMIM:245800 |
Orphanet:2377 |
Laurence-Moon syndrome |
MONDO:0014897 |
- |
- |
obsolete portal hypertension, noncirrhotic |
MONDO:0000087 |
- |
Orphanet:35981 |
polymicrogyria |
MONDO:0034106 |
OMIM:618379 |
Orphanet:544503 |
developmental and epileptic encephalopathy, 73 |
MONDO:0010313 |
OMIM:300387 |
- |
intellectual disability, X-linked 63 |
MONDO:0013219 |
OMIM:613312 |
Orphanet:289176 |
hypophosphatemic rickets, autosomal recessive, 2 |
MONDO:0030967 |
OMIM:619196 |
- |
deafness, congenital, and adult-onset progressive leukoencephalopathy |
MONDO:0016596 |
OMIM:616809 |
Orphanet:247262 |
hyperphosphatasia-intellectual disability syndrome |
MONDO:0019349 |
OMIM:617169 |
Orphanet:821 |
Sotos syndrome |
MONDO:0013128 |
OMIM:613092 |
Orphanet:217330 |
familial juvenile hyperuricemic nephropathy type 2 |
MONDO:0019774 |
OMIM:309580 |
Orphanet:93970 |
Holmes-Gang syndrome |
MONDO:0015241 |
- |
Orphanet:1149 |
arthrogryposis-like syndrome |
MONDO:0008145 |
OMIM:166000 |
Orphanet:296 |
Ollier disease |
MONDO:0014959 |
OMIM:617184 |
- |
mitochondrial DNA depletion syndrome 12A (cardiomyopathic type), autosomal dominant |
MONDO:0020357 |
- |
Orphanet:98946 |
coloboma of eyelid |
MONDO:0014665 |
OMIM:616491 |
Orphanet:447964 |
Charcot-Marie-Tooth disease axonal type 2V |
MONDO:0009901 |
OMIM:263650 |
Orphanet:1234 |
Bartsocas-Papas syndrome |
MONDO:0015196 |
- |
Orphanet:1053 |
vein of Galen aneurysm |
MONDO:0020775 |
OMIM:618005 |
- |
congenital disorder of glycosylation with defective fucosylation 1 |
MONDO:0015469 |
OMIM:615529 |
Orphanet:1531 |
craniosynostosis |
MONDO:0014696 |
OMIM:616570 |
Orphanet:191 |
cerebrooculofacioskeletal syndrome 3 |
MONDO:0009864 |
OMIM:261650 |
Orphanet:79317 |
phosphoenolpyruvate carboxykinase deficiency, mitochondrial |
MONDO:0010916 |
OMIM:600666 |
Orphanet:730 |
polycystic kidney disease 3 with or without polycystic liver disease |
MONDO:0017174 |
- |
Orphanet:276238 |
Machado-Joseph disease type 1 |
MONDO:0009287 |
OMIM:232200 |
Orphanet:79258 |
glycogen storage disease due to glucose-6-phosphatase deficiency type IA |
MONDO:0014019 |
OMIM:615034 |
Orphanet:420485 |
dystonia 24 |
MONDO:0007774 |
OMIM:145290 |
- |
hyperreflexia |
MONDO:0018881 |
OMIM:614286 |
Orphanet:52688 |
myelodysplastic syndrome |
MONDO:0010968 |
OMIM:600975 |
Orphanet:98976 |
glaucoma 3, primary infantile, B |
MONDO:8000012 |
OMIM:616263 |
Orphanet:456312 |
neurologic, endocrine, and pancreatic disease, multisystem, infantile-onset 1 |
MONDO:0011176 |
OMIM:602014 |
Orphanet:30924 |
intestinal hypomagnesemia 1 |
MONDO:0013874 |
OMIM:614736 |
Orphanet:361 |
glucocorticoid deficiency 4 |
MONDO:0005518 |
- |
- |
pseudohermaphroditism |
MONDO:0010533 |
OMIM:301835 |
Orphanet:1187 |
Arts syndrome |
MONDO:0001008 |
- |
- |
blepharophimosis |
MONDO:0013919 |
OMIM:614847 |
- |
epilepsy, idiopathic generalized, susceptibility to, 12 |
MONDO:0012505 |
OMIM:610475 |
Orphanet:189439 |
pigmented nodular adrenocortical disease, primary, 2 |
MONDO:0009428 |
OMIM:241510 |
Orphanet:436 |
obsolete childhood hypophosphatasia |
MONDO:0015986 |
- |
Orphanet:1848 |
bilateral renal agenesis |
MONDO:0042977 |
OMIM:601606 |
Orphanet:867 |
trichoepithelioma, multiple familial, 1 |
MONDO:0011291 |
OMIM:603147 |
Orphanet:79320 |
congenital disorder of glycosylation type 1C |
MONDO:0020478 |
OMIM:500001 |
Orphanet:99718 |
Leber plus disease |
MONDO:0014660 |
OMIM:616486 |
Orphanet:2512 |
microcephaly 15, primary, autosomal recessive |
MONDO:0013425 |
OMIM:613794 |
- |
retinitis pigmentosa 20 |
MONDO:0013349 |
OMIM:613661 |
Orphanet:280071 |
ALG11-CDG |
MONDO:0013776 |
OMIM:614487 |
Orphanet:313772 |
spastic ataxia 5 |
MONDO:0044792 |
OMIM:137550 |
Orphanet:626 |
large congenital melanocytic nevus |
MONDO:0011558 |
OMIM:605472 |
Orphanet:886 |
Usher syndrome type 2C |
MONDO:0012670 |
OMIM:611451 |
- |
autosomal recessive nonsyndromic hearing loss 63 |
MONDO:0018662 |
OMIM:271630 |
Orphanet:448242 |
autosomal recessive brachyolmia |
MONDO:0014731 |
OMIM:616682 |
Orphanet:466926 |
seizures-scoliosis-macrocephaly syndrome |
MONDO:0013444 |
OMIM:613824 |
Orphanet:655 |
nephronophthisis 9 |
MONDO:0007915 |
OMIM:614420 |
Orphanet:536 |
systemic lupus erythematosus |
MONDO:0014950 |
OMIM:617168 |
- |
aortic aneurysm, familial thoracic 10 |
MONDO:0014387 |
OMIM:615889 |
- |
leukoencephalopathy, progressive, with ovarian failure |
MONDO:0018466 |
- |
- |
obsolete hereditary late onset Parkinson disease |
MONDO:0009479 |
OMIM:260450 |
Orphanet:2315 |
Johanson-Blizzard syndrome |
MONDO:0009642 |
OMIM:252100 |
Orphanet:2751 |
orofaciodigital syndrome type II |
MONDO:0032678 |
OMIM:618328 |
- |
developmental and epileptic encephalopathy, 71 |
MONDO:0007745 |
OMIM:143500 |
Orphanet:357 |
Gilbert syndrome |
MONDO:0027068 |
OMIM:500014 |
- |
mitochondrial complex 1 deficiency, mitochondrial type 1 |
MONDO:0009492 |
OMIM:245050 |
Orphanet:832 |
succinyl-CoA:3-ketoacid CoA transferase deficiency |
MONDO:0007788 |
OMIM:145750 |
- |
hypertriglyceridemia, familial |
MONDO:0014409 |
OMIM:615942 |
- |
intellectual disability, autosomal recessive 44 |
MONDO:0010355 |
OMIM:300534 |
Orphanet:85279 |
syndromic X-linked intellectual disability Claes-Jensen type |
MONDO:0012787 |
OMIM:612020 |
Orphanet:139480 |
hereditary spastic paraplegia 39 |
MONDO:0013878 |
OMIM:614742 |
Orphanet:88 |
pulmonary fibrosis and/or bone marrow failure, Telomere-related, 1 |
MONDO:0014827 |
OMIM:616907 |
Orphanet:488594 |
autosomal recessive spastic paraplegia type 76 |
MONDO:0018894 |
- |
Orphanet:53739 |
distal hereditary motor neuropathy |
MONDO:0100058 |
OMIM:618850 |
- |
hypervalinemia and hyperleucine-isoleucinemia |
MONDO:0009644 |
OMIM:252160 |
Orphanet:99732 |
sulfite oxidase deficiency due to molybdenum cofactor deficiency type B |
MONDO:0012996 |
OMIM:612718 |
Orphanet:35704 |
AGAT deficiency |
MONDO:0010480 |
OMIM:300908 |
Orphanet:466026 |
anemia, nonspherocytic hemolytic, due to G6PD deficiency |
MONDO:0011890 |
OMIM:607678 |
Orphanet:101084 |
Charcot-Marie-Tooth disease type 1D |
MONDO:0012901 |
OMIM:612423 |
Orphanet:749 |
inherited prekallikrein deficiency |
MONDO:0014140 |
OMIM:615350 |
Orphanet:588 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A14 |
MONDO:0012405 |
OMIM:610069 |
Orphanet:157794 |
polyposis syndrome, hereditary mixed, 2 |
MONDO:0016605 |
OMIM:241500 |
Orphanet:247623 |
perinatal lethal hypophosphatasia |
MONDO:0007488 |
OMIM:127750 |
Orphanet:1648 |
Lewy body dementia |
MONDO:0011257 |
OMIM:602579 |
Orphanet:79319 |
MPI-CDG |
MONDO:0018055 |
- |
Orphanet:33402 |
pediatric hepatocellular carcinoma |
MONDO:0021163 |
- |
- |
kidney neoplasm |
MONDO:0014982 |
OMIM:617238 |
- |
myopia 25, autosomal dominant |
MONDO:0032574 |
OMIM:618167 |
- |
osteochondrodysplasia, brachydactyly, and overlapping malformed digits |
MONDO:0011503 |
OMIM:604931 |
Orphanet:168588 |
cortisone reductase deficiency 1 |
MONDO:0012945 |
OMIM:612577 |
Orphanet:803 |
amyotrophic lateral sclerosis type 11 |
MONDO:0014227 |
OMIM:615522 |
Orphanet:324561 |
hypopigmentation-punctate palmoplantar keratoderma syndrome |
MONDO:0054750 |
OMIM:617892 |
- |
amyotrophic lateral sclerosis, susceptibility to, 24 |
MONDO:0032684 |
OMIM:618336 |
- |
intrauterine growth retardation, metaphyseal dysplasia, adrenal hypoplasia congenita, genital anomalies, and immunodeficiency |
MONDO:0033642 |
OMIM:619075 |
- |
neurodevelopmental disorder with alopecia and brain abnormalities |
MONDO:0019267 |
OMIM:251000 |
Orphanet:79312 |
vitamin B12-unresponsive methylmalonic acidemia type mut- |
MONDO:0017288 |
OMIM:601200 |
Orphanet:284343 |
DICER1 syndrome |
MONDO:0013722 |
OMIM:614381 |
Orphanet:88637 |
hypomyelinating leukodystrophy 8 with or without oligodontia and-or hypogonadotropic hypogonadism |
MONDO:0013661 |
OMIM:614265 |
Orphanet:289504 |
combined malonic and methylmalonic acidemia |
MONDO:0013423 |
OMIM:613791 |
Orphanet:331187 |
immunodeficiency due to MASP-2 deficiency |
MONDO:0005611 |
- |
- |
bladder transitional cell carcinoma |
MONDO:0015554 |
- |
Orphanet:158766 |
typical urticaria pigmentosa |
MONDO:0008379 |
OMIM:180105 |
- |
retinitis pigmentosa 10 |
MONDO:0014343 |
OMIM:615777 |
Orphanet:1425 |
Desbuquois dysplasia 2 |
MONDO:0012163 |
OMIM:608971 |
Orphanet:169160 |
severe combined immunodeficiency, autosomal recessive, T cell-negative, B cell-positive, NK cell-positive |
MONDO:0016316 |
- |
Orphanet:217093 |
mucopolysaccharidosis type 2, attenuated form |
MONDO:0011395 |
OMIM:604116 |
- |
cone-rod dystrophy 3 |
MONDO:0027451 |
OMIM:617403 |
Orphanet:357074 |
autosomal recessive cutis laxa type 2D |
MONDO:0013437 |
OMIM:613810 |
- |
retinitis pigmentosa 43 |
MONDO:0009274 |
OMIM:231095 |
Orphanet:1802 |
ghosal hematodiaphyseal dysplasia |
MONDO:0017054 |
OMIM:248600 |
Orphanet:268184 |
thiamine-responsive maple syrup urine disease |
MONDO:0014992 |
OMIM:617255 |
- |
lissencephaly 8 |
MONDO:0017812 |
- |
Orphanet:314662 |
segmental progressive overgrowth syndrome with fibroadipose hyperplasia |
MONDO:0009656 |
OMIM:252920 |
Orphanet:79270 |
Sanfilippo syndrome type B |
MONDO:0008416 |
OMIM:181600 |
Orphanet:384 |
palmoplantar keratoderma-sclerodactyly syndrome |
MONDO:0007400 |
OMIM:123150 |
Orphanet:1540 |
Jackson-Weiss syndrome |
MONDO:0010947 |
OMIM:600880 |
Orphanet:131 |
Budd-Chiari syndrome |
MONDO:0002281 |
- |
- |
macrocytic anemia |
MONDO:0009354 |
OMIM:236270 |
Orphanet:622 |
methylcobalamin deficiency type cblE |
MONDO:0014222 |
OMIM:615513 |
Orphanet:397596 |
immunodeficiency 14 |
MONDO:0009919 |
OMIM:264470 |
Orphanet:2971 |
peroxisomal acyl-CoA oxidase deficiency |
MONDO:0011759 |
OMIM:607015 |
Orphanet:93476 |
Hurler-Scheie syndrome |
MONDO:0009340 |
OMIM:235700 |
Orphanet:90031 |
non-spherocytic hemolytic anemia due to hexokinase deficiency |
MONDO:0044318 |
OMIM:617450 |
- |
intellectual developmental disorder with gastrointestinal difficulties and high pain threshold |
MONDO:0018852 |
OMIM:616517 |
Orphanet:49382 |
achromatopsia |
MONDO:0012872 |
OMIM:612348 |
- |
thrombophilia, familial, due to decreased release of tissue plasminogen activator |
MONDO:0027407 |
OMIM:610253 |
- |
Kleefstra syndrome 1 |
MONDO:0009291 |
OMIM:232400 |
Orphanet:366 |
glycogen storage disease III |
MONDO:0017402 |
OMIM:610193 |
Orphanet:293899 |
familial isolated arrhythmogenic ventricular dysplasia, biventricular form |
MONDO:0011234 |
OMIM:602483 |
Orphanet:137888 |
auriculocondylar syndrome 1 |
MONDO:0032653 |
OMIM:618280 |
- |
cardiac-urogenital syndrome |
MONDO:0011338 |
OMIM:603554 |
Orphanet:39041 |
Omenn syndrome |
MONDO:0010788 |
OMIM:535000 |
Orphanet:104 |
Leber hereditary optic neuropathy |
MONDO:0017268 |
- |
Orphanet:281127 |
acral self-healing collodion baby |
MONDO:0007037 |
OMIM:100800 |
Orphanet:15 |
achondroplasia |
MONDO:0000561 |
- |
Orphanet:98770 |
spinocerebellar ataxia type 16 |
MONDO:0013835 |
OMIM:614643 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type a, 7 |
MONDO:0009890 |
OMIM:263210 |
Orphanet:79328 |
Gillessen-Kaesbach-Nishimura syndrome |
MONDO:0014187 |
OMIM:615436 |
Orphanet:91387 |
aortic aneurysm, familial thoracic 8 |
MONDO:0029135 |
OMIM:618135 |
- |
muscular dystrophy-dystroglycanopathy (limb-girdle), type C, 8 |
MONDO:0014007 |
OMIM:615010 |
Orphanet:51 |
Aicardi-Goutieres syndrome 6 |
MONDO:0007908 |
OMIM:151800 |
Orphanet:2398 |
multiple symmetric lipomatosis |
MONDO:0031446 |
OMIM:607748 |
Orphanet:238475 |
hypercholanemia, familial 1 |
MONDO:0054754 |
OMIM:617900 |
- |
encephalopathy, acute, infection-induced (herpes-specific), susceptibility to, 8 |
MONDO:8000015 |
OMIM:273250 |
- |
46,XY sex reversal 11 |
MONDO:0008304 |
OMIM:176430 |
- |
premature chromatid separation trait |
MONDO:0018159 |
OMIM:615008 |
Orphanet:357008 |
atypical hemolytic-uremic syndrome with DGKE deficiency |
MONDO:0019192 |
- |
Orphanet:79085 |
AKT2-related familial partial lipodystrophy |
MONDO:0018227 |
- |
Orphanet:36412 |
hypocomplementemic urticarial vasculitis |
MONDO:0014567 |
OMIM:616281 |
Orphanet:477673 |
glutamate pyruvate transaminase 2 deficiency |
MONDO:0014976 |
OMIM:617228 |
Orphanet:478049 |
lethal left ventricular non-compaction-seizures-hypotonia-cataract-developmental delay syndrome |
MONDO:0008234 |
OMIM:171400 |
Orphanet:653 |
multiple endocrine neoplasia type 2A |
MONDO:0015010 |
OMIM:617301 |
Orphanet:289863 |
atypical glycine encephalopathy |
MONDO:0021094 |
- |
- |
immunodeficiency disease |
MONDO:0013970 |
OMIM:614923 |
Orphanet:308410 |
branched-chain keto acid dehydrogenase kinase deficiency |
MONDO:0005514 |
OMIM:615972 |
Orphanet:35612 |
nanophthalmia |
MONDO:0011905 |
- |
- |
obsolete familial hypercholanemia |
MONDO:0016575 |
OMIM:617092 |
Orphanet:244 |
primary ciliary dyskinesia |
MONDO:0100213 |
OMIM:308205 |
Orphanet:85284 |
IFAP syndrome with or without BRESHECK syndrome |
MONDO:0008814 |
OMIM:207800 |
Orphanet:90 |
hyperargininemia |
MONDO:0014349 |
OMIM:615803 |
Orphanet:411493 |
pontocerebellar hypoplasia type 10 |
MONDO:0049223 |
OMIM:301014 |
- |
osteogenesis imperfecta, type 19 |
MONDO:0016815 |
OMIM:616277 |
Orphanet:255241 |
Leigh syndrome with leukodystrophy |
MONDO:0032572 |
OMIM:618164 |
- |
cardiac, facial, and digital anomalies with developmental delay |
MONDO:0014071 |
OMIM:615181 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type a, 11 |
MONDO:0008769 |
OMIM:204500 |
Orphanet:79264 |
neuronal ceroid lipofuscinosis 2 |
MONDO:0014056 |
OMIM:615134 |
Orphanet:618 |
melanoma, cutaneous malignant, susceptibility to, 9 |
MONDO:0007744 |
OMIM:614028 |
Orphanet:79506 |
cholesterol-ester transfer protein deficiency |
MONDO:0008156 |
OMIM:166600 |
Orphanet:53 |
autosomal dominant osteopetrosis 2 |
MONDO:0014989 |
OMIM:617251 |
- |
uncombable hair syndrome 2 |
MONDO:0002974 |
OMIM:603956 |
- |
cervical cancer |
MONDO:0011143 |
OMIM:601777 |
- |
cone-rod dystrophy 6 |
MONDO:0011098 |
OMIM:601518 |
- |
prostate cancer, hereditary, 1 |
MONDO:0016809 |
OMIM:607459 |
Orphanet:254881 |
spinocerebellar ataxia with epilepsy |
MONDO:0014322 |
OMIM:615724 |
- |
premature ovarian failure 9 |
MONDO:0010940 |
OMIM:600807 |
- |
inherited susceptibility to asthma |
MONDO:0014038 |
OMIM:615083 |
- |
colorectal cancer, susceptibility to, 12 |
OMIM:145400 |
OMIM:145400 |
- |
HYPERTELORISM |
MONDO:0003669 |
OMIM:273300 |
Orphanet:842 |
testicular seminoma |
MONDO:0100224 |
OMIM:252010 |
Orphanet:2609 |
mitochondrial complex I deficiency, nuclear type 1 |
MONDO:0013290 |
OMIM:613506 |
Orphanet:33110 |
agammaglobulinemia 5, autosomal dominant |
MONDO:0019083 |
OMIM:256000 |
Orphanet:70474 |
Leigh syndrome with cardiomyopathy |
MONDO:0018177 |
OMIM:613029 |
Orphanet:360 |
glioblastoma |
MONDO:0033260 |
OMIM:617663 |
- |
hearing loss, autosomal dominant 73 |
MONDO:0016225 |
- |
Orphanet:211047 |
specific learning disability |
MONDO:0014911 |
OMIM:617093 |
Orphanet:541423 |
growth retardation, intellectual developmental disorder, hypotonia, and hepatopathy |
MONDO:0007354 |
OMIM:120430 |
Orphanet:35737 |
coloboma of optic nerve |
MONDO:0013806 |
OMIM:614564 |
Orphanet:313846 |
familial cutaneous telangiectasia and oropharyngeal predisposition cancer syndrome |
MONDO:0044625 |
- |
Orphanet:487814 |
autosomal dominant charcot-marie-tooth disease type 2 due to DGAT2 mutation |
MONDO:0044704 |
- |
Orphanet:500478 |
oropharynx squamous cell carcinoma |
MONDO:0008998 |
OMIM:216411 |
Orphanet:90324 |
Cockayne syndrome type 3 |
MONDO:0014177 |
OMIM:615420 |
- |
myopia 22, autosomal dominant |
MONDO:0054782 |
OMIM:617951 |
- |
leukodystrophy, hypomyelinating, 15 |
MONDO:0024607 |
OMIM:617404 |
- |
congenital muscular dystrophy with cataracts and intellectual disability |
MONDO:0033614 |
OMIM:619027 |
- |
spastic paraplegia 83, autosomal recessive |
MONDO:0008056 |
OMIM:160900 |
Orphanet:273 |
myotonic dystrophy type 1 |
MONDO:0008764 |
OMIM:204000 |
- |
Leber congenital amaurosis 1 |
MONDO:0009613 |
OMIM:251100 |
Orphanet:79310 |
vitamin B12-responsive methylmalonic acidemia type cblA |
MONDO:0044740 |
OMIM:275355 |
Orphanet:500481 |
salivary gland squamous cell carcinoma |
MONDO:0018507 |
- |
Orphanet:423894 |
microcephaly-complex motor and sensory axonal neuropathy syndrome |
MONDO:0008318 |
OMIM:176920 |
Orphanet:744 |
Proteus syndrome |
MONDO:0009111 |
OMIM:222748 |
Orphanet:38874 |
dihydropyrimidinuria |
MONDO:0019454 |
- |
Orphanet:86839 |
myelodysplastic syndrome with excess blasts |
MONDO:0015016 |
OMIM:617315 |
- |
anterior segment dysgenesis 6 |
MONDO:0013155 |
OMIM:613151 |
Orphanet:370959 |
muscular dystrophy-dystroglycanopathy (congenital with intellectual disability), type B3 |
MONDO:0032895 |
OMIM:618744 |
- |
developmental and epileptic encephalopathy, 83 |
MONDO:0032752 |
OMIM:618437 |
- |
developmental and epileptic encephalopathy, 75 |
MONDO:0013837 |
OMIM:614651 |
Orphanet:254898 |
deafness-encephaloneuropathy-obesity-valvulopathy syndrome |
MONDO:0019779 |
OMIM:309580 |
Orphanet:93975 |
Renier-Gabreels-Jasper syndrome |
MONDO:0014062 |
OMIM:615156 |
Orphanet:352470 |
mitochondrial DNA deletion syndrome with progressive myopathy |
MONDO:0015924 |
- |
Orphanet:182090 |
pulmonary arterial hypertension |
MONDO:0009704 |
OMIM:255110 |
Orphanet:228302 |
carnitine palmitoyl transferase II deficiency, myopathic form |
MONDO:0011436 |
OMIM:604320 |
Orphanet:98920 |
autosomal recessive distal spinal muscular atrophy 1 |
MONDO:0034121 |
OMIM:618321 |
Orphanet:555402 |
NAD(P)HX dehydratase deficiency |
MONDO:0008542 |
OMIM:187500 |
Orphanet:3303 |
tetralogy of fallot |
MONDO:0009410 |
- |
- |
obsolete Addison disease |
MONDO:0054748 |
OMIM:617883 |
- |
Fanconi anemia, complementation group S |
MONDO:0019335 |
- |
Orphanet:79651 |
mild hyperphenylalaninemia |
MONDO:0012173 |
OMIM:609016 |
Orphanet:5 |
long chain 3-hydroxyacyl-CoA dehydrogenase deficiency |
MONDO:0030893 |
OMIM:619147 |
- |
leukoencephalopathy, progressive, infantile-onset, with or without deafness |
MONDO:0010130 |
OMIM:274270 |
Orphanet:1675 |
dihydropyrimidine dehydrogenase deficiency |
MONDO:0018766 |
- |
Orphanet:468641 |
chronic enteropathy associated with SLCO2A1 gene |
MONDO:0019756 |
OMIM:610829 |
Orphanet:93924 |
lobar holoprosencephaly |
MONDO:0030037 |
OMIM:618879 |
- |
neurodevelopmental disorder with hypotonia and cerebellar atrophy, with or without seizures |
MONDO:0014613 |
OMIM:616373 |
Orphanet:2032 |
pulmonary fibrosis and/or bone marrow failure, Telomere-related, 3 |
MONDO:0060490 |
OMIM:617481 |
- |
neurodevelopmental disorder with microcephaly, hypotonia, and variable brain anomalies |
MONDO:0026782 |
- |
- |
obsolete chondrodysplasia punctata 2, X-linked dominant |
MONDO:0012926 |
OMIM:612529 |
Orphanet:100033 |
amelogenesis imperfecta hypomaturation type 2A2 |
MONDO:0013165 |
OMIM:613162 |
Orphanet:320396 |
hereditary spastic paraplegia 45 |
MONDO:0011604 |
OMIM:605822 |
Orphanet:85194 |
spondylo-ocular syndrome |
MONDO:0009696 |
OMIM:614280 |
Orphanet:307 |
juvenile myoclonic epilepsy |
MONDO:0006065 |
OMIM:223100 |
Orphanet:319681 |
lactose intolerance adult type |
MONDO:0024566 |
OMIM:614418 |
Orphanet:165805 |
febrile seizures, familial, 11 |
OMIM:619311 |
OMIM:619311 |
- |
HIATT-NEU-COOPER NEURODEVELOPMENTAL SYNDROME |
MONDO:0015780 |
OMIM:616353 |
Orphanet:1775 |
dyskeratosis congenita |
MONDO:0018655 |
OMIM:607694 |
Orphanet:447893 |
hypomyelination-cerebellar atrophy-hypoplasia of the corpus callosum syndrome |
MONDO:0011240 |
OMIM:602501 |
Orphanet:60040 |
megalencephaly-capillary malformation-polymicrogyria syndrome |
MONDO:0009657 |
OMIM:252930 |
Orphanet:79271 |
Sanfilippo syndrome type C |
MONDO:0008723 |
OMIM:201475 |
Orphanet:26793 |
very long chain acyl-CoA dehydrogenase deficiency |
MONDO:0003789 |
OMIM:605074 |
Orphanet:47044 |
hereditary papillary renal cell carcinoma |
MONDO:0012582 |
OMIM:610921 |
Orphanet:440402 |
interstitial lung disease due to ABCA3 deficiency |
MONDO:0013400 |
OMIM:613743 |
Orphanet:168558 |
Congenital adrenal insuffiency with 46, XY sex reversal OR 46,XY disorder of sex development-adrenal insufficiency due to CYP11A1 deficiency |
MONDO:0009711 |
OMIM:300580 |
Orphanet:2020 |
congenital fiber-type disproportion myopathy |
MONDO:0014039 |
OMIM:615084 |
Orphanet:352447 |
mitochondrial DNA depletion syndrome 11 |
MONDO:0012115 |
OMIM:608765 |
- |
scoliosis, isolated, susceptibility to, 3 |
MONDO:0033549 |
OMIM:618977 |
- |
optic atrophy 12 |
MONDO:0008345 |
OMIM:616373 |
Orphanet:79126 |
idiopathic pulmonary fibrosis |
MONDO:0014966 |
OMIM:617201 |
- |
periventricular nodular heterotopia 7 |
MONDO:0011452 |
OMIM:604379 |
Orphanet:55654 |
hypotrichosis 7 |
MONDO:0009050 |
OMIM:219090 |
Orphanet:96253 |
Cushing disease due to pituitary adenoma |
MONDO:0014716 |
OMIM:616638 |
Orphanet:457485 |
macrocephaly-intellectual disability-neurodevelopmental disorder-small thorax syndrome |
MONDO:0032882 |
OMIM:618724 |
- |
Heyn-Sproul-Jackson syndrome |
MONDO:0009694 |
OMIM:254600 |
Orphanet:2587 |
myeloperoxidase deficiency |
MONDO:0030894 |
OMIM:619151 |
- |
AMED syndrome, digenic |
MONDO:0014651 |
OMIM:616462 |
- |
acrofacial dysostosis Cincinnati type |
MONDO:0016203 |
- |
Orphanet:209902 |
hypercholesterolemia due to cholesterol 7alpha-hydroxylase deficiency |
MONDO:0010046 |
OMIM:270750 |
Orphanet:101003 |
hereditary spastic paraplegia 23 |
MONDO:0008244 |
OMIM:172800 |
Orphanet:2884 |
piebaldism |
MONDO:0013154 |
OMIM:613150 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A2 |
MONDO:0013904 |
OMIM:614830 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type a, 8 |
MONDO:0016995 |
OMIM:607174 |
Orphanet:263662 |
familial multiple meningioma |
MONDO:0012187 |
OMIM:609054 |
- |
Fanconi anemia complementation group J |
MONDO:0013611 |
OMIM:614181 |
- |
retinitis pigmentosa 62 |
MONDO:0009897 |
OMIM:263570 |
Orphanet:206583 |
adult polyglucosan body disease |
MONDO:0044647 |
OMIM:617114 |
Orphanet:496686 |
kyphosis-lateral tongue atrophy-myofibrillar myopathy syndrome |
MONDO:0018137 |
OMIM:606952 |
Orphanet:352737 |
temperature-sensitive oculocutaneous albinism type 1 |
MONDO:0009294 |
OMIM:232700 |
Orphanet:369 |
glycogen storage disease VI |
MONDO:0014739 |
OMIM:616705 |
- |
autosomal recessive nonsyndromic hearing loss 97 |
MONDO:0011764 |
OMIM:607060 |
Orphanet:411602 |
autosomal dominant Parkinson disease 8 |
MONDO:0054838 |
OMIM:618052 |
- |
cardiomyopathy, familial hypertrophic 27 |
MONDO:0005155 |
OMIM:215600 |
- |
cirrhosis of liver |
MONDO:0011624 |
OMIM:606003 |
Orphanet:101028 |
transaldolase deficiency |
MONDO:0015446 |
- |
Orphanet:1456 |
atypical coarctation of aorta |
MONDO:0014506 |
OMIM:616140 |
Orphanet:438114 |
hypomyelinating leukodystrophy 9 |
MONDO:0014713 |
OMIM:616631 |
- |
porokeratosis 9, multiple types |
MONDO:0013845 |
OMIM:614669 |
Orphanet:137888 |
auriculocondylar syndrome 2 |
MONDO:0010886 |
OMIM:600430 |
Orphanet:1001 |
2q37 microdeletion syndrome |
MONDO:0054698 |
OMIM:256040 |
- |
proteasome-associated autoinflammatory syndrome 1 |
MONDO:0030025 |
OMIM:618862 |
- |
neurodevelopmental disorder with hypotonia, microcephaly, and seizures |
MONDO:0018874 |
OMIM:601626 |
Orphanet:519 |
acute myeloid leukemia |
MONDO:0019259 |
- |
Orphanet:79254 |
classic phenylketonuria |
MONDO:0013118 |
OMIM:613078 |
Orphanet:240760 |
Nijmegen breakage syndrome-like disorder |
MONDO:0009809 |
OMIM:259600 |
- |
multicentric osteolysis, nodulosis, and arthropathy |
MONDO:0014271 |
OMIM:615597 |
Orphanet:370924 |
STT3B-CDG |
MONDO:0020678 |
- |
- |
sensorineural hearing loss disorder |
MONDO:0012427 |
OMIM:610168 |
Orphanet:91387 |
Loeys-Dietz syndrome 2 |
MONDO:0007664 |
OMIM:137750 |
Orphanet:98977 |
glaucoma 1, open angle, A |
MONDO:0011971 |
OMIM:608106 |
Orphanet:183666 |
hyper-IgM syndrome type 5 |
MONDO:0015461 |
- |
Orphanet:1505 |
short rib-polydactyly syndrome |
MONDO:0014853 |
OMIM:616968 |
- |
autosomal dominant nonsyndromic hearing loss 70 |
MONDO:0013601 |
OMIM:614164 |
- |
gluthathione peroxidase deficiency |
MONDO:0010561 |
OMIM:303600 |
Orphanet:192 |
Coffin-Lowry syndrome |
MONDO:0018998 |
OMIM:615360 |
Orphanet:65 |
Leber congenital amaurosis |
MONDO:0012890 |
OMIM:612389 |
Orphanet:2524 |
pontocerebellar hypoplasia type 2B |
MONDO:0013501 |
OMIM:613954 |
Orphanet:803 |
frontotemporal dementia and/or amyotrophic lateral sclerosis 6 |
MONDO:0018821 |
- |
Orphanet:480880 |
X-linked female restricted facial dysmorphism-short stature-choanal atresia-intellectual disability |
MONDO:0014270 |
OMIM:615596 |
Orphanet:370921 |
STT3A-CDG |
MONDO:0011405 |
OMIM:604173 |
Orphanet:221046 |
poikiloderma with neutropenia |
MONDO:0013123 |
OMIM:613087 |
Orphanet:1478 |
atrial septal defect 6 |
MONDO:0015293 |
- |
Orphanet:137608 |
segmental outgrowth-lipomatosis-arteriovenous malformation-epidermal nevus syndrome |
MONDO:0029137 |
OMIM:618140 |
- |
hearing loss, autosomal dominant 74 |
MONDO:0004946 |
- |
- |
hypoglycemia |
MONDO:0009254 |
OMIM:230000 |
Orphanet:349 |
fucosidosis |
MONDO:0007565 |
OMIM:132700 |
Orphanet:79493 |
familial cylindromatosis |
MONDO:0010506 |
OMIM:300978 |
- |
intellectual disability, X-linked 61 |
MONDO:0005406 |
- |
- |
gestational diabetes |
MONDO:0021427 |
OMIM:275355 |
Orphanet:502366 |
squamous cell carcinoma of lip |
MONDO:0005835 |
OMIM:614385 |
Orphanet:144 |
Lynch syndrome |
MONDO:0018309 |
OMIM:613712 |
Orphanet:388 |
Hirschsprung disease |
MONDO:0011760 |
OMIM:607016 |
Orphanet:93474 |
Scheie syndrome |
MONDO:0032828 |
OMIM:618598 |
- |
spastic tetraplegia and axial hypotonia, progressive |
MONDO:0007103 |
OMIM:105400 |
Orphanet:803 |
amyotrophic lateral sclerosis type 1 |
MONDO:0009443 |
OMIM:242500 |
Orphanet:457 |
autosomal recessive congenital ichthyosis 4B |
MONDO:0008265 |
OMIM:617004 |
Orphanet:2924 |
polycystic liver disease 1 |
MONDO:0013699 |
OMIM:614337 |
Orphanet:144 |
colorectal cancer, hereditary nonpolyposis, type 4 |
MONDO:0009112 |
OMIM:222765 |
Orphanet:309796 |
rhizomelic chondrodysplasia punctata type 2 |
MONDO:0008031 |
OMIM:158901 |
Orphanet:269 |
facioscapulohumeral muscular dystrophy 2 |
MONDO:0017722 |
OMIM:268800 |
Orphanet:309162 |
Sandhoff disease, juvenile form |
MONDO:0032771 |
OMIM:618475 |
- |
paragangliomas 7 |
MONDO:0032790 |
OMIM:618505 |
- |
neurodevelopmental disorder with coarse facies and mild distal skeletal abnormalities |
MONDO:0007295 |
OMIM:245570 |
Orphanet:1945 |
childhood epilepsy with centrotemporal spikes |
MONDO:0010122 |
OMIM:274150 |
Orphanet:93583 |
congenital thrombotic thrombocytopenic purpura |
MONDO:0008328 |
OMIM:177700 |
- |
glaucoma 1, open angle, P |
MONDO:0011006 |
OMIM:601162 |
Orphanet:447753 |
hereditary spastic paraplegia 9A |
MONDO:0016244 |
OMIM:615008 |
Orphanet:2134 |
atypical hemolytic-uremic syndrome |
MONDO:0014658 |
OMIM:616482 |
Orphanet:85165 |
severe achondroplasia-developmental delay-acanthosis nigricans syndrome |
MONDO:0019177 |
OMIM:607694 |
Orphanet:77295 |
odontoleukodystrophy |
MONDO:0013670 |
OMIM:614292 |
Orphanet:98619 |
myopia, high, with cataract and vitreoretinal degeneration |
MONDO:0009664 |
OMIM:253250 |
Orphanet:2576 |
mulibrey nanism |
MONDO:0007211 |
OMIM:112410 |
Orphanet:1276 |
brachydactyly-arterial hypertension syndrome |
MONDO:0013291 |
OMIM:613507 |
Orphanet:263297 |
glycogen storage disease XV |
MONDO:0014898 |
OMIM:617069 |
- |
progressive external ophthalmoplegia with mitochondrial DNA deletions, autosomal recessive 3 |
MONDO:0018698 |
- |
Orphanet:456333 |
hereditary neuroendocrine tumor of small intestine |
MONDO:0018037 |
- |
Orphanet:331223 |
hyper-IgE syndrome |
MONDO:0009370 |
OMIM:236792 |
Orphanet:79314 |
L-2-hydroxyglutaric aciduria |
MONDO:0010215 |
OMIM:278760 |
Orphanet:910 |
xeroderma pigmentosum group F |
MONDO:0012999 |
OMIM:612736 |
Orphanet:382 |
guanidinoacetate methyltransferase deficiency |
MONDO:0008922 |
OMIM:615418 |
Orphanet:1369 |
Sengers syndrome |
MONDO:0013002 |
OMIM:612775 |
- |
cone-rod dystrophy 9 |
MONDO:0009746 |
OMIM:256800 |
Orphanet:642 |
hereditary sensory and autonomic neuropathy type 4 |
MONDO:0008887 |
OMIM:211400 |
Orphanet:60033 |
bronchiectasis with or without elevated sweat chloride 1 |
MONDO:0008410 |
OMIM:181440 |
Orphanet:3135 |
Scheuermann disease |
MONDO:0030046 |
OMIM:618890 |
- |
neurodevelopmental disorder and structural brain anomalies with or without seizures and spasticity |
MONDO:0011803 |
OMIM:607259 |
Orphanet:99013 |
hereditary spastic paraplegia 7 |
MONDO:0011789 |
OMIM:607174 |
Orphanet:263662 |
familial meningioma |
MONDO:0007048 |
OMIM:101900 |
Orphanet:79151 |
acrokeratosis verruciformis |
MONDO:0010396 |
OMIM:300672 |
Orphanet:505652 |
developmental and epileptic encephalopathy, 2 |
MONDO:0044776 |
OMIM:612885 |
- |
premature ovarian failure 10 |
MONDO:0017697 |
OMIM:232500 |
Orphanet:308655 |
glycogen storage disease due to glycogen branching enzyme deficiency, fatal perinatal neuromuscular form |
MONDO:0030029 |
OMIM:618870 |
- |
skeletal dysplasia, mild, with joint laxity and advanced bone age |
MONDO:0014527 |
OMIM:616200 |
Orphanet:435953 |
progeroid features-hepatocellular carcinoma predisposition syndrome |
MONDO:0014866 |
OMIM:617017 |
Orphanet:443950 |
Charcot-Marie-Tooth disease axonal type 2T |
MONDO:0009678 |
OMIM:253800 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A, 4 |
MONDO:0016393 |
OMIM:603457 |
Orphanet:2250 |
hyposmia-nasal and ocular hypoplasia-hypogonadotropic hypogonadism syndrome |
MONDO:0019456 |
OMIM:601626 |
Orphanet:86845 |
acute myeloid leukemia with multilineage dysplasia |
MONDO:0014196 |
OMIM:615465 |
Orphanet:2117 |
Hartsfield-Bixler-Demyer syndrome |
MONDO:0033557 |
OMIM:618998 |
- |
hemophagocytic lymphohistiocytosis, familial, 6 |
MONDO:0011429 |
OMIM:604302 |
Orphanet:92 |
juvenile idiopathic arthritis |
MONDO:0002529 |
- |
- |
skin squamous cell carcinoma |
MONDO:0011053 |
OMIM:601358 |
Orphanet:3051 |
intellectual disability-sparse hair-brachydactyly syndrome |
MONDO:0014331 |
OMIM:615750 |
Orphanet:401945 |
Moyamoya disease with early-onset achalasia |
MONDO:0011383 |
OMIM:603909 |
Orphanet:3261 |
autoimmune lymphoproliferative syndrome type 2A |
MONDO:0013047 |
OMIM:612933 |
Orphanet:284426 |
glycogen storage disease due to lactate dehydrogenase M-subunit deficiency |
MONDO:0016293 |
OMIM:616389 |
Orphanet:215 |
congenital stationary night blindness |
MONDO:0013389 |
OMIM:613722 |
Orphanet:3451 |
developmental and epileptic encephalopathy, 12 |
MONDO:0019661 |
- |
Orphanet:93260 |
Pfeiffer syndrome type 3 |
MONDO:0007719 |
OMIM:142340 |
Orphanet:2140 |
diaphragmatic hernia, congenital 1 |
MONDO:0016215 |
OMIM:617008 |
Orphanet:210141 |
spastic quadriplegic cerebral palsy |
MONDO:0010787 |
OMIM:530000 |
Orphanet:480 |
Kearns-Sayre syndrome |
MONDO:0014194 |
OMIM:615453 |
Orphanet:1460 |
mitochondrial complex III deficiency nuclear type 6 |
MONDO:0007962 |
OMIM:155500 |
- |
Megalodactyly |
MONDO:0033008 |
OMIM:617730 |
Orphanet:2065 |
Galloway-Mowat syndrome 4 |
MONDO:0010060 |
OMIM:271245 |
Orphanet:1186 |
infantile onset spinocerebellar ataxia |
MONDO:0017102 |
OMIM:607341 |
Orphanet:269008 |
isolated focal cortical dysplasia type IIb |
MONDO:0010923 |
OMIM:600706 |
Orphanet:521305 |
proximal myopathy with focal depletion of mitochondria |
MONDO:0013058 |
OMIM:612951 |
Orphanet:85136 |
cystic leukoencephalopathy without megalencephaly |
MONDO:0018908 |
OMIM:605027 |
Orphanet:547 |
non-Hodgkin lymphoma |
MONDO:0009249 |
OMIM:229600 |
Orphanet:469 |
hereditary fructose intolerance |
MONDO:0013111 |
OMIM:613070 |
Orphanet:217371 |
acute infantile liver failure due to synthesis defect of mtDNA-encoded proteins |
MONDO:0020741 |
OMIM:266100 |
Orphanet:3006 |
pyridoxine-dependent epilepsy caused by ALDH7A1 mutant |
MONDO:0014993 |
OMIM:617258 |
- |
myofibrillar myopathy 8 |
MONDO:0017972 |
- |
Orphanet:325524 |
classic congenital lipoid adrenal hyperplasia due to STAR deficency |
MONDO:0014195 |
OMIM:615458 |
Orphanet:369970 |
microcornea-myopic chorioretinal atrophy |
MONDO:0033558 |
OMIM:618999 |
- |
autoinflammation, immune dysregulation, and eosinophilia |
MONDO:0060562 |
OMIM:617668 |
- |
encephalopathy, neonatal severe, with lactic acidosis and brain abnormalities |
MONDO:0010842 |
OMIM:600195 |
Orphanet:2451 |
multiple cutaneous and mucosal venous malformations |
MONDO:0020164 |
- |
Orphanet:98573 |
epicanthal fold |
MONDO:0018393 |
OMIM:616950 |
Orphanet:399805 |
male infertility with azoospermia or oligozoospermia due to single gene mutation |
MONDO:0017398 |
OMIM:265050 |
Orphanet:293843 |
3MC syndrome |
MONDO:0009491 |
OMIM:245010 |
Orphanet:2342 |
Haim-Munk syndrome |
MONDO:0014764 |
OMIM:616756 |
Orphanet:464282 |
spastic paraplegia-severe developmental delay-epilepsy syndrome |
MONDO:0014639 |
OMIM:616436 |
Orphanet:101046 |
familial temporal lobe epilepsy 7 |
MONDO:0008006 |
OMIM:157900 |
Orphanet:570 |
Mobius syndrome |
MONDO:0032868 |
OMIM:618681 |
- |
lessel-kubisch syndrome |
MONDO:0014526 |
OMIM:616199 |
Orphanet:456369 |
polyglucosan body myopathy type 2 |
MONDO:0012212 |
OMIM:609192 |
Orphanet:97295 |
Loeys-Dietz syndrome 1 |
MONDO:0011774 |
OMIM:607101 |
Orphanet:90636 |
autosomal recessive nonsyndromic hearing loss 30 |
MONDO:0009955 |
OMIM:266280 |
Orphanet:3021 |
rapadilino syndrome |
MONDO:0012699 |
OMIM:611588 |
Orphanet:206554 |
autosomal recessive limb-girdle muscular dystrophy type 2M |
MONDO:0007790 |
OMIM:145900 |
Orphanet:64748 |
Charcot-Marie-Tooth disease type 3 |
MONDO:0013753 |
OMIM:614436 |
Orphanet:99941 |
Charcot-Marie-Tooth disease axonal type 2P |
MONDO:0020354 |
OMIM:120200 |
Orphanet:98942 |
coloboma of choroid and retina |
MONDO:0029144 |
OMIM:618148 |
- |
extraoral halitosis due to methanethiol oxidase deficiency |
MONDO:0015601 |
OMIM:301030 |
Orphanet:163976 |
X-linked intellectual disability, van Esch type |
MONDO:0014761 |
OMIM:616744 |
Orphanet:476102 |
hereditary pediatric Behçet-like disease |
MONDO:0016091 |
- |
Orphanet:206448 |
adult Krabbe disease |
MONDO:0019778 |
OMIM:309580 |
Orphanet:93974 |
Smith-Fineman-Myers syndrome |
MONDO:0020739 |
OMIM:143880 |
Orphanet:300547 |
hypercalcemia, infantile, 1 |
MONDO:0016308 |
- |
Orphanet:216978 |
Niemann-Pick disease type C, late infantile neurologic onset |
MONDO:0011837 |
OMIM:607473 |
- |
vitamin K-dependent clotting factors, combined deficiency of, type 2 |
MONDO:0020511 |
OMIM:615545 |
Orphanet:99860 |
precursor B-cell acute lymphoblastic leukemia |
MONDO:0030858 |
OMIM:619126 |
- |
immunodeficiency 75 |
MONDO:0011686 |
OMIM:606593 |
Orphanet:99812 |
DNA ligase IV deficiency |
MONDO:0013060 |
OMIM:612953 |
Orphanet:199351 |
autosomal recessive Parkinson disease 14 |
MONDO:0013419 |
OMIM:613783 |
Orphanet:169147 |
complement component C1s deficiency |
MONDO:0014798 |
OMIM:616849 |
- |
brachydactyly type A1D |
MONDO:0009278 |
- |
- |
obsolete hyperinsulinism due to short chain 3-hydroxylacyl-CoA dehydrogenase deficiency |
MONDO:0009650 |
OMIM:252500 |
Orphanet:576 |
mucolipidosis type II |
MONDO:0019505 |
OMIM:616494 |
Orphanet:88637 |
hypomyelination-hypogonadotropic hypogonadism-hypodontia syndrome |
MONDO:0013794 |
OMIM:614521 |
Orphanet:71493 |
thrombocythemia 3 |
MONDO:0054588 |
OMIM:617506 |
- |
Noonan syndrome-like disorder with loose anagen hair 2 |
MONDO:0009549 |
OMIM:248200 |
Orphanet:827 |
severe early-childhood-onset retinal dystrophy |
MONDO:0009606 |
OMIM:250800 |
Orphanet:621 |
methemoglobinemia due to deficiency of methemoglobin reductase |
MONDO:0100186 |
OMIM:233910 |
Orphanet:238583 |
GTP cyclohydrolase I deficiency with hyperphenylalaninemia |
MONDO:0010622 |
OMIM:308100 |
Orphanet:461 |
recessive X-linked ichthyosis |
MONDO:0018320 |
OMIM:616817 |
Orphanet:391408 |
primary microcephaly-mild intellectual disability-young-onset diabetes syndrome |
MONDO:0007829 |
OMIM:147480 |
Orphanet:69665 |
cholestasis, intrahepatic, of pregnancy, 1 |
MONDO:0010089 |
OMIM:272300 |
Orphanet:99731 |
isolated sulfite oxidase deficiency |
MONDO:0021020 |
OMIM:218800 |
Orphanet:79234 |
Crigler-Najjar syndrome type 1 |
MONDO:0009723 |
OMIM:256000 |
Orphanet:506 |
Leigh syndrome |
MONDO:0015558 |
- |
Orphanet:158778 |
isolated bone marrow mastocytosis |
MONDO:0012648 |
OMIM:611283 |
Orphanet:79159 |
isobutyryl-CoA dehydrogenase deficiency |
MONDO:0018279 |
OMIM:613152 |
Orphanet:370980 |
congenital muscular dystrophy without intellectual disability |
MONDO:0014603 |
OMIM:616357 |
- |
autosomal dominant nonsyndromic hearing loss 40 |
MONDO:0014504 |
OMIM:616138 |
Orphanet:2855 |
Perrault syndrome 5 |
MONDO:0004948 |
OMIM:612559 |
Orphanet:67038 |
B-cell chronic lymphocytic leukemia |
MONDO:0032806 |
OMIM:618546 |
- |
trichothiodystrophy 7, nonphotosensitive |
MONDO:0014353 |
OMIM:615816 |
Orphanet:443811 |
immunodeficiency 23 |
MONDO:0007574 |
OMIM:133190 |
Orphanet:1955 |
spinocerebellar ataxia type 34 |
MONDO:0006292 |
OMIM:156240 |
Orphanet:50251 |
malignant mesothelioma |
MONDO:0010358 |
OMIM:300554 |
- |
hypophosphatemic rickets, X-linked recessive |
MONDO:0011014 |
OMIM:601200 |
Orphanet:64742 |
pleuropulmonary blastoma |
MONDO:0012585 |
OMIM:610938 |
- |
coronary heart disease, susceptibility to, 7 |
MONDO:0018349 |
- |
Orphanet:397941 |
MAN1B1-CDG |
MONDO:0013842 |
OMIM:614662 |
Orphanet:168588 |
cortisone reductase deficiency 2 |
MONDO:0013660 |
OMIM:614262 |
- |
arthrogryposis, Perthes disease, and upward gaze palsy |
MONDO:0019346 |
OMIM:256550 |
Orphanet:812 |
sialidosis type 1 |
MONDO:0014564 |
OMIM:616278 |
- |
congenital bile acid synthesis defect 5 |
MONDO:0012953 |
OMIM:612591 |
- |
colorectal cancer, susceptibility to, 10 |
MONDO:0011275 |
OMIM:602875 |
Orphanet:40 |
acromesomelic dysplasia 1, Maroteaux type |
MONDO:0013212 |
OMIM:613287 |
Orphanet:228174 |
Charcot-Marie-Tooth disease axonal type 2N |
MONDO:0011246 |
OMIM:602541 |
Orphanet:280671 |
megaconial type congenital muscular dystrophy |
MONDO:0012138 |
OMIM:608840 |
Orphanet:98894 |
muscular dystrophy-dystroglycanopathy type B6 |
MONDO:0008586 |
OMIM:189960 |
Orphanet:1199 |
esophageal atresia/tracheoesophageal fistula |
MONDO:0014088 |
OMIM:615224 |
Orphanet:164736 |
advanced sleep phase syndrome 2 |
MONDO:0012217 |
OMIM:609220 |
Orphanet:2771 |
Bruck syndrome 2 |
MONDO:0012120 |
OMIM:608782 |
Orphanet:79246 |
pyruvate dehydrogenase phosphatase deficiency |
MONDO:0009293 |
OMIM:232600 |
Orphanet:368 |
glycogen storage disease V |
MONDO:0013995 |
OMIM:614972 |
Orphanet:69665 |
cholestasis, intrahepatic, of pregnancy, 3 |
MONDO:0016392 |
OMIM:213000 |
Orphanet:2246 |
cerebellar hypoplasia-tapetoretinal degeneration syndrome |
MONDO:0011217 |
OMIM:602398 |
Orphanet:35107 |
desmosterolosis |
MONDO:0100255 |
OMIM:614300 |
Orphanet:289290 |
adenosine kinase deficiency |
MONDO:0011631 |
OMIM:606069 |
Orphanet:139491 |
hemochromatosis type 4 |
MONDO:0014143 |
OMIM:615355 |
Orphanet:648 |
Noonan syndrome 8 |
MONDO:0015517 |
OMIM:616576 |
Orphanet:1572 |
common variable immunodeficiency |
MONDO:0020246 |
- |
Orphanet:98668 |
inherited vitreoretinopathy |
MONDO:0012233 |
OMIM:609265 |
Orphanet:524 |
Li-Fraumeni syndrome 2 |
MONDO:0009683 |
OMIM:254110 |
Orphanet:1878 |
autosomal recessive limb-girdle muscular dystrophy type 2H |
MONDO:0013254 |
OMIM:613402 |
Orphanet:228418 |
microcephaly, seizures, and developmental delay |
MONDO:0032609 |
OMIM:618225 |
- |
mitochondrial complex 1 deficiency, nuclear type 4 |
MONDO:0007496 |
OMIM:128235 |
Orphanet:71517 |
dystonia 12 |
MONDO:0010671 |
OMIM:309800 |
Orphanet:85275 |
microphthalmia, syndromic 1 |
MONDO:0013821 |
OMIM:614609 |
Orphanet:1465 |
intellectual disability, autosomal dominant 16 |
MONDO:0015278 |
OMIM:614320 |
Orphanet:1333 |
familial pancreatic carcinoma |
MONDO:0010107 |
- |
- |
obsolete testicular regression syndrome |
MONDO:0016601 |
- |
Orphanet:247573 |
adult-onset citrullinemia type I |
MONDO:0044319 |
OMIM:617452 |
Orphanet:505237 |
intellectual developmental disorder with dysmorphic facies, seizures, and distal limb anomalies |
MONDO:0019775 |
OMIM:309580 |
Orphanet:93971 |
Chudley-Lowry-Hoar syndrome |
MONDO:0008559 |
OMIM:188050 |
- |
thrombophilia due to thrombin defect |
MONDO:0010029 |
OMIM:270100 |
Orphanet:450 |
situs inversus |
MONDO:0011551 |
OMIM:605407 |
Orphanet:101150 |
TH-deficient dopa-responsive dystonia |
MONDO:0010655 |
OMIM:309520 |
Orphanet:776 |
X-linked intellectual disability with marfanoid habitus |
MONDO:0005387 |
- |
Orphanet:619 |
primary ovarian failure |
MONDO:0005335 |
OMIM:114500 |
- |
colorectal neoplasm |
MONDO:0008661 |
OMIM:193200 |
Orphanet:247871 |
vitiligo |
MONDO:0016692 |
- |
Orphanet:251615 |
pilomyxoid astrocytoma |
MONDO:0014228 |
OMIM:615523 |
Orphanet:98974 |
corneal dystrophy, Fuchs endothelial, 8 |
MONDO:0007723 |
OMIM:142623 |
Orphanet:388 |
Hirschsprung disease, susceptibility to, 1 |
MONDO:0013900 |
OMIM:614820 |
Orphanet:2131 |
alternating hemiplegia of childhood 2 |
MONDO:0033643 |
OMIM:619079 |
- |
inflammatory bowel disease 30 |
MONDO:0015009 |
OMIM:617300 |
- |
lymphatic malformation 7 |
MONDO:0035124 |
- |
Orphanet:589608 |
linear hypopigmentation and craniofacial asymmetry with acral, ocular and brain anomalies |
MONDO:0030856 |
OMIM:619124 |
- |
developmental and epileptic encephalopathy 89 |
MONDO:0010907 |
OMIM:600627 |
Orphanet:2224 |
familial hypertryptophanemia |
MONDO:0032600 |
OMIM:618205 |
- |
Snijders Blok-Campeau syndrome |
MONDO:0014895 |
OMIM:617065 |
- |
developmental and epileptic encephalopathy, 40 |
MONDO:0013825 |
OMIM:614616 |
Orphanet:314373 |
congenital diarrhea 6 |
MONDO:0009064 |
OMIM:219750 |
Orphanet:411641 |
ocular cystinosis |
MONDO:0012792 |
OMIM:612075 |
Orphanet:298 |
mitochondrial DNA depletion syndrome 8a |
MONDO:0014334 |
OMIM:615758 |
Orphanet:280142 |
severe combined immunodeficiency due to LCK deficiency |
MONDO:0017700 |
OMIM:232500 |
Orphanet:308698 |
glycogen storage disease due to glycogen branching enzyme deficiency, childhood neuromuscular form |
MONDO:0008226 |
OMIM:608526 |
- |
periodontitis, aggressive 1 |
MONDO:0015556 |
- |
Orphanet:158772 |
nodular urticaria pigmentosa |
MONDO:0014348 |
OMIM:615802 |
- |
intellectual disability, autosomal recessive 42 |
MONDO:0017571 |
OMIM:158350 |
Orphanet:2969 |
Proteus-like syndrome |
MONDO:0014417 |
OMIM:615957 |
Orphanet:423296 |
spinocerebellar ataxia type 38 |
MONDO:0005029 |
OMIM:614521 |
Orphanet:71493 |
essential thrombocythemia |
MONDO:0009439 |
OMIM:242100 |
Orphanet:79394 |
autosomal recessive congenital ichthyosis 2 |
MONDO:0044638 |
- |
Orphanet:494547 |
hypopharynx squamous cell carcinoma |
MONDO:0044302 |
OMIM:617360 |
- |
congenital heart defects, dysmorphic facial features, and intellectual developmental disorder |
MONDO:0007806 |
OMIM:146550 |
Orphanet:444 |
hypotrichosis 4 |
MONDO:0015447 |
OMIM:607464 |
Orphanet:146 |
differentiated thyroid carcinoma |
MONDO:0009958 |
OMIM:600964 |
Orphanet:773 |
adult Refsum disease |
MONDO:0017193 |
- |
Orphanet:276630 |
symptomatic form of Coffin-Lowry syndrome in female carriers |
MONDO:0013529 |
OMIM:614021 |
Orphanet:3286 |
catecholaminergic polymorphic ventricular tachycardia 3 |
MONDO:0029131 |
OMIM:618124 |
- |
peripheral neuropathy, autosomal recessive, with or without impaired intellectual development |
MONDO:0007606 |
OMIM:135100 |
Orphanet:337 |
fibrodysplasia ossificans progressiva |
MONDO:0011962 |
OMIM:608089 |
- |
endometrial cancer |
MONDO:0014207 |
OMIM:615489 |
- |
age related macular degeneration 14 |
MONDO:0014389 |
OMIM:615895 |
Orphanet:397937 |
polyglucosan body myopathy 1 with or without immunodeficiency |
MONDO:0008727 |
OMIM:201810 |
Orphanet:90791 |
congenital adrenal hyperplasia due to 3-beta-hydroxysteroid dehydrogenase deficiency |
MONDO:0010031 |
OMIM:270200 |
Orphanet:816 |
Sjogren-Larsson syndrome |
MONDO:0010600 |
OMIM:306400 |
Orphanet:379 |
granulomatous disease, chronic, X-linked |
MONDO:0009387 |
OMIM:238600 |
Orphanet:309015 |
familial lipoprotein lipase deficiency |
MONDO:0009502 |
OMIM:245348 |
Orphanet:79244 |
pyruvate dehydrogenase E2 deficiency |
MONDO:0044640 |
OMIM:617017 |
Orphanet:495274 |
charcot-marie-tooth disease type 2T |
MONDO:0014856 |
OMIM:616974 |
Orphanet:478042 |
combined oxidative phosphorylation defect type 30 |
MONDO:0008729 |
OMIM:202010 |
Orphanet:90795 |
congenital adrenal hyperplasia due to 11-beta-hydroxylase deficiency |
MONDO:0009705 |
OMIM:255120 |
Orphanet:156 |
carnitine palmitoyl transferase 1A deficiency |
MONDO:0014233 |
OMIM:615530 |
Orphanet:391411 |
early-onset Parkinson disease 20 |
MONDO:0018005 |
- |
Orphanet:329475 |
spastic paraplegia-Paget disease of bone syndrome |
MONDO:0100101 |
OMIM:208150 |
Orphanet:994 |
fetal akinesia deformation sequence 1 |
MONDO:0008855 |
OMIM:209920 |
Orphanet:572 |
MHC class II deficiency |
MONDO:0009266 |
OMIM:230900 |
Orphanet:77260 |
Gaucher disease type II |
MONDO:0009675 |
OMIM:253600 |
Orphanet:267 |
autosomal recessive limb-girdle muscular dystrophy type 2A |
MONDO:0100251 |
- |
Orphanet:53715 |
familial hyperphosphatemic tumoral calcinosis/hyperphosphatemic hyperostosis syndrome |
MONDO:0044637 |
- |
Orphanet:494526 |
infantile-onset generalized dyskinesia with orofacial involvement |
MONDO:0018464 |
OMIM:300661 |
Orphanet:411543 |
severe phosphoribosylpyrophosphate synthetase superactivity |
MONDO:0009593 |
OMIM:250220 |
Orphanet:93317 |
spondylometaphyseal dysplasia, Sedaghatian type |
MONDO:0009783 |
OMIM:258450 |
Orphanet:254886 |
progressive external ophthalmoplegia with mitochondrial DNA deletions, autosomal recessive 1 |
MONDO:0017360 |
OMIM:251000 |
Orphanet:289916 |
vitamin B12-unresponsive methylmalonic acidemia type mut0 |
MONDO:0008977 |
OMIM:215300 |
Orphanet:55880 |
chondrosarcoma |
MONDO:0029141 |
OMIM:618144 |
- |
Usher syndrome, type 4 |
MONDO:0005090 |
OMIM:181500 |
Orphanet:3140 |
schizophrenia |
MONDO:0009485 |
OMIM:244450 |
Orphanet:2707 |
oculocerebrofacial syndrome, Kaufman type |
MONDO:0030077 |
OMIM:618845 |
- |
vertebral, cardiac, renal, and limb defects syndrome 3 |
MONDO:0013259 |
OMIM:613411 |
Orphanet:75382 |
Oguchi disease-2 |
MONDO:0032608 |
OMIM:618224 |
- |
mitochondrial complex 1 deficiency, nuclear type 3 |
MONDO:0018463 |
OMIM:300661 |
Orphanet:411536 |
mild phosphoribosylpyrophosphate synthetase superactivity |
MONDO:0012520 |
OMIM:610549 |
Orphanet:2297 |
insulin-resistance syndrome type A |
MONDO:0010465 |
OMIM:300867 |
Orphanet:2322 |
Kabuki syndrome 2 |
MONDO:0018876 |
- |
Orphanet:52416 |
mantle cell lymphoma |
MONDO:0011214 |
OMIM:602347 |
Orphanet:79305 |
progressive familial intrahepatic cholestasis type 3 |
MONDO:0100348 |
OMIM:619091 |
- |
neurodevelopmental disorder with microcephaly, impaired language, and gait abnormalities |
MONDO:0013354 |
OMIM:613672 |
Orphanet:254343 |
spastic ataxia 4 |
MONDO:0033615 |
OMIM:619028 |
- |
coenzyme q10 deficiency, primary, 9 |
MONDO:0013162 |
OMIM:613158 |
Orphanet:206559 |
autosomal recessive limb-girdle muscular dystrophy type 2N |
MONDO:0012393 |
OMIM:610015 |
Orphanet:71278 |
congenital brain dysgenesis due to glutamine synthetase deficiency |
MONDO:0010159 |
OMIM:276300 |
Orphanet:252202 |
mismatch repair cancer syndrome 1 |
MONDO:0004691 |
- |
Orphanet:730 |
autosomal dominant polycystic kidney disease |
MONDO:0014599 |
OMIM:616351 |
- |
intellectual disability, autosomal dominant 34 |
MONDO:0016505 |
- |
Orphanet:231625 |
aldosterone-producing adrenal cortex adenoma |
MONDO:0020332 |
- |
Orphanet:98849 |
systemic mastocytosis with an associated clonal hematologic non-mast cell lineage disease |
MONDO:0019623 |
OMIM:610618 |
Orphanet:91378 |
hereditary angioedema |
MONDO:0009441 |
OMIM:242300 |
Orphanet:313 |
autosomal recessive congenital ichthyosis 1 |
MONDO:0019502 |
OMIM:617188 |
Orphanet:88616 |
autosomal recessive non-syndromic intellectual disability |
MONDO:0009539 |
OMIM:247640 |
Orphanet:513 |
lymphoblastic leukemia, acute, with lymphomatous features |
MONDO:0013386 |
OMIM:613718 |
Orphanet:90636 |
autosomal recessive nonsyndromic hearing loss 74 |
MONDO:0014253 |
OMIM:615559 |
Orphanet:3261 |
autoimmune lymphoproliferative syndrome type 3 |
MONDO:0012672 |
OMIM:611465 |
- |
cholelithiasis |
MONDO:0005347 |
- |
- |
hypertriglyceridemia |
MONDO:0018097 |
OMIM:617065 |
Orphanet:3451 |
West syndrome |
MONDO:0018273 |
- |
Orphanet:370930 |
XYLT1-CDG |
MONDO:0018767 |
OMIM:602079 |
Orphanet:468726 |
severe primary trimethylaminuria |
MONDO:0060622 |
OMIM:617804 |
- |
neurodevelopmental disorder with severe motor impairment and absent language |
MONDO:0013327 |
OMIM:613616 |
Orphanet:93600 |
primary hyperoxaluria type 3 |
MONDO:0018138 |
OMIM:103470 |
Orphanet:352740 |
ocular albinism with congenital sensorineural hearing loss |
MONDO:0014126 |
OMIM:615300 |
Orphanet:2855 |
Perrault syndrome 4 |
MONDO:0014679 |
OMIM:616531 |
Orphanet:98889 |
polymicrogyria, perisylvian, with cerebellar hypoplasia and arthrogryposis |
MONDO:0018644 |
- |
Orphanet:447757 |
autosomal dominant complex spastic paraplegia type 9B |
MONDO:0009504 |
OMIM:245400 |
Orphanet:17 |
mitochondrial DNA depletion syndrome 9 |
MONDO:0013692 |
OMIM:614327 |
Orphanet:289539 |
BAP1-related tumor predisposition syndrome |
MONDO:0020526 |
- |
Orphanet:99887 |
acute megakaryoblastic leukemia in down syndrome |
MONDO:0016485 |
OMIM:614504 |
Orphanet:231183 |
Usher syndrome type 3 |
MONDO:0014175 |
OMIM:615418 |
Orphanet:1369 |
mitochondrial DNA depletion syndrome 12B (cardiomyopathic type), autosomal recessive |
MONDO:0015170 |
OMIM:616868 |
Orphanet:103908 |
congenital sodium diarrhea |
MONDO:0010977 |
OMIM:601003 |
Orphanet:53347 |
Brody myopathy |
MONDO:0011730 |
OMIM:606812 |
Orphanet:24 |
fumaric aciduria |
MONDO:0009950 |
OMIM:266200 |
Orphanet:766 |
pyruvate kinase deficiency of red cells |
MONDO:0020736 |
OMIM:191480 |
Orphanet:1410 |
uncombable hair syndrome 1 |
MONDO:0042490 |
OMIM:202700 |
Orphanet:486 |
neutropenia, severe congenital, 1, autosomal dominant |
MONDO:0011537 |
OMIM:605309 |
Orphanet:210548 |
macrocephaly-autism syndrome |
MONDO:0014946 |
OMIM:617159 |
- |
Sifrim-Hitz-Weiss syndrome |
MONDO:0012348 |
OMIM:609812 |
Orphanet:552 |
maturity-onset diabetes of the young type 8 |
MONDO:0013456 |
OMIM:613839 |
Orphanet:319651 |
constitutional megaloblastic anemia with severe neurologic disease |
MONDO:0014612 |
OMIM:616371 |
Orphanet:2032 |
pulmonary fibrosis and/or bone marrow failure, Telomere-related, 4 |
MONDO:0012353 |
OMIM:609820 |
Orphanet:247511 |
erythrocytosis, familial, 3 |
MONDO:0018485 |
- |
Orphanet:420429 |
glycogen storage disease due to acid maltase deficiency, late-onset |
MONDO:0013338 |
OMIM:613641 |
Orphanet:254334 |
Charcot-Marie-Tooth disease recessive intermediate B |
MONDO:0014418 |
OMIM:615959 |
Orphanet:169186 |
myopathy, centronuclear, 5 |
MONDO:0010814 |
OMIM:600092 |
Orphanet:1422 |
chondrodysplasia-pseudohermaphroditism syndrome |
MONDO:0018461 |
- |
Orphanet:411511 |
Angelman syndrome due to a point mutation |
MONDO:0020358 |
- |
Orphanet:98947 |
coloboma of optic disc |
MONDO:0014873 |
OMIM:617025 |
Orphanet:64754 |
nevus comedonicus syndrome |
MONDO:0009021 |
OMIM:217980 |
Orphanet:3338 |
Toriello-Carey syndrome |
MONDO:0013741 |
OMIM:614417 |
Orphanet:165805 |
familial temporal lobe epilepsy 5 |
MONDO:0012398 |
OMIM:610024 |
Orphanet:49382 |
retinal cone dystrophy 3A |
MONDO:0012546 |
OMIM:610725 |
- |
nephrotic syndrome, type 3 |
MONDO:0012127 |
OMIM:608807 |
Orphanet:140922 |
autosomal recessive limb-girdle muscular dystrophy type 2J |
MONDO:0012994 |
OMIM:612716 |
Orphanet:70594 |
dopa-responsive dystonia due to sepiapterin reductase deficiency |
MONDO:0060527 |
OMIM:617596 |
- |
maleylacetoacetate isomerase deficiency |
MONDO:0030982 |
OMIM:619221 |
- |
sulfide quinone oxidoreductase deficiency |
MONDO:0017698 |
OMIM:232500 |
Orphanet:308670 |
glycogen storage disease due to glycogen branching enzyme deficiency, congenital neuromuscular form |
MONDO:0009660 |
OMIM:253010 |
Orphanet:582 |
mucopolysaccharidosis type 4B |
MONDO:0019637 |
- |
Orphanet:93101 |
renal hypoplasia |
MONDO:0008765 |
OMIM:204100 |
- |
Leber congenital amaurosis 2 |
MONDO:0023644 |
- |
- |
lip and oral cavity carcinoma |
MONDO:0017602 |
- |
Orphanet:300895 |
ALK-positive anaplastic large cell lymphoma |
MONDO:0018832 |
- |
Orphanet:482077 |
HTRA1-related autosomal dominant cerebral small vessel disease |
MONDO:0013579 |
OMIM:614105 |
Orphanet:289307 |
methylmalonate semialdehyde dehydrogenase deficiency |
MONDO:0030105 |
OMIM:618881 |
Orphanet:570422 |
galactosemia 4 |
OMIM:181800 |
OMIM:181800 |
- |
SCOLIOSIS, ISOLATED, SUSCEPTIBILITY TO, 1 |
MONDO:0008280 |
OMIM:175200 |
Orphanet:2869 |
Peutz-Jeghers syndrome |
MONDO:0007376 |
OMIM:121850 |
Orphanet:98970 |
fleck corneal dystrophy |
MONDO:0015020 |
OMIM:617323 |
- |
intellectual disability, autosomal recessive 59 |
MONDO:0009940 |
OMIM:265800 |
Orphanet:763 |
pycnodysostosis |
MONDO:0018663 |
OMIM:618019 |
Orphanet:448267 |
regressive spondylometaphyseal dysplasia |
MONDO:0013539 |
OMIM:614037 |
Orphanet:79507 |
hypotonia-failure to thrive-microcephaly syndrome |
MONDO:0030947 |
OMIM:619173 |
- |
neurodegeneration, childhood-onset, with hypotonia, respiratory insufficiency, and brain imaging abnormalities |
MONDO:0032687 |
OMIM:618342 |
- |
intellectual developmental disorder with abnormal behavior, microcephaly, and short stature |
MONDO:0009624 |
OMIM:616335 |
Orphanet:2518 |
microcephaly and chorioretinopathy 1 |
MONDO:0024553 |
OMIM:600462 |
Orphanet:2598 |
myopathy, lactic acidosis, and sideroblastic anemia 1 |
MONDO:0009659 |
OMIM:253000 |
Orphanet:582 |
mucopolysaccharidosis type 4A |
MONDO:0000468 |
- |
- |
third-degree atrioventricular block |
MONDO:0013083 |
OMIM:613014 |
- |
neuroblastoma, susceptibility to, 3 |
MONDO:0014208 |
OMIM:615490 |
Orphanet:397968 |
Charcot-Marie-Tooth disease type 2R |
MONDO:0009797 |
OMIM:258900 |
Orphanet:30 |
orotic aciduria |
MONDO:0009874 |
OMIM:262190 |
Orphanet:769 |
Rabson-Mendenhall syndrome |
MONDO:0017582 |
- |
Orphanet:300385 |
pituitary adenocarcinoma |
MONDO:0010502 |
OMIM:300968 |
- |
intellectual disability, X-linked 99, syndromic, female-restricted |
MONDO:0010767 |
OMIM:415000 |
Orphanet:1646 |
spermatogenic failure, Y-linked, 2 |
MONDO:0013160 |
OMIM:613156 |
Orphanet:370968 |
muscular dystrophy-dystroglycanopathy (congenital with intellectual disability), type B2 |
MONDO:0032906 |
OMIM:618770 |
- |
spastic paraplegia 82, autosomal recessive |
MONDO:0014728 |
OMIM:616672 |
Orphanet:477774 |
combined oxidative phosphorylation defect type 27 |
MONDO:0014212 |
OMIM:615501 |
Orphanet:99732 |
sulfite oxidase deficiency due to molybdenum cofactor deficiency type C |
MONDO:0014867 |
OMIM:617018 |
Orphanet:497764 |
spinocerebellar ataxia 43 |
MONDO:0044737 |
- |
Orphanet:506353 |
autosomal recessive complex spastic paraplegia due to kennedy pathway dysfunction |
MONDO:0014141 |
OMIM:615351 |
Orphanet:370968 |
muscular dystrophy-dystroglycanopathy (congenital with intellectual disability), type B14 |
MONDO:0019569 |
OMIM:216400 |
Orphanet:90324 |
Cockayne syndrome type 1 |
MONDO:0009235 |
OMIM:228980 |
Orphanet:363989 |
familial benign flecked retina |
MONDO:0013792 |
OMIM:614519 |
- |
intracerebral hemorrhage |
MONDO:0008296 |
OMIM:176100 |
Orphanet:95159 |
familial porphyria cutanea tarda |
MONDO:0005010 |
OMIM:614466 |
- |
coronary artery disorder |
MONDO:0008340 |
OMIM:616219 |
Orphanet:91411 |
congenital ptosis |
MONDO:0015372 |
OMIM:615193 |
Orphanet:140957 |
autosomal dominant macrothrombocytopenia |
MONDO:0009327 |
OMIM:234750 |
- |
heart, malformation of |
MONDO:0032648 |
OMIM:618273 |
- |
mega-corpus-callosum syndrome with cerebellar hypoplasia and cortical malformations |
MONDO:0014018 |
OMIM:615033 |
Orphanet:320380 |
hereditary spastic paraplegia 54 |
MONDO:0013074 |
OMIM:613001 |
Orphanet:2396 |
encephalocraniocutaneous lipomatosis |
MONDO:0032913 |
OMIM:618780 |
- |
congenital heart defects, multiple types, 7 |
MONDO:0005336 |
OMIM:300695 |
- |
myopathy |
MONDO:0012518 |
OMIM:610542 |
Orphanet:590 |
congenital myasthenic syndrome 12 |
MONDO:0012367 |
OMIM:609923 |
- |
retinitis pigmentosa 31 |
MONDO:0032930 |
OMIM:618808 |
- |
intellectual developmental disorder with poor growth and with or without seizures or ataxia |
MONDO:0044330 |
OMIM:618011 |
- |
hyperekplexia 4 |
MONDO:0020121 |
OMIM:600416 |
Orphanet:98473 |
muscular dystrophy |
MONDO:0010780 |
OMIM:500009 |
Orphanet:254864 |
mitochondrial myopathy with reversible cytochrome C oxidase deficiency |
MONDO:0011717 |
OMIM:606762 |
Orphanet:35878 |
hyperinsulinism-hyperammonemia syndrome |
MONDO:0043364 |
OMIM:261500 |
- |
eosinophil peroxidase deficiency |
MONDO:0014008 |
OMIM:615011 |
- |
phosphohydroxylysinuria |
MONDO:0012450 |
OMIM:610246 |
Orphanet:101109 |
spinocerebellar ataxia type 28 |
MONDO:0024535 |
OMIM:182250 |
Orphanet:85191 |
Singleton-Merten syndrome 1 |
MONDO:0008759 |
OMIM:203740 |
Orphanet:31 |
oxoglutaricaciduria |
MONDO:0020378 |
OMIM:613763 |
Orphanet:98993 |
early-onset posterior polar cataract |
MONDO:0010389 |
OMIM:300645 |
Orphanet:319623 |
X-linked mendelian susceptibility to mycobacterial diseases due to CYBB deficiency |
MONDO:0032642 |
OMIM:618265 |
Orphanet:565858 |
arthrogryposis, cleft palate, craniosynostosis, and impaired intellectual development |
MONDO:0008910 |
OMIM:212070 |
- |
carboxypeptidase N deficiency |
MONDO:0024573 |
- |
Orphanet:155 |
familial hypertrophic cardiomyopathy |
MONDO:0013485 |
OMIM:613908 |
Orphanet:276193 |
spinocerebellar ataxia type 35 |
MONDO:0060624 |
OMIM:617807 |
- |
neurodevelopmental disorder with ataxic gait, absent speech, and decreased cortical white matter |
MONDO:0011749 |
OMIM:606952 |
Orphanet:79434 |
oculocutaneous albinism type 1B |
MONDO:0019636 |
- |
Orphanet:93100 |
renal agenesis, unilateral |
MONDO:0014762 |
OMIM:616749 |
- |
heterotaxy, visceral, 7, autosomal |
MONDO:0007817 |
OMIM:147050 |
- |
IgE responsiveness, atopic |
MONDO:0017354 |
- |
Orphanet:289860 |
infantile glycine encephalopathy |
MONDO:0012421 |
OMIM:610154 |
- |
autosomal recessive nonsyndromic hearing loss 44 |
MONDO:0030899 |
OMIM:619165 |
Orphanet:597733 |
oculocutaneous albinism type 8 |
MONDO:0009215 |
OMIM:227650 |
Orphanet:84 |
Fanconi anemia complementation group A |
MONDO:0012221 |
OMIM:609241 |
Orphanet:79281 |
alpha-N-acetylgalactosaminidase deficiency type 1 |
MONDO:0010870 |
OMIM:600334 |
Orphanet:609 |
tibial muscular dystrophy |
MONDO:0014861 |
OMIM:617006 |
- |
autoimmune disease, multisystem, infantile-onset, 2 |
MONDO:0011397 |
OMIM:604121 |
Orphanet:314404 |
autosomal dominant cerebellar ataxia, deafness and narcolepsy |
MONDO:0013473 |
OMIM:613870 |
- |
Hirschsprung disease, cardiac defects, and autonomic dysfunction |
MONDO:0014869 |
OMIM:617021 |
Orphanet:528091 |
hydrops-lactic acidosis-sideroblastic anemia-multisystemic failure syndrome |
MONDO:0004675 |
- |
- |
mitochondrial encephalomyopathy |
MONDO:0019742 |
- |
Orphanet:93589 |
late-onset nephronophthisis |
MONDO:0012969 |
OMIM:612633 |
- |
microvascular complications of diabetes, susceptibility to, 5 |
MONDO:0011787 |
OMIM:607155 |
Orphanet:34515 |
autosomal recessive limb-girdle muscular dystrophy type 2I |
MONDO:0011969 |
OMIM:608104 |
Orphanet:79325 |
ALG8-CDG |
MONDO:0054742 |
OMIM:617873 |
- |
combined oxidative phosphorylation deficiency 35 |
MONDO:0013802 |
OMIM:614559 |
Orphanet:313850 |
infantile cerebellar-retinal degeneration |
MONDO:0054785 |
OMIM:617954 |
- |
multiple mitochondrial dysfunctions syndrome 6 |
MONDO:0008751 |
OMIM:203400 |
Orphanet:99763 |
corticosterone methyloxidase type 1 deficiency |
MONDO:0015626 |
- |
Orphanet:166 |
Charcot-Marie-Tooth disease |
MONDO:0014632 |
OMIM:616420 |
- |
hypomyelinating leukodystrophy 10 |
MONDO:0010363 |
OMIM:300577 |
- |
intellectual disability, X-linked 91 |
MONDO:0020850 |
OMIM:618109 |
- |
intellectual disability, autosomal recessive 65 |
MONDO:0044329 |
OMIM:617952 |
- |
osteogenesis imperfecta, type 18 |
MONDO:0013536 |
OMIM:614034 |
Orphanet:562509 |
heme oxygenase 1 deficiency |
MONDO:0026724 |
OMIM:301025 |
- |
Paganini-Miozzo syndrome |
MONDO:0010318 |
OMIM:300422 |
Orphanet:323 |
FG syndrome 4 |
MONDO:0014130 |
OMIM:615327 |
Orphanet:79145 |
Dowling-Degos disease 2 |
MONDO:0005575 |
OMIM:615083 |
Orphanet:466667 |
colorectal cancer |
MONDO:0014139 |
OMIM:615349 |
Orphanet:75496 |
Ehlers-Danlos syndrome, spondylodysplastic type, 2 |
MONDO:0010184 |
OMIM:277400 |
Orphanet:79282 |
methylmalonic aciduria and homocystinuria type cblC |
MONDO:0011137 |
OMIM:601718 |
Orphanet:791 |
retinitis pigmentosa 19 |
MONDO:0009756 |
OMIM:257200 |
Orphanet:77292 |
Niemann-Pick disease type A |
MONDO:0032890 |
OMIM:618733 |
- |
neuromuscular disease and ocular or auditory anomalies with or without seizures |
MONDO:0044331 |
- |
Orphanet:226316 |
genetic transient congenital hypothyroidism |
MONDO:0012074 |
OMIM:608612 |
Orphanet:90154 |
mandibuloacral dysplasia with type B lipodystrophy |
MONDO:0014759 |
OMIM:616739 |
- |
intellectual disability, autosomal recessive 51 |
MONDO:0014684 |
OMIM:616539 |
Orphanet:477684 |
combined oxidative phosphorylation defect type 26 |
MONDO:0009353 |
OMIM:236250 |
Orphanet:395 |
homocystinuria due to methylene tetrahydrofolate reductase deficiency |
MONDO:0033046 |
OMIM:617564 |
- |
Meier-Gorlin syndrome 8 |
MONDO:0011218 |
OMIM:602400 |
Orphanet:91132 |
autosomal recessive congenital ichthyosis 11 |
MONDO:0010961 |
OMIM:600955 |
Orphanet:71528 |
obesity due to prohormone convertase I deficiency |
MONDO:0010258 |
OMIM:300987 |
Orphanet:85282 |
MEHMO syndrome |
MONDO:0013391 |
OMIM:613724 |
Orphanet:163684 |
sterol carrier protein 2 deficiency |
MONDO:0013817 |
OMIM:614595 |
Orphanet:275555 |
preeclampsia/eclampsia 5 |
MONDO:0017175 |
- |
Orphanet:276241 |
Machado-Joseph disease type 2 |
MONDO:0007681 |
OMIM:138800 |
Orphanet:276399 |
goiter, multinodular 1, with or without Sertoli-Leydig cell tumors |
MONDO:0009054 |
OMIM:617403 |
Orphanet:357074 |
autosomal recessive cutis laxa type 2, classic type |
MONDO:0014190 |
OMIM:615440 |
Orphanet:369913 |
combined oxidative phosphorylation defect type 17 |
MONDO:0012885 |
OMIM:612379 |
Orphanet:324737 |
SRD5A3-CDG |
MONDO:0014005 |
OMIM:615008 |
Orphanet:54370 |
immunoglobulin-mediated membranoproliferative glomerulonephritis |
MONDO:0010938 |
OMIM:600802 |
Orphanet:35078 |
T-B+ severe combined immunodeficiency due to JAK3 deficiency |
MONDO:0013495 |
OMIM:613943 |
Orphanet:313 |
autosomal recessive congenital ichthyosis 8 |
MONDO:0017725 |
- |
Orphanet:309185 |
Tay-Sachs disease, b variant, juvenile form |
MONDO:0011283 |
OMIM:603041 |
Orphanet:298 |
mitochondrial DNA depletion syndrome 1 |
MONDO:0009923 |
OMIM:264600 |
Orphanet:753 |
46,XY disorder of sex development due to 5-alpha-reductase 2 deficiency |
MONDO:0009992 |
OMIM:268200 |
Orphanet:99845 |
myoglobinuria, acute recurrent, autosomal recessive |
MONDO:0030005 |
OMIM:618832 |
- |
epilepsy, early-onset, with or without developmental delay |
MONDO:0020376 |
OMIM:611391 |
Orphanet:98991 |
early-onset nuclear cataract |
MONDO:0032897 |
OMIM:618748 |
- |
intellectual developmental disorder with hypotonia and behavioral abnormalities |
MONDO:0023692 |
OMIM:248600 |
- |
maple syrup urine disease type 1B |
MONDO:0054695 |
OMIM:617760 |
- |
myopathy, centronuclear, 6, with fiber-type disproportion |
MONDO:0010619 |
OMIM:307800 |
Orphanet:89936 |
X-linked dominant hypophosphatemic rickets |
MONDO:0032838 |
OMIM:618622 |
- |
neurodevelopmental disorder with microcephaly, arthrogryposis, and structural brain anomalies |
MONDO:0009414 |
OMIM:240600 |
Orphanet:2089 |
glycogen storage disorder due to hepatic glycogen synthase deficiency |
MONDO:0019068 |
- |
Orphanet:69063 |
congenital membranous nephropathy due to maternal anti-neutral endopeptidase alloimmunization |
MONDO:0009490 |
OMIM:245000 |
Orphanet:678 |
Papillon-Lefevre disease |
MONDO:0007289 |
OMIM:116700 |
Orphanet:91492 |
cataract 13 with adult I phenotype |
MONDO:0008772 |
OMIM:204700 |
Orphanet:100033 |
amelogenesis imperfecta type 2A1 |
MONDO:0010602 |
OMIM:306700 |
Orphanet:98878 |
hemophilia A |
MONDO:0014969 |
OMIM:617213 |
Orphanet:440713 |
isolated sedoheptulokinase deficiency |
MONDO:0013350 |
OMIM:613662 |
Orphanet:298 |
mitochondrial DNA depletion syndrome 4b |
MONDO:0007847 |
OMIM:148100 |
- |
keloid formation |
MONDO:0012213 |
OMIM:609195 |
Orphanet:101006 |
hereditary spastic paraplegia 26 |
MONDO:0005012 |
OMIM:615848 |
- |
cutaneous melanoma |
MONDO:0008185 |
OMIM:167800 |
Orphanet:676 |
hereditary chronic pancreatitis |
MONDO:0011136 |
OMIM:601709 |
Orphanet:220436 |
Quebec platelet disorder |
MONDO:0013726 |
OMIM:614388 |
Orphanet:330050 |
encephalopathy, lethal, due to defective mitochondrial peroxisomal fission 1 |
MONDO:0009285 |
OMIM:231950 |
Orphanet:33573 |
gamma-glutamyl transpeptidase deficiency |
MONDO:0030876 |
OMIM:619142 |
- |
cardioacrofacial dysplasia 1 |
MONDO:0005292 |
OMIM:191390 |
- |
colitis |
MONDO:0010857 |
OMIM:600274 |
Orphanet:282 |
semantic dementia |
MONDO:0011528 |
OMIM:605258 |
Orphanet:183666 |
hyper-IgM syndrome type 2 |
MONDO:0009629 |
OMIM:251450 |
Orphanet:1425 |
Desbuquois dysplasia 1 |
MONDO:0009277 |
OMIM:231300 |
Orphanet:98977 |
glaucoma 3A |
MONDO:0030914 |
OMIM:617752 |
- |
Clark-Baraitser syndrome |
MONDO:0017190 |
- |
Orphanet:276621 |
sporadic pheochromocytoma/secreting paraganglioma |
MONDO:0011215 |
OMIM:602361 |
Orphanet:2763 |
osteocraniostenosis |
MONDO:0013521 |
OMIM:613989 |
Orphanet:3322 |
dyskeratosis congenita, autosomal dominant 2 |
MONDO:0010879 |
OMIM:600373 |
Orphanet:1458 |
CODAS syndrome |
MONDO:0008996 |
OMIM:216360 |
Orphanet:1454 |
COACH syndrome 1 |
MONDO:0010819 |
OMIM:600110 |
Orphanet:827 |
Stargardt disease 3 |
MONDO:0008721 |
OMIM:201450 |
Orphanet:42 |
medium chain acyl-CoA dehydrogenase deficiency |
MONDO:0009559 |
OMIM:248400 |
- |
mandibulofacial dysostosis with mental deficiency |
MONDO:0012052 |
OMIM:608540 |
Orphanet:79327 |
ALG1-CDG |
MONDO:0011669 |
OMIM:606407 |
Orphanet:238523 |
hypotonia-cystinuria syndrome |
MONDO:0013337 |
OMIM:613640 |
Orphanet:36386 |
neuropathy, hereditary sensory and autonomic, type 1C |
MONDO:0060554 |
OMIM:617660 |
- |
vertebral, cardiac, renal, and limb defects syndrome 1 |
MONDO:0012143 |
OMIM:608885 |
Orphanet:168577 |
hereditary cryohydrocytosis with reduced stomatin |
MONDO:0010500 |
OMIM:300966 |
- |
intellectual disability, X-linked, syndromic 33 |
MONDO:0011476 |
OMIM:604571 |
Orphanet:34592 |
MHC class I deficiency |
MONDO:0019536 |
OMIM:235400 |
Orphanet:90038 |
typical hemolytic-uremic syndrome |
MONDO:0010717 |
OMIM:312170 |
Orphanet:79243 |
pyruvate dehydrogenase E1-alpha deficiency |
MONDO:0015362 |
- |
Orphanet:140465 |
autosomal dominant distal hereditary motor neuropathy |
MONDO:0012963 |
OMIM:612624 |
- |
microvascular complications of diabetes, susceptibility to, 3 |
MONDO:0014615 |
OMIM:616390 |
- |
trichothiodystrophy 2, photosensitive |
MONDO:0014908 |
OMIM:617090 |
- |
microcephaly 17, primary, autosomal recessive |
MONDO:0009292 |
OMIM:263570 |
Orphanet:367 |
glycogen storage disease due to glycogen branching enzyme deficiency |
MONDO:0013245 |
OMIM:613385 |
Orphanet:228426 |
syndromic multisystem autoimmune disease due to ITCH deficiency |
MONDO:0018834 |
- |
Orphanet:482601 |
adenylosuccinate synthetase-like 1-related distal myopathy |
MONDO:0009427 |
OMIM:241500 |
Orphanet:436 |
obsolete infantile hypophosphatasia |
MONDO:0060611 |
OMIM:617780 |
- |
combined immunodeficiency and megaloblastic anemia with or without hyperhomocysteinemia |
MONDO:0009072 |
OMIM:220200 |
Orphanet:217 |
Dandy-Walker syndrome |
MONDO:0012524 |
OMIM:610600 |
Orphanet:99763 |
corticosterone methyloxidase type 2 deficiency |
MONDO:0054861 |
OMIM:618095 |
- |
intellectual disability, autosomal recessive 63 |
MONDO:0007405 |
OMIM:123500 |
Orphanet:207 |
Crouzon syndrome |
MONDO:0007932 |
OMIM:153800 |
- |
age related macular degeneration 2 |
MONDO:0014558 |
OMIM:616268 |
Orphanet:457193 |
autosomal dominant intellectual disability-craniofacial anomalies-cardiac defects syndrome |
MONDO:0019791 |
- |
Orphanet:94125 |
recessive mitochondrial ataxia syndrome |
MONDO:0008199 |
OMIM:616361 |
Orphanet:411602 |
late-onset Parkinson disease |
MONDO:0013041 |
OMIM:612923 |
Orphanet:93580 |
atypical hemolytic-uremic syndrome with I factor anomaly |
MONDO:0017791 |
- |
Orphanet:314029 |
high bone mass osteogenesis imperfecta |
MONDO:0011738 |
OMIM:606854 |
Orphanet:268940 |
bilateral frontoparietal polymicrogyria |
MONDO:0014481 |
OMIM:616069 |
Orphanet:294023 |
inflammatory skin and bowel disease, neonatal, 2 |
MONDO:0014157 |
OMIM:615381 |
Orphanet:363649 |
mandibular hypoplasia-deafness-progeroid syndrome |
MONDO:0013303 |
OMIM:613551 |
- |
autoimmune disease, susceptibility to, 6 |
MONDO:0013543 |
OMIM:614044 |
- |
trypsinogen deficiency |
MONDO:0009857 |
OMIM:261550 |
Orphanet:2856 |
persistent Mullerian duct syndrome |
MONDO:0008147 |
OMIM:610915 |
Orphanet:216804 |
osteogenesis imperfecta type 2 |
MONDO:0000170 |
OMIM:616428 |
Orphanet:98938 |
microphthalmia, isolated, with coloboma |
MONDO:0013624 |
OMIM:614202 |
- |
Rafiq syndrome |
MONDO:0014397 |
OMIM:615917 |
Orphanet:420728 |
combined oxidative phosphorylation defect type 20 |
MONDO:0013528 |
OMIM:614020 |
- |
intellectual disability, autosomal recessive 14 |
MONDO:0009416 |
OMIM:240900 |
Orphanet:293964 |
hypoinsulinemic hypoglycemia and body hemihypertrophy |
MONDO:0032665 |
OMIM:618302 |
- |
intellectual developmental disorder, autosomal recessive 68 |
MONDO:0030872 |
OMIM:619132 |
- |
frontotemporal dementia and/or amyotrophic lateral sclerosis 8 |
MONDO:0011232 |
OMIM:602481 |
Orphanet:569 |
migraine, familial hemiplegic, 2 |
MONDO:0011698 |
OMIM:606664 |
Orphanet:289891 |
glycine N-methyltransferase deficiency |
MONDO:0009100 |
OMIM:222100 |
- |
IDDM 1 |
MONDO:0014004 |
OMIM:615007 |
Orphanet:1980 |
basal ganglia calcification, idiopathic, 4 |
MONDO:0013276 |
OMIM:613471 |
Orphanet:779 |
Reynolds syndrome |
MONDO:0009591 |
OMIM:250100 |
Orphanet:512 |
metachromatic leukodystrophy, juvenile form |
MONDO:0010949 |
OMIM:600882 |
Orphanet:99936 |
Charcot-Marie-Tooth disease type 2B |
MONDO:0002032 |
- |
- |
colon carcinoma |
MONDO:0010247 |
OMIM:300100 |
Orphanet:43 |
X-linked cerebral adrenoleukodystrophy |
MONDO:0009615 |
OMIM:251120 |
Orphanet:308425 |
methylmalonic acidemia due to methylmalonyl-CoA epimerase deficiency |
MONDO:0032749 |
OMIM:618434 |
- |
hearing loss, autosomal recessive 94 |
MONDO:0013334 |
OMIM:613630 |
Orphanet:465824 |
cocoon syndrome |
MONDO:0019776 |
OMIM:309580 |
Orphanet:93972 |
Juberg-Marsidi syndrome |
MONDO:0014757 |
OMIM:616737 |
Orphanet:487796 |
macrothrombocytopenia-lymphedema-developmental delay-facial dysmorphism-camptodactyly syndrome |
MONDO:0014351 |
OMIM:615809 |
Orphanet:369920 |
pontocerebellar hypoplasia type 9 |
MONDO:0013924 |
OMIM:614856 |
Orphanet:216812 |
osteogenesis imperfecta type 13 |
MONDO:0013737 |
OMIM:614409 |
Orphanet:320391 |
hereditary spastic paraplegia 46 |
MONDO:0010495 |
OMIM:300953 |
- |
trichothiodystrophy 5, nonphotosensitive |
MONDO:0013252 |
OMIM:613398 |
Orphanet:280558 |
Warsaw breakage syndrome |
MONDO:0014600 |
OMIM:616353 |
Orphanet:3322 |
dyskeratosis congenita, autosomal recessive 6 |
MONDO:0013046 |
OMIM:612932 |
Orphanet:99849 |
glycogen storage disease due to muscle beta-enolase deficiency |
MONDO:0030991 |
OMIM:619232 |
- |
bile acid conjugation defect 1 |
MONDO:0014484 |
OMIM:616080 |
- |
microcephaly 12, primary, autosomal recessive |
MONDO:0010328 |
OMIM:300448 |
Orphanet:231401 |
alpha-thalassemia-myelodysplastic syndrome |
MONDO:0019777 |
OMIM:309580 |
Orphanet:93973 |
Carpenter-Waziri syndrome |
MONDO:0014382 |
OMIM:615879 |
Orphanet:404443 |
tall stature-intellectual disability-facial dysmorphism syndrome |
MONDO:0018877 |
OMIM:136880 |
Orphanet:52427 |
retinitis punctata albescens |
MONDO:0030974 |
OMIM:619224 |
- |
mitochondrial complex 2 deficiency, nuclear type 4 |
MONDO:0011141 |
OMIM:601775 |
- |
megaloblastic anemia, folate-responsive |
MONDO:0011719 |
OMIM:606764 |
Orphanet:44890 |
gastrointestinal stromal tumor |
MONDO:0011610 |
OMIM:605850 |
Orphanet:243343 |
dimethylglycine dehydrogenase deficiency |
MONDO:0010772 |
OMIM:500001 |
Orphanet:99718 |
Leber optic atrophy and dystonia |
MONDO:0009096 |
OMIM:221820 |
Orphanet:313808 |
hereditary diffuse leukoencephalopathy with axonal spheroids and pigmented glia |
MONDO:0021067 |
- |
- |
mediastinal germ cell tumor |
MONDO:0011527 |
OMIM:605253 |
Orphanet:99951 |
Charcot-Marie-Tooth disease type 4E |
MONDO:0011613 |
OMIM:605909 |
Orphanet:2828 |
autosomal recessive early-onset Parkinson disease 6 |
MONDO:0014339 |
OMIM:615768 |
Orphanet:412057 |
autosomal recessive spinocerebellar ataxia 16 |
MONDO:0010217 |
OMIM:278800 |
Orphanet:1569 |
de Sanctis-Cacchione syndrome |
MONDO:0019588 |
OMIM:616958 |
Orphanet:90636 |
hearing loss, autosomal recessive |
MONDO:0011178 |
OMIM:602066 |
Orphanet:31709 |
infantile convulsions and choreoathetosis |
MONDO:0013663 |
OMIM:614278 |
- |
platelet-activating factor acetylhydrolase deficiency |
MONDO:0012624 |
OMIM:611126 |
Orphanet:99901 |
acyl-CoA dehydrogenase 9 deficiency |
MONDO:0011866 |
OMIM:607596 |
Orphanet:2254 |
pontocerebellar hypoplasia type 1A |
MONDO:0007540 |
OMIM:131100 |
Orphanet:652 |
multiple endocrine neoplasia type 1 |
MONDO:0032611 |
OMIM:618228 |
- |
mitochondrial complex 1 deficiency, nuclear type 6 |
MONDO:0016419 |
OMIM:613399 |
Orphanet:227535 |
hereditary breast carcinoma |
MONDO:0009227 |
OMIM:228550 |
Orphanet:2591 |
myofibromatosis, infantile, 1 |
MONDO:0013977 |
OMIM:614932 |
Orphanet:319514 |
combined oxidative phosphorylation defect type 13 |
MONDO:0008233 |
OMIM:171300 |
Orphanet:29072 |
pheochromocytoma |
MONDO:0020091 |
- |
Orphanet:98343 |
obsolete male infertility due to obstructive azoospermia |
MONDO:0009173 |
OMIM:226200 |
Orphanet:168601 |
congenital enteropathy due to enteropeptidase deficiency |
MONDO:0100294 |
OMIM:252011 |
Orphanet:3208 |
mitochondrial complex II deficiency, nuclear type 1 |
MONDO:0100105 |
OMIM:618360 |
- |
brain small vessel disease 3 |
MONDO:0019434 |
OMIM:604302 |
Orphanet:85414 |
systemic-onset juvenile idiopathic arthritis |
MONDO:0009776 |
OMIM:258150 |
- |
spermatogenic failure 1 |
MONDO:0020723 |
OMIM:264700 |
Orphanet:289157 |
vitamin D-dependent rickets, type 1A |
MONDO:0011518 |
OMIM:605130 |
Orphanet:319182 |
Wiedemann-Steiner syndrome |
MONDO:0005061 |
OMIM:211980 |
Orphanet:415268 |
lung adenocarcinoma |
MONDO:0020333 |
- |
Orphanet:98850 |
aggressive systemic mastocytosis |
MONDO:0010645 |
OMIM:309000 |
Orphanet:534 |
oculocerebrorenal syndrome |
MONDO:0013662 |
OMIM:614266 |
Orphanet:99976 |
Barrett esophagus |
MONDO:0010421 |
OMIM:300755 |
Orphanet:47 |
Bruton-type agammaglobulinemia |
MONDO:0007619 |
OMIM:136000 |
Orphanet:289465 |
isolated congenital adermatoglyphia |
MONDO:0007763 |
OMIM:144700 |
Orphanet:422526 |
nonpapillary renal cell carcinoma |
MONDO:0009728 |
OMIM:615382 |
Orphanet:93592 |
nephronophthisis 1 |
MONDO:0014076 |
OMIM:615190 |
Orphanet:3322 |
dyskeratosis congenita, autosomal recessive 5 |
MONDO:0011680 |
OMIM:606545 |
Orphanet:79394 |
autosomal recessive congenital ichthyosis 3 |
MONDO:0013872 |
OMIM:614731 |
- |
prostate cancer, hereditary, 2 |
MONDO:0014150 |
OMIM:615369 |
Orphanet:2382 |
developmental and epileptic encephalopathy 94 |
MONDO:0013762 |
OMIM:614462 |
Orphanet:401859 |
lipoic acid synthetase deficiency |
MONDO:0008437 |
OMIM:182600 |
Orphanet:100984 |
hereditary spastic paraplegia 3A |
MONDO:0024554 |
OMIM:600721 |
Orphanet:79315 |
D-2-hydroxyglutaric aciduria 1 |
MONDO:0005097 |
- |
- |
squamous cell lung carcinoma |
MONDO:0033559 |
OMIM:619000 |
- |
intellectual developmental disorder with seizures and language delay |
MONDO:0014587 |
OMIM:616325 |
Orphanet:590 |
congenital myasthenic syndrome 9 |
MONDO:0012545 |
OMIM:610717 |
Orphanet:98908 |
neutral lipid storage myopathy |
MONDO:0013438 |
OMIM:613811 |
Orphanet:2524 |
pontocerebellar hypoplasia type 2D |
MONDO:0008847 |
OMIM:209500 |
Orphanet:86819 |
atrichia with papular lesions |
MONDO:0014630 |
OMIM:616415 |
Orphanet:454840 |
NTHL1-related attenuated familial adenomatous polyposis |
MONDO:0016396 |
OMIM:616081 |
Orphanet:2254 |
pontocerebellar hypoplasia type 1 |
MONDO:0009047 |
OMIM:219050 |
- |
cryptorchidism |
MONDO:0011086 |
OMIM:601457 |
Orphanet:331206 |
severe combined immunodeficiency, autosomal recessive, T cell-negative, B cell-negative, NK cell-positive |
MONDO:0009259 |
OMIM:230450 |
Orphanet:33574 |
gamma-glutamylcysteine synthetase deficiency |
MONDO:0014267 |
OMIM:615592 |
Orphanet:397787 |
severe combined immunodeficiency due to IKK2 deficiency |
MONDO:0008319 |
OMIM:177000 |
Orphanet:79278 |
protoporphyria, erythropoietic, 1 |
MONDO:0013418 |
OMIM:613780 |
Orphanet:91387 |
aortic aneurysm, familial thoracic 7 |
MONDO:0020845 |
OMIM:618098 |
- |
progressive external ophthalmoplegia with mitochondrial DNA deletions, autosomal recessive 5 |
MONDO:0001149 |
OMIM:612703 |
- |
microcephaly |
MONDO:0033092 |
OMIM:617574 |
- |
ichthyosis, congenital, autosomal recessive 13 |
MONDO:0012561 |
OMIM:610805 |
- |
congenital anomalies of kidney and urinary tract 1 |
MONDO:0018825 |
- |
Orphanet:481152 |
PYCR2-related microcephaly-progressive leukoencephalopathy |
MONDO:0017148 |
- |
Orphanet:275777 |
heritable pulmonary arterial hypertension |
MONDO:0020849 |
OMIM:618108 |
- |
immunodeficiency 57 |
MONDO:0011236 |
OMIM:602485 |
Orphanet:79299 |
hyperinsulinism due to glucokinase deficiency |
MONDO:0010404 |
OMIM:300703 |
Orphanet:314978 |
X-linked non progressive cerebellar ataxia |
MONDO:0012594 |
OMIM:610984 |
Orphanet:200418 |
complement factor I deficiency |
MONDO:0010196 |
OMIM:277700 |
Orphanet:902 |
Werner syndrome |
MONDO:0010005 |
OMIM:268700 |
Orphanet:3124 |
saccharopinuria |
MONDO:0011533 |
OMIM:605282 |
Orphanet:363417 |
temtamy preaxial brachydactyly syndrome |
MONDO:0018314 |
- |
Orphanet:391316 |
infantile-onset mesial temporal lobe epilepsy with severe cognitive regression |
MONDO:0013777 |
OMIM:614491 |
Orphanet:88939 |
pseudohypoaldosteronism type 2B |
MONDO:0033621 |
OMIM:619042 |
- |
spinal muscular atrophy, infantile, James type |
MONDO:0009271 |
OMIM:231070 |
Orphanet:2078 |
geroderma osteodysplastica |
MONDO:0014876 |
OMIM:617028 |
- |
intellectual disability, autosomal recessive 54 |
MONDO:0013059 |
OMIM:612952 |
Orphanet:51 |
Aicardi-Goutieres syndrome 5 |
MONDO:0030018 |
OMIM:618852 |
- |
autoinflammation with episodic fever and lymphadenopathy |
MONDO:0012472 |
OMIM:610333 |
Orphanet:51 |
Aicardi-Goutieres syndrome 4 |
MONDO:0011035 |
OMIM:601321 |
Orphanet:638 |
neurofibromatosis-Noonan syndrome |
MONDO:0008316 |
OMIM:176860 |
Orphanet:745 |
thrombophilia due to protein C deficiency, autosomal dominant |
MONDO:0008879 |
OMIM:211180 |
Orphanet:1270 |
Bowen-Conradi syndrome |
MONDO:0014906 |
OMIM:617087 |
- |
Charcot-Marie-Tooth disease, axonal, autosomal recessive, type 2a2b; |
MONDO:0016660 |
OMIM:617090 |
Orphanet:2512 |
autosomal recessive primary microcephaly |
MONDO:0014520 |
OMIM:616185 |
Orphanet:444048 |
46,XX ovarian dysgenesis-short stature syndrome |
MONDO:0030843 |
OMIM:619101 |
- |
mismatch repair cancer syndrome 4 |
MONDO:0013740 |
OMIM:614416 |
Orphanet:293925 |
lethal occipital encephalocele-skeletal dysplasia syndrome |
MONDO:0014698 |
OMIM:616577 |
Orphanet:457351 |
microcephaly-intellectual disability-sensorineural hearing loss-epilepsy-abnormal muscle tone syndrome |
MONDO:0019149 |
OMIM:278000 |
Orphanet:75234 |
cholesteryl ester storage disease |
MONDO:0012099 |
OMIM:608688 |
Orphanet:250977 |
AICA-ribosiduria |
MONDO:0014223 |
OMIM:615515 |
Orphanet:803 |
amyotrophic lateral sclerosis type 19 |
MONDO:0019681 |
- |
Orphanet:93399 |
juvenile sialidosis type 2 |
MONDO:0008861 |
OMIM:210200 |
Orphanet:6 |
3-methylcrotonyl-CoA carboxylase 1 deficiency |
MONDO:0016996 |
- |
Orphanet:263665 |
NK-cell enteropathy |
MONDO:0014401 |
OMIM:615923 |
Orphanet:329191 |
tall stature-scoliosis-macrodactyly of the great toes syndrome |
MONDO:0014013 |
OMIM:615026 |
Orphanet:411712 |
maternal riboflavin deficiency |
MONDO:0014042 |
OMIM:615092 |
Orphanet:54260 |
left ventricular noncompaction 7 |
MONDO:0060582 |
OMIM:617717 |
Orphanet:542585 |
auditory neuropathy-optic atrophy syndrome |
MONDO:0033481 |
OMIM:617770 |
Orphanet:589522 |
spinocerebellar ataxia 46 |
MONDO:0017177 |
- |
Orphanet:276280 |
hemihyperplasia-multiple lipomatosis syndrome |
MONDO:0007934 |
OMIM:153870 |
Orphanet:251287 |
benign concentric annular macular dystrophy |
MONDO:0009216 |
OMIM:227810 |
Orphanet:2088 |
glycogen storage disease due to GLUT2 deficiency |
MONDO:0032606 |
OMIM:618222 |
- |
mitochondrial complex 1 deficiency, nuclear type 2 |
MONDO:0013176 |
OMIM:613195 |
Orphanet:363992 |
Weill-Marchesani 4 syndrome, recessive |
MONDO:0008903 |
OMIM:614210 |
- |
lung cancer |
MONDO:0009804 |
OMIM:616229 |
Orphanet:216812 |
osteogenesis imperfecta type 3 |
MONDO:0005212 |
OMIM:268220 |
Orphanet:780 |
rhabdomyosarcoma |
MONDO:0014350 |
OMIM:615807 |
Orphanet:808 |
Seckel syndrome 8 |
MONDO:0013081 |
OMIM:613011 |
Orphanet:538963 |
lymphoproliferative syndrome 1 |
MONDO:0013340 |
OMIM:613643 |
Orphanet:2828 |
Parkinson disease 5, autosomal dominant, susceptibility to |
MONDO:0010572 |
OMIM:304150 |
Orphanet:198 |
occipital horn syndrome |
MONDO:0019391 |
OMIM:616435 |
Orphanet:84 |
Fanconi anemia |
MONDO:0018828 |
OMIM:617397 |
Orphanet:481665 |
pseudo-TORCH syndrome 2 |
MONDO:0013616 |
OMIM:614190 |
Orphanet:189439 |
pigmented nodular adrenocortical disease, primary, 3 |
MONDO:0008876 |
OMIM:210900 |
Orphanet:125 |
Bloom syndrome |
MONDO:0015705 |
OMIM:615959 |
Orphanet:169186 |
autosomal recessive centronuclear myopathy |
MONDO:0013373 |
OMIM:613697 |
- |
dilated cardiomyopathy 1V |
MONDO:0015802 |
- |
Orphanet:178469 |
autosomal dominant non-syndromic intellectual disability |
MONDO:0010015 |
OMIM:269400 |
Orphanet:289499 |
anterior segment dysgenesis 7 |
MONDO:0013403 |
OMIM:613751 |
Orphanet:450 |
heterotaxy, visceral, 4, autosomal |
MONDO:0012392 |
OMIM:610006 |
Orphanet:79157 |
2-methylbutyryl-CoA dehydrogenase deficiency |
MONDO:0011873 |
OMIM:607625 |
Orphanet:646 |
Niemann-Pick disease, type C2 |
MONDO:0012596 |
OMIM:610992 |
Orphanet:284417 |
PSAT deficiency |
MONDO:0011225 |
OMIM:603554 |
Orphanet:275 |
severe combined immunodeficiency due to DCLRE1C deficiency |
MONDO:0018274 |
OMIM:609056 |
Orphanet:370938 |
GM3 synthase deficiency |
MONDO:0100245 |
- |
Orphanet:447 |
acquired paroxysmal nocturnal hemoglobinuria |
MONDO:0018823 |
- |
Orphanet:480907 |
X-linked intellectual disability-global development delay-facial dysmorphism-sacral caudal remnant syndrome |
MONDO:0013566 |
OMIM:614083 |
- |
Fanconi anemia complementation group L |
MONDO:0014089 |
OMIM:616964 |
Orphanet:352662 |
corneal intraepithelial dyskeratosis-palmoplantar hyperkeratosis-laryngeal dyskeratosis syndrome |
MONDO:0008908 |
OMIM:212066 |
Orphanet:79329 |
MGAT2-CDG |
MONDO:0010469 |
OMIM:300872 |
- |
epsilon-trimethyllysine hydroxylase deficiency |
MONDO:0008393 |
OMIM:180849 |
Orphanet:783 |
Rubinstein-Taybi syndrome due to CREBBP mutations |
MONDO:0008758 |
OMIM:203700 |
Orphanet:726 |
mitochondrial DNA depletion syndrome 4a |
MONDO:0014474 |
OMIM:616052 |
Orphanet:352479 |
autosomal recessive limb-girdle muscular dystrophy type 2U |
MONDO:0011939 |
OMIM:607944 |
Orphanet:50816 |
Spondyloenchondrodysplasia with immune dysregulation |
MONDO:0010823 |
OMIM:600121 |
Orphanet:309803 |
rhizomelic chondrodysplasia punctata type 3 |
MONDO:0010385 |
OMIM:300635 |
Orphanet:538934 |
X-linked lymphoproliferative disease due to XIAP deficiency |
MONDO:0014793 |
OMIM:616834 |
Orphanet:488168 |
microcephaly-congenital cataract-psoriasiform dermatitis syndrome |
MONDO:0009760 |
OMIM:257320 |
Orphanet:89844 |
Norman-Roberts syndrome |
MONDO:0009825 |
OMIM:260005 |
Orphanet:33572 |
5-oxoprolinase deficiency |
MONDO:0014094 |
OMIM:615234 |
Orphanet:300298 |
severe congenital hypochromic anemia with ringed sideroblasts |
MONDO:0007661 |
OMIM:137580 |
Orphanet:856 |
Tourette syndrome |
MONDO:0017053 |
OMIM:248600 |
Orphanet:268173 |
intermittent maple syrup urine disease |
MONDO:0014974 |
OMIM:617223 |
- |
sudden cardiac failure, alcohol-induced |
MONDO:0008779 |
- |
- |
arthrogryposis |
MONDO:0007970 |
OMIM:155950 |
Orphanet:2485 |
melorheostosis |
MONDO:0008783 |
OMIM:205400 |
Orphanet:31150 |
Tangier disease |
MONDO:0020747 |
OMIM:210250 |
- |
sitosterolemia 1 |
MONDO:0008907 |
OMIM:212065 |
Orphanet:79318 |
PMM2-CDG |
MONDO:0014230 |
OMIM:615527 |
- |
candidiasis, familial, 8 |
MONDO:0009505 |
OMIM:245450 |
- |
lactic aciduria due to D-lactic acid |
MONDO:0013700 |
OMIM:614338 |
Orphanet:309111 |
pancreatic triacylglycerol lipase deficiency |
MONDO:0012064 |
OMIM:616462 |
Orphanet:1200 |
choanal atresia-hearing loss-cardiac defects-craniofacial dysmorphism syndrome |
MONDO:0009461 |
OMIM:243060 |
Orphanet:399808 |
male infertility due to large-headed multiflagellar polyploid spermatozoa |
MONDO:0044705 |
- |
Orphanet:500464 |
paranasal sinus squamous cell carcinoma |
MONDO:0014533 |
OMIM:616211 |
- |
developmental and epileptic encephalopathy, 28 |
MONDO:0010939 |
OMIM:600803 |
Orphanet:69663 |
low phospholipid associated cholelithiasis |
MONDO:0008218 |
OMIM:169600 |
Orphanet:2841 |
Hailey-Hailey disease |
MONDO:0012056 |
OMIM:608553 |
Orphanet:65 |
Leber congenital amaurosis 9 |
MONDO:0009218 |
OMIM:228000 |
Orphanet:333 |
Farber lipogranulomatosis |
MONDO:0013324 |
OMIM:613611 |
Orphanet:99141 |
lymphedema-posterior choanal atresia syndrome |
MONDO:0007351 |
OMIM:120300 |
Orphanet:98945 |
coloboma of macula |
MONDO:0009284 |
OMIM:231900 |
Orphanet:32 |
glutathione synthetase deficiency without 5-oxoprolinuria |
MONDO:0044326 |
OMIM:617836 |
- |
developmental delay and seizures with or without movement abnormalities |
MONDO:0005298 |
OMIM:166710 |
- |
osteoporosis |
MONDO:0014332 |
OMIM:615751 |
Orphanet:401948 |
hyperammonemic encephalopathy due to carbonic anhydrase VA deficiency |
MONDO:0009517 |
OMIM:246200 |
Orphanet:508 |
Donohue syndrome |
MONDO:0012153 |
OMIM:608907 |
Orphanet:1020 |
Alzheimer disease 9 |
MONDO:0005712 |
OMIM:614826 |
Orphanet:651 |
congenital nystagmus |
MONDO:0019732 |
- |
Orphanet:93561 |
ALys amyloidosis |
MONDO:0010547 |
OMIM:302500 |
Orphanet:1175 |
X-linked progressive cerebellar ataxia |
MONDO:0013364 |
OMIM:613684 |
Orphanet:783 |
Rubinstein-Taybi syndrome due to EP300 haploinsufficiency |
MONDO:0014149 |
OMIM:615368 |
Orphanet:363409 |
fetal akinesia-cerebral and retinal hemorrhage syndrome |
MONDO:0013693 |
OMIM:614328 |
Orphanet:294023 |
inflammatory skin and bowel disease, neonatal, 1 |
MONDO:0009734 |
OMIM:256450 |
Orphanet:79643 |
hyperinsulinemic hypoglycemia, familial, 1 |
MONDO:0007478 |
OMIM:127000 |
Orphanet:93325 |
autosomal dominant Kenny-Caffey syndrome |
MONDO:0011628 |
OMIM:606054 |
Orphanet:35 |
propionic acidemia |
MONDO:0010726 |
OMIM:613454 |
Orphanet:778 |
Rett syndrome |
MONDO:0013815 |
OMIM:614592 |
Orphanet:313855 |
FGFR2-related bent bone dysplasia |
MONDO:0013778 |
OMIM:614492 |
Orphanet:88940 |
pseudohypoaldosteronism type 2C |
MONDO:0014464 |
OMIM:616034 |
Orphanet:431361 |
progressive encephalopathy with leukodystrophy due to DECR deficiency |
MONDO:0032526 |
OMIM:618093 |
- |
spinocerebellar ataxia 48 |
MONDO:0009165 |
OMIM:225750 |
Orphanet:51 |
Aicardi-Goutieres syndrome 1 |
MONDO:0011223 |
OMIM:602433 |
Orphanet:357043 |
amyotrophic lateral sclerosis type 4 |
MONDO:0016307 |
- |
Orphanet:216975 |
Niemann-Pick disease type C, severe early infantile neurologic onset |
MONDO:0011614 |
OMIM:605911 |
Orphanet:35701 |
3-hydroxy-3-methylglutaryl-CoA synthase deficiency |
MONDO:0014820 |
OMIM:616896 |
- |
mitochondrial DNA depletion syndrome 14 (cardioencephalomyopathic type) |
MONDO:0010080 |
OMIM:500003 |
Orphanet:225154 |
familial infantile bilateral striatal necrosis |
MONDO:0013920 |
OMIM:614849 |
Orphanet:1930 |
herpes simplex encephalitis, susceptibility to, 3 |
MONDO:0010983 |
OMIM:601042 |
Orphanet:53583 |
dystonia 9 |
MONDO:0009364 |
OMIM:236670 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A1 |
MONDO:0007485 |
OMIM:127550 |
Orphanet:1775 |
dyskeratosis congenita, autosomal dominant 1 |
MONDO:0015177 |
OMIM:613073 |
Orphanet:1040 |
metaphyseal anadysplasia |
MONDO:0008807 |
OMIM:207720 |
- |
apnea, central sleep |
MONDO:0008438 |
OMIM:182601 |
Orphanet:100985 |
hereditary spastic paraplegia 4 |
MONDO:0007256 |
OMIM:114550 |
Orphanet:88673 |
hepatocellular carcinoma |
MONDO:0009211 |
OMIM:227500 |
Orphanet:327 |
congenital factor VII deficiency |
MONDO:0005105 |
OMIM:155755 |
Orphanet:411533 |
melanoma |
MONDO:0018636 |
- |
Orphanet:444463 |
autoimmune hemolytic anemia-autoimmune thrombocytopenia-primary immunodeficiency syndrome |
MONDO:0009846 |
OMIM:260800 |
Orphanet:2843 |
pentosuria |
MONDO:0007495 |
OMIM:128230 |
Orphanet:98808 |
dystonia 5 |
MONDO:0011964 |
OMIM:608093 |
Orphanet:86309 |
DPAGT1-CDG |
MONDO:0019659 |
- |
Orphanet:93258 |
Pfeiffer syndrome type 1 |
MONDO:0009251 |
OMIM:229700 |
Orphanet:348 |
fructose-1,6-bisphosphatase deficiency |
MONDO:0010038 |
OMIM:270450 |
Orphanet:73273 |
growth delay due to insulin-like growth factor I resistance |
MONDO:0012166 |
OMIM:608984 |
- |
autosomal dominant sensory ataxia 1 |
MONDO:0018136 |
- |
Orphanet:352734 |
minimal pigment oculocutaneous albinism type 1 |
MONDO:0010187 |
OMIM:607473 |
Orphanet:98434 |
vitamin K-dependent clotting factors, combined deficiency of, type 1 |
MONDO:0012553 |
OMIM:610756 |
Orphanet:191 |
cerebrooculofacioskeletal syndrome 2 |
MONDO:0010747 |
OMIM:314250 |
Orphanet:53351 |
X-linked dystonia-parkinsonism |
MONDO:0014518 |
OMIM:616176 |
Orphanet:438207 |
platelet-type bleeding disorder 19 |
MONDO:0032908 |
OMIM:618774 |
- |
CEBALID syndrome |
MONDO:0010854 |
OMIM:600268 |
Orphanet:3339 |
Toriello-Lacassie-Droste syndrome |
MONDO:0032765 |
OMIM:618462 |
- |
bleeding disorder, platelet-type, 22 |
MONDO:0014105 |
OMIM:615269 |
- |
hypogonadotropic hypogonadism 19 with or without anosmia |
MONDO:0016573 |
- |
Orphanet:243367 |
acute fatty liver of pregnancy |
MONDO:0009597 |
OMIM:250400 |
Orphanet:2501 |
metaphyseal chondrodysplasia, Spahr type |
MONDO:0018761 |
- |
Orphanet:466962 |
SMARCA4-deficient sarcoma of thorax |
MONDO:0016600 |
- |
Orphanet:247546 |
acute neonatal citrullinemia type I |
MONDO:0011258 |
OMIM:602588 |
Orphanet:52429 |
branchiootic syndrome 1 |
MONDO:0044312 |
OMIM:617425 |
- |
immunoskeletal dysplasia with neurodevelopmental abnormalities |
MONDO:0014507 |
OMIM:616145 |
Orphanet:1388 |
Catel-Manzke syndrome |
MONDO:0014115 |
OMIM:615281 |
Orphanet:363412 |
hypomyelination with brain stem and spinal cord involvement and leg spasticity |
MONDO:0007812 |
OMIM:146750 |
Orphanet:313 |
ichthyosis, lamellar, autosomal dominant |
MONDO:0011229 |
OMIM:602473 |
Orphanet:51188 |
ethylmalonic encephalopathy |
MONDO:0018321 |
OMIM:615530 |
Orphanet:391411 |
atypical juvenile parkinsonism |
MONDO:0030048 |
OMIM:618892 |
- |
harderoporphyria |
MONDO:0019392 |
- |
Orphanet:840 |
syringocystadenoma papilliferum |
MONDO:0017992 |
OMIM:615895 |
Orphanet:329173 |
autoinflammatory syndrome with pyogenic bacterial infection and amylopectinosis |
MONDO:0010417 |
OMIM:300749 |
Orphanet:163937 |
syndromic X-linked intellectual disability Najm type |
MONDO:0009715 |
OMIM:255700 |
Orphanet:614 |
myotonia congenita, autosomal recessive |
MONDO:0009020 |
OMIM:217800 |
Orphanet:98969 |
macular corneal dystrophy |
MONDO:0015238 |
OMIM:603457 |
Orphanet:1135 |
arrhinia-choanal atresia-microphthalmia syndrome |
MONDO:0009019 |
OMIM:217700 |
Orphanet:293603 |
congenital hereditary endothelial dystrophy of cornea |
MONDO:0007843 |
OMIM:147920 |
Orphanet:2322 |
Kabuki syndrome 1 |
MONDO:0013761 |
OMIM:614458 |
Orphanet:293955 |
childhood encephalopathy due to thiamine pyrophosphokinase deficiency |
MONDO:0015993 |
OMIM:616502 |
Orphanet:1872 |
cone-rod dystrophy |
MONDO:0014392 |
OMIM:615905 |
Orphanet:442835 |
developmental and epileptic encephalopathy, 25 |
MONDO:0014835 |
OMIM:616922 |
- |
striatal degeneration, autosomal dominant 2 |
MONDO:0013755 |
OMIM:614438 |
Orphanet:2962 |
PYCR1-related de Barsy syndrome |
MONDO:0014114 |
OMIM:615280 |
Orphanet:1340 |
cardiofaciocutaneous syndrome 4 |
MONDO:0010524 |
OMIM:301310 |
Orphanet:2802 |
X-linked sideroblastic anemia with ataxia |
MONDO:0012664 |
OMIM:611390 |
Orphanet:314603 |
spastic ataxia 3 |
MONDO:0007564 |
OMIM:132600 |
Orphanet:91414 |
pilomatrixoma |
MONDO:0008148 |
OMIM:616507 |
Orphanet:216820 |
osteogenesis imperfecta type 4 |
MONDO:0014058 |
OMIM:615139 |
Orphanet:352712 |
facial dysmorphism-immunodeficiency-livedo-short stature syndrome |
MONDO:0030920 |
OMIM:617799 |
Orphanet:178469 |
intellectual disability, autosomal dominant 54 |
MONDO:0013873 |
OMIM:614732 |
Orphanet:85173 |
IMAGe syndrome |
MONDO:0010884 |
OMIM:600416 |
Orphanet:269 |
muscular dystrophy, scapulohumeral |
MONDO:0011464 |
OMIM:604432 |
Orphanet:98767 |
spinocerebellar ataxia type 11 |
MONDO:0017152 |
- |
Orphanet:275803 |
obsolete pulmonary arterial hypertension associated with congenital heart disease |
MONDO:0018907 |
- |
Orphanet:54595 |
craniopharyngioma |
MONDO:0014816 |
OMIM:616890 |
Orphanet:488232 |
split-foot malformation-mesoaxial polydactyly syndrome |
MONDO:0014236 |
OMIM:615539 |
Orphanet:2953 |
Ehlers-Danlos syndrome, musculocontractural type 2 |
MONDO:0009061 |
OMIM:219700 |
Orphanet:586 |
cystic fibrosis |
MONDO:0007216 |
OMIM:112600 |
Orphanet:93396 |
brachydactyly type A2 |
MONDO:0034143 |
- |
Orphanet:556985 |
early-onset calcifying leukoencephalopathy-skeletal dysplasia |
MONDO:0020512 |
- |
Orphanet:99861 |
precursor T-cell acute lymphoblastic leukemia |
MONDO:0013163 |
OMIM:613159 |
Orphanet:655 |
nephronophthisis-like nephropathy 1 |
MONDO:0032631 |
OMIM:618248 |
- |
mitochondrial complex 1 deficiency, nuclear type 27 |
MONDO:0011191 |
OMIM:602089 |
Orphanet:91415 |
capillary infantile hemangioma |
MONDO:0011443 |
OMIM:604352 |
- |
febrile seizures, familial, 4 |
MONDO:0017317 |
- |
Orphanet:2874 |
phakomatosis pigmentokeratotica |
MONDO:0007585 |
OMIM:133700 |
Orphanet:321 |
exostoses, multiple, type 1 |
MONDO:0010472 |
OMIM:300884 |
Orphanet:324422 |
developmental and epileptic encephalopathy, 36 |
MONDO:0012084 |
OMIM:608643 |
Orphanet:35708 |
aromatic L-amino acid decarboxylase deficiency |
MONDO:0032800 |
OMIM:618529 |
- |
robinow syndrome, autosomal recessive 2 |
MONDO:0007067 |
OMIM:102900 |
- |
pyruvate kinase hyperactivity |
MONDO:0033630 |
OMIM:619056 |
- |
neurodevelopmental disorder with speech impairment and dysmorphic facies |
MONDO:0010099 |
OMIM:272750 |
Orphanet:309246 |
Tay-Sachs disease AB variant |
MONDO:0014846 |
OMIM:616949 |
Orphanet:404493 |
autosomal recessive cerebellar ataxia - epilepsy - intellectual disability syndrome due to TUD deficiency |
MONDO:0013204 |
OMIM:613268 |
Orphanet:98974 |
corneal dystrophy, Fuchs endothelial, 4 |
MONDO:0008086 |
OMIM:162400 |
Orphanet:36386 |
neuropathy, hereditary sensory and autonomic, type 1A |
MONDO:0010498 |
OMIM:300960 |
Orphanet:401973 |
MEND syndrome |
MONDO:0018142 |
OMIM:266150 |
Orphanet:353314 |
pyruvate carboxylase deficiency, severe neonatal type |
MONDO:0013345 |
OMIM:613657 |
Orphanet:79315 |
d-2-hydroxyglutaric aciduria 2 |
MONDO:0010526 |
OMIM:301500 |
Orphanet:324 |
Fabry disease |
MONDO:0017267 |
OMIM:606545 |
Orphanet:281122 |
self-healing collodion baby |
MONDO:0014152 |
OMIM:615373 |
Orphanet:54260 |
left ventricular noncompaction 8 |
MONDO:0017694 |
- |
Orphanet:308552 |
glycogen storage disease due to acid maltase deficiency, infantile onset |
MONDO:0009126 |
OMIM:223400 |
Orphanet:1203 |
duodenal atresia |
MONDO:0013051 |
OMIM:612940 |
Orphanet:357064 |
autosomal recessive cutis laxa type 2B |
MONDO:0019181 |
OMIM:309549 |
Orphanet:777 |
non-syndromic X-linked intellectual disability |
MONDO:0011897 |
OMIM:607694 |
Orphanet:88637 |
leukoencephalopathy-ataxia-hypodontia-hypomyelination syndrome |
MONDO:0014336 |
OMIM:615761 |
Orphanet:404440 |
intellectual disability-facial dysmorphism syndrome due to SETD5 haploinsufficiency |
MONDO:0009511 |
OMIM:245600 |
Orphanet:284139 |
Larsen-like syndrome, B3GAT3 type |
MONDO:0018418 |
- |
Orphanet:401815 |
autosomal recessive spastic paraplegia type 66 |
MONDO:0014265 |
OMIM:615590 |
- |
Alzheimer disease 18 |
MONDO:0017724 |
- |
Orphanet:309178 |
Tay-Sachs disease, b variant, infantile form |
MONDO:0013050 |
OMIM:612938 |
Orphanet:210144 |
lethal polymalformative syndrome, Boissel type |
MONDO:0013293 |
OMIM:613517 |
Orphanet:2542 |
isolated microphthalmia 6 |
MONDO:0014547 |
OMIM:616239 |
Orphanet:444458 |
combined oxidative phosphorylation defect type 24 |
MONDO:0007390 |
OMIM:122700 |
- |
coumarin resistance |
MONDO:0060621 |
OMIM:617802 |
- |
neurodevelopmental disorder with microcephaly, seizures, and cortical atrophy |
MONDO:0009580 |
OMIM:249500 |
- |
intellectual disability, autosomal recessive 1 |
MONDO:0033203 |
OMIM:617575 |
Orphanet:506334 |
nephrotic syndrome 14 |
MONDO:0017219 |
OMIM:610829 |
Orphanet:280200 |
microform holoprosencephaly |
MONDO:0014431 |
OMIM:615980 |
Orphanet:435660 |
LIPE-related familial partial lipodystrophy |
MONDO:0009818 |
OMIM:267200 |
Orphanet:2785 |
autosomal recessive osteopetrosis 3 |
MONDO:0012422 |
OMIM:610155 |
- |
type 1 diabetes mellitus 19 |
MONDO:0010286 |
OMIM:300263 |
Orphanet:85287 |
syndromic X-linked intellectual disability Siderius type |
MONDO:0033683 |
- |
Orphanet:508542 |
congenital progressive bone marrow failure-B-cell immunodeficiency-skeletal dysplasia syndrome |
MONDO:0012683 |
OMIM:611523 |
Orphanet:166073 |
pontocerebellar hypoplasia type 6 |
MONDO:0008150 |
OMIM:166250 |
Orphanet:2645 |
osteoglophonic dwarfism |
MONDO:0009855 |
OMIM:261515 |
Orphanet:300 |
d-bifunctional protein deficiency |
MONDO:0012031 |
OMIM:608404 |
- |
platelet-type bleeding disorder 10 |
MONDO:0014805 |
OMIM:616863 |
Orphanet:500055 |
Hao-Fountain syndrome |
MONDO:0014561 |
OMIM:616271 |
Orphanet:445038 |
3-methylglutaconic aciduria with cataracts, neurologic involvement and neutropenia |
MONDO:0030055 |
OMIM:618912 |
- |
sorbitol dehydrogenase deficiency with peripheral neuropathy |
MONDO:0017296 |
OMIM:307030 |
Orphanet:284414 |
glycerol kinase deficiency, adult form |
MONDO:0010108 |
OMIM:300228 |
Orphanet:99865 |
testicular germ cell tumor |
MONDO:0014455 |
OMIM:616007 |
Orphanet:436174 |
cataract-growth hormone deficiency-sensory neuropathy-sensorineural hearing loss-skeletal dysplasia syndrome |
MONDO:0012791 |
OMIM:612073 |
Orphanet:254803 |
mitochondrial DNA depletion syndrome, encephalomyopathic form with methylmalonic aciduria |
MONDO:0004585 |
- |
- |
polyhydramnios |
MONDO:0011951 |
OMIM:608030 |
Orphanet:803 |
amyotrophic lateral sclerosis type 6 |
MONDO:0014352 |
OMIM:615812 |
- |
abdominal obesity-metabolic syndrome 3 |
MONDO:0032662 |
OMIM:618295 |
- |
intellectual developmental disorder, autosomal recessive 67 |
MONDO:0005290 |
- |
- |
rhabdomyolysis |
MONDO:0012805 |
OMIM:612126 |
Orphanet:98811 |
childhood onset GLUT1 deficiency syndrome 2 |
MONDO:0020721 |
OMIM:300751 |
Orphanet:75563 |
X-linked sideroblastic anemia 1 |
MONDO:0014258 |
OMIM:615574 |
Orphanet:391376 |
congenital microcephaly - severe encephalopathy - progressive cerebral atrophy syndrome |
MONDO:0032815 |
OMIM:618567 |
- |
mitochondrial DNA depletion syndrome 17 |
MONDO:0018656 |
OMIM:607694 |
Orphanet:447896 |
tremor-ataxia-central hypomyelination syndrome |
MONDO:0023691 |
OMIM:248600 |
- |
maple syrup urine disease type 1A |
MONDO:0007154 |
OMIM:108010 |
Orphanet:46724 |
arteriovenous malformations of the brain |
MONDO:0032685 |
OMIM:618339 |
- |
infantile cataract, skin abnormalities, glutamate excess, and impaired intellectual development |
MONDO:0019487 |
- |
Orphanet:86911 |
epilepsy with myoclonic absences |
MONDO:0010880 |
OMIM:600376 |
Orphanet:774 |
telangiectasia, hereditary hemorrhagic, type 2 |
MONDO:0015884 |
OMIM:614940 |
Orphanet:1810 |
autosomal dominant hypohidrotic ectodermal dysplasia |
MONDO:0018045 |
OMIM:616553 |
Orphanet:3322 |
Hoyeraal-Hreidarsson syndrome |
MONDO:0032914 |
OMIM:618781 |
- |
ciliary dyskinesia, primary, 44 |
MONDO:0009999 |
OMIM:268310 |
Orphanet:97360 |
autosomal recessive Robinow syndrome |
MONDO:0030012 |
OMIM:618846 |
- |
Diets-Jongmans syndrome |
MONDO:0008913 |
OMIM:212093 |
- |
cardiac valvular defect, developmental |
MONDO:0018277 |
OMIM:615351 |
Orphanet:370959 |
congenital muscular dystrophy with cerebellar involvement |
MONDO:0100296 |
OMIM:614594 |
Orphanet:659 |
Olmsted syndrome 1 |
MONDO:0012592 |
OMIM:610968 |
Orphanet:666 |
osteogenesis imperfecta type 11 |
MONDO:0014751 |
OMIM:616728 |
Orphanet:477993 |
palatal anomalies-widely spaced teeth-facial dysmorphism-developmental delay syndrome |
MONDO:0014335 |
OMIM:615760 |
Orphanet:404437 |
diffuse cerebral and cerebellar atrophy - intractable seizures - progressive microcephaly syndrome |
MONDO:0012241 |
OMIM:609286 |
Orphanet:254892 |
progressive external ophthalmoplegia with mitochondrial DNA deletions, autosomal dominant 3 |
MONDO:0009295 |
OMIM:232800 |
Orphanet:371 |
glycogen storage disease VII |
MONDO:0011707 |
OMIM:606703 |
Orphanet:324588 |
familial dyskinesia and facial myokymia |
MONDO:0007566 |
OMIM:132800 |
Orphanet:65748 |
multiple self-healing squamous epithelioma |
MONDO:0008053 |
OMIM:160700 |
- |
myopia 2, autosomal dominant |
MONDO:0008955 |
OMIM:214150 |
Orphanet:191 |
cerebrooculofacioskeletal syndrome 1 |
MONDO:0007572 |
OMIM:133100 |
Orphanet:90042 |
primary familial polycythemia due to EPO receptor mutation |
MONDO:0010194 |
OMIM:277600 |
Orphanet:3449 |
Weill-Marchesani syndrome 1 |
MONDO:0011895 |
OMIM:607685 |
Orphanet:3260 |
idiopathic hypereosinophilic syndrome |
MONDO:0008703 |
OMIM:609441 |
Orphanet:2098 |
acromesomelic dysplasia 2A |
MONDO:0020837 |
OMIM:617996 |
- |
oocyte maturation defect 5 |
MONDO:0008146 |
OMIM:166230 |
Orphanet:216796 |
osteogenesis imperfecta type 1 |
MONDO:0010209 |
OMIM:278300 |
Orphanet:93601 |
xanthinuria type I |
MONDO:0007573 |
OMIM:133180 |
Orphanet:318 |
acute erythroleukemia, familial |
MONDO:0013838 |
OMIM:614652 |
Orphanet:255249 |
coenzyme Q10 deficiency, primary, 3 |
MONDO:0020493 |
OMIM:209880 |
Orphanet:99803 |
Haddad syndrome |
MONDO:0007104 |
OMIM:105500 |
Orphanet:90020 |
amyotrophic lateral sclerosis-parkinsonism-dementia complex |
MONDO:0019203 |
OMIM:178500 |
Orphanet:79126 |
acute interstitial pneumonia |
MONDO:0014870 |
OMIM:617022 |
Orphanet:464366 |
NEK9-related lethal skeletal dysplasia |
MONDO:0032697 |
OMIM:618354 |
- |
neurodevelopmental disorder and language delay with or without structural brain abnormalities |
MONDO:0016315 |
- |
Orphanet:217085 |
mucopolysaccharidosis type 2, severe form |
MONDO:0011804 |
OMIM:607271 |
Orphanet:275517 |
autoimmune lymphoproliferative syndrome type 2B |
MONDO:0032909 |
OMIM:618775 |
- |
mitochondrial complex 3 deficiency, nuclear type 10 |
MONDO:0030963 |
OMIM:619189 |
- |
Li-Campeau syndrome |
MONDO:0009268 |
OMIM:231005 |
Orphanet:355 |
Gaucher disease-ophthalmoplegia-cardiovascular calcification syndrome |
MONDO:0012784 |
OMIM:612016 |
Orphanet:139485 |
autosomal recessive ataxia due to ubiquinone deficiency |
MONDO:0014220 |
OMIM:615511 |
Orphanet:45 |
myopathy due to myoadenylate deaminase deficiency |
MONDO:0015699 |
OMIM:614380 |
Orphanet:169147 |
immunodeficiency due to a classical component pathway complement deficiency |
MONDO:0009614 |
OMIM:251110 |
Orphanet:79311 |
vitamin B12-responsive methylmalonic acidemia type cblB |
MONDO:0007417 |
OMIM:124200 |
Orphanet:218 |
Darier disease |
MONDO:0044648 |
- |
Orphanet:496689 |
kyphoscoliosis-lateral tongue atrophy-hereditary spastic paraplegia syndrome |
MONDO:0005377 |
OMIM:615861 |
- |
nephrotic syndrome |
MONDO:0009736 |
OMIM:616038 |
- |
Neu-Laxova syndrome 1 |
MONDO:0012824 |
OMIM:612233 |
Orphanet:280288 |
hypomyelinating leukodystrophy 4 |
MONDO:0015713 |
- |
Orphanet:169615 |
idiopathic central precocious puberty |
MONDO:0009401 |
OMIM:239510 |
Orphanet:79101 |
hyperprolinemia type 2 |
MONDO:0010829 |
OMIM:600142 |
Orphanet:199354 |
CARASIL syndrome |
MONDO:0005036 |
- |
Orphanet:464463 |
gastric adenocarcinoma |
MONDO:0010789 |
OMIM:540000 |
Orphanet:550 |
MELAS syndrome |
MONDO:0020713 |
OMIM:265450 |
- |
pulmonary venoocclusive disease 1 |
MONDO:0032925 |
OMIM:618803 |
- |
respiratory papillomatosis, juvenile recurrent, congenital |
MONDO:0010660 |
OMIM:309549 |
Orphanet:777 |
intellectual disability, X-linked 9 |
MONDO:0014554 |
- |
- |
obsolete infantile multisystem neurologic-endocrine-pancreatic disease |
MONDO:0007453 |
OMIM:125851 |
Orphanet:552 |
maturity-onset diabetes of the young type 2 |
MONDO:0010075 |
OMIM:271640 |
Orphanet:93359 |
spondyloepimetaphyseal dysplasia with joint laxity, type 1, with or without fractures |
MONDO:0032566 |
OMIM:618156 |
- |
squalene synthase deficiency |
MONDO:0005224 |
- |
Orphanet:98833 |
acute myeloblastic leukemia without maturation |
MONDO:0011933 |
OMIM:607906 |
Orphanet:79326 |
ALG2-CDG |
MONDO:0008082 |
OMIM:162300 |
Orphanet:653 |
multiple endocrine neoplasia type 2B |
MONDO:0011751 |
OMIM:606963 |
- |
COPD, severe early onset |
MONDO:0032564 |
OMIM:618154 |
- |
hennekam lymphangiectasia-lymphedema syndrome 3 |
MONDO:0007220 |
OMIM:113000 |
Orphanet:93383 |
brachydactyly type B1 |
MONDO:0018218 |
- |
Orphanet:363969 |
autosomal recessive cerebral atrophy |
MONDO:0017699 |
OMIM:232500 |
Orphanet:308684 |
glycogen storage disease due to glycogen branching enzyme deficiency, childhood combined hepatic and myopathic form |
MONDO:0030907 |
OMIM:300997 |
- |
intellectual disability, X-linked 106 |
MONDO:0009946 |
OMIM:266120 |
Orphanet:35120 |
hemolytic anemia due to pyrimidine 5' nucleotidase deficiency |
MONDO:0013092 |
OMIM:613028 |
Orphanet:182067 |
glioma susceptibility 2 |
MONDO:0002321 |
- |
- |
sensory peripheral neuropathy |
MONDO:0013664 |
OMIM:614279 |
Orphanet:90796 |
46,XY disorder of sex development due to testicular 17,20-desmolase deficiency |
MONDO:0009315 |
OMIM:234000 |
Orphanet:330 |
congenital factor XII deficiency |
MONDO:0009388 |
OMIM:238710 |
Orphanet:2203 |
hyperlysinemia |
MONDO:0009603 |
OMIM:250620 |
Orphanet:88639 |
3-hydroxyisobutyryl-CoA hydrolase deficiency |
MONDO:0010664 |
OMIM:309583 |
Orphanet:3063 |
syndromic X-linked intellectual disability Snyder type |
MONDO:0016674 |
OMIM:616425 |
Orphanet:251510 |
46,XY partial gonadal dysgenesis |
MONDO:0009666 |
OMIM:253270 |
Orphanet:79242 |
holocarboxylase synthetase deficiency |
MONDO:0011144 |
OMIM:601780 |
Orphanet:79262 |
ceroid lipofuscinosis, neuronal, 6A |
MONDO:0013483 |
OMIM:613886 |
- |
obesity, hyperphagia, and developmental delay |
MONDO:0008295 |
OMIM:176090 |
Orphanet:443057 |
sporadic porphyria cutanea tarda |
MONDO:0019005 |
OMIM:615862 |
Orphanet:655 |
nephronophthisis |
MONDO:0030067 |
OMIM:618939 |
- |
treacher collins syndrome 4 |
MONDO:0014702 |
OMIM:616586 |
Orphanet:447760 |
autosomal recessive complex spastic paraplegia type 9B |
MONDO:0014022 |
OMIM:615041 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type a, 10 |
MONDO:0010201 |
OMIM:277950 |
- |
Winchester syndrome |
MONDO:0008290 |
OMIM:175800 |
Orphanet:735 |
porokeratosis 1, Mibelli type |
MONDO:0013760 |
OMIM:614457 |
Orphanet:352333 |
congenital ichthyosis-intellectual disability-spastic quadriplegia syndrome |
MONDO:0007436 |
OMIM:125400 |
Orphanet:99789 |
dentin dysplasia type I |
MONDO:0009258 |
OMIM:230400 |
Orphanet:79239 |
classic galactosemia |
MONDO:0011783 |
OMIM:607143 |
Orphanet:79324 |
ALG12-CDG |
MONDO:0008935 |
OMIM:605672 |
Orphanet:1173 |
cerebellar ataxia-hypogonadism syndrome |
MONDO:0008297 |
OMIM:176200 |
Orphanet:79473 |
variegate porphyria |
MONDO:0010790 |
OMIM:545000 |
Orphanet:551 |
MERRF syndrome |
MONDO:0010523 |
OMIM:301220 |
Orphanet:85453 |
X-linked reticulate pigmentary disorder |
MONDO:0013226 |
OMIM:613328 |
Orphanet:221139 |
combined immunodeficiency with faciooculoskeletal anomalies |
MONDO:0014010 |
OMIM:615023 |
Orphanet:79394 |
autosomal recessive congenital ichthyosis 9 |
MONDO:0032650 |
OMIM:618276 |
- |
neurodegeneration, childhood-onset, with cerebellar atrophy |
MONDO:0019264 |
OMIM:609241 |
Orphanet:79281 |
alpha-N-acetylgalactosaminidase deficiency type 3 |
MONDO:0023113 |
OMIM:114500 |
- |
familial colorectal cancer |
MONDO:0007586 |
OMIM:133701 |
Orphanet:321 |
exostoses, multiple, type 2 |
MONDO:0014487 |
OMIM:616084 |
Orphanet:369861 |
congenital sideroblastic anemia-B-cell immunodeficiency-periodic fever-developmental delay syndrome |
MONDO:0014396 |
OMIM:615916 |
- |
dilated cardiomyopathy 1NN |
MONDO:0008948 |
OMIM:213700 |
Orphanet:909 |
cerebrotendinous xanthomatosis |
MONDO:0012622 |
OMIM:611105 |
Orphanet:137898 |
leukoencephalopathy with brain stem and spinal cord involvement-high lactate syndrome |
MONDO:0030919 |
OMIM:617798 |
Orphanet:178469 |
intellectual disability, autosomal dominant 53 |
MONDO:0032939 |
OMIM:618825 |
- |
intellectual developmental disorder, autosomal dominant 63, with macrocephaly |
MONDO:0020781 |
OMIM:617186 |
Orphanet:555407 |
encephalopathy, progressive, early-onset, with brain edema and/or leukoencephalopathy, 1 |
MONDO:0020341 |
OMIM:617201 |
Orphanet:98892 |
periventricular nodular heterotopia |
MONDO:0007080 |
OMIM:103900 |
Orphanet:403 |
glucocorticoid-remediable aldosteronism |
OMIM:619647 |
OMIM:619647 |
- |
DYSKINESIA WITH OROFACIAL INVOLVEMENT, AUTOSOMAL RECESSIVE |
MONDO:0013186 |
OMIM:613224 |
Orphanet:648 |
Noonan syndrome 6 |
MONDO:0010466 |
OMIM:300868 |
Orphanet:300496 |
multiple congenital anomalies-hypotonia-seizures syndrome 2 |
MONDO:0019261 |
OMIM:256730 |
Orphanet:79263 |
infantile neuronal ceroid lipofuscinosis |
MONDO:0021548 |
OMIM:616509 |
Orphanet:98994 |
total early-onset cataract |
MONDO:0015270 |
OMIM:617936 |
Orphanet:132 |
butyrylcholinesterase deficiency |
MONDO:0014829 |
OMIM:616911 |
- |
immunodeficiency-centromeric instability-facial anomalies syndrome 4 |
MONDO:0011125 |
OMIM:601675 |
Orphanet:670 |
trichothiodystrophy 1, photosensitive |
MONDO:0032655 |
OMIM:618283 |
- |
visual impairment and progressive phthisis bulbi |
MONDO:0015715 |
- |
Orphanet:169793 |
severe hemophilia B |
MONDO:0031007 |
OMIM:619260 |
- |
spondyloepiphyseal dysplasia, sensorineural hearing loss, impaired intellectual development, and leber congenital amaurosis |
MONDO:0054701 |
OMIM:617768 |
- |
Kleefstra syndrome 2 |
MONDO:0015003 |
OMIM:617282 |
Orphanet:508093 |
dystonia, childhood-onset, with optic atrophy and basal ganglia abnormalities |
MONDO:0008865 |
OMIM:210370 |
Orphanet:41751 |
Bietti crystalline corneoretinal dystrophy |
MONDO:0009212 |
OMIM:227600 |
Orphanet:328 |
congenital factor X deficiency |
MONDO:0009240 |
OMIM:229100 |
Orphanet:51208 |
formiminoglutamic aciduria |
MONDO:0010945 |
OMIM:600852 |
- |
retinitis pigmentosa 17 |
MONDO:0030835 |
OMIM:619090 |
- |
developmental delay, impaired growth, dysmorphic facies, and axonal neuropathy |
MONDO:0018338 |
OMIM:616005 |
Orphanet:397596 |
activated PI3K-delta syndrome |
MONDO:0016216 |
- |
Orphanet:210159 |
adult hepatocellular carcinoma |
MONDO:0014028 |
OMIM:615065 |
Orphanet:329457 |
distal arthrogryposis type 5D |
MONDO:0030007 |
OMIM:618838 |
- |
combined oxidative phosphorylation deficiency 41 |
MONDO:0010528 |
OMIM:301700 |
- |
anosmia |
MONDO:0010407 |
OMIM:309590 |
Orphanet:85328 |
intellectual disability, X-linked syndromic, Turner type |
MONDO:0030971 |
OMIM:619220 |
- |
immunodeficiency 78 with autoimmunity and developmental delay |
MONDO:0013659 |
OMIM:614261 |
Orphanet:294016 |
microcephaly-capillary malformation syndrome |
MONDO:0007205 |
OMIM:112250 |
Orphanet:85182 |
diaphyseal medullary stenosis-bone malignancy syndrome |
MONDO:0024532 |
OMIM:166780 |
Orphanet:2792 |
otofaciocervical syndrome 1 |
MONDO:0011485 |
OMIM:604777 |
Orphanet:313 |
autosomal recessive congenital ichthyosis 5 |
MONDO:0013458 |
OMIM:613845 |
Orphanet:363694 |
hyperuricemia-pulmonary hypertension-renal failure-alkalosis syndrome |
MONDO:0024533 |
OMIM:178600 |
Orphanet:422 |
pulmonary hypertension, primary, 1 |
MONDO:0012098 |
OMIM:608687 |
Orphanet:101110 |
spinocerebellar ataxia type 20 |
MONDO:0018939 |
OMIM:615350 |
Orphanet:588 |
muscle-eye-brain disease |
MONDO:0014791 |
OMIM:616831 |
- |
Luscan-Lumish syndrome |
MONDO:0014098 |
OMIM:615238 |
Orphanet:435651 |
CIDEC-related familial partial lipodystrophy |
MONDO:0012256 |
OMIM:609340 |
Orphanet:101008 |
hereditary spastic paraplegia 28 |
MONDO:0014423 |
OMIM:615966 |
Orphanet:317425 |
severe combined immunodeficiency due to DNA-PKcs deficiency |
MONDO:0018422 |
- |
Orphanet:401835 |
autosomal recessive spastic paraplegia type 70 |
MONDO:0007483 |
OMIM:127400 |
Orphanet:41 |
dyschromatosis symmetrica hereditaria |
MONDO:0100345 |
OMIM:223100 |
Orphanet:319681 |
lactose intolerance |
MONDO:0014499 |
OMIM:616116 |
- |
intellectual disability, autosomal recessive 46 |
MONDO:0012231 |
OMIM:609260 |
Orphanet:99947 |
Charcot-Marie-Tooth disease type 2A2 |
MONDO:0032624 |
OMIM:618241 |
- |
mitochondrial complex 1 deficiency, nuclear type 19 |
MONDO:0007900 |
OMIM:151600 |
Orphanet:2387 |
nonsyndromic congenital nail disorder 3 |
MONDO:0011400 |
OMIM:604145 |
- |
dilated cardiomyopathy 1G |
MONDO:0014367 |
OMIM:615846 |
Orphanet:51 |
Aicardi-Goutieres syndrome 7 |
MONDO:0011872 |
OMIM:607624 |
Orphanet:79477 |
Griscelli syndrome type 2 |
MONDO:0007947 |
OMIM:610168 |
Orphanet:558 |
Marfan syndrome |
MONDO:0014962 |
OMIM:617188 |
- |
intellectual disability, autosomal recessive 57 |
MONDO:0009469 |
OMIM:243300 |
Orphanet:99960 |
benign recurrent intrahepatic cholestasis type 1 |
MONDO:0013739 |
OMIM:614415 |
Orphanet:90280 |
chilblain lupus 2 |
MONDO:0007759 |
OMIM:144250 |
- |
hyperlipidemia, familial combined, LPL related |
MONDO:0009283 |
OMIM:231690 |
Orphanet:35706 |
glutaric acidemia type 3 |
MONDO:0012613 |
OMIM:611091 |
- |
intellectual disability, autosomal recessive 5 |
MONDO:0010338 |
OMIM:300489 |
Orphanet:139557 |
X-linked distal spinal muscular atrophy type 3 |
MONDO:0018328 |
OMIM:603813 |
Orphanet:391665 |
homozygous familial hypercholesterolemia |
MONDO:0044626 |
- |
Orphanet:488191 |
female infertility due to oocyte meiotic arrest |
MONDO:0013127 |
OMIM:613091 |
Orphanet:93270 |
asphyxiating thoracic dystrophy 3 |
MONDO:0002442 |
- |
Orphanet:768 |
long QT syndrome |
MONDO:0008566 |
OMIM:188470 |
Orphanet:319487 |
thyroid cancer, nonmedullary, 2 |
MONDO:0014012 |
OMIM:615025 |
Orphanet:329258 |
Charcot-Marie-Tooth disease axonal type 2Q |
MONDO:0011724 |
OMIM:606777 |
Orphanet:71277 |
encephalopathy due to GLUT1 deficiency |
MONDO:0006033 |
- |
Orphanet:497188 |
diffuse intrinsic pontine glioma |
MONDO:0013934 |
OMIM:614868 |
Orphanet:314689 |
combined immunodeficiency due to STK4 deficiency |
MONDO:0010168 |
OMIM:614990 |
Orphanet:886 |
Usher syndrome type 1 |
MONDO:0017116 |
- |
Orphanet:269505 |
congenital communicating hydrocephalus |
MONDO:0010998 |
OMIM:601110 |
Orphanet:79321 |
ALG3-CDG |
MONDO:0018278 |
OMIM:615351 |
Orphanet:370968 |
congenital muscular dystrophy with intellectual disability |
MONDO:0014893 |
OMIM:617062 |
- |
Okur-Chung neurodevelopmental syndrome |
MONDO:0013799 |
OMIM:614546 |
- |
efavirenz, poor metabolism of |
MONDO:0001384 |
- |
- |
myopia |
MONDO:0009567 |
OMIM:248800 |
Orphanet:559 |
Marinesco-Sjogren syndrome |
MONDO:0018494 |
- |
Orphanet:423306 |
microcephaly-short stature-intellectual disability-facial dysmorphism syndrome |
MONDO:0009637 |
OMIM:251900 |
Orphanet:206966 |
inborn mitochondrial myopathy |
MONDO:0012967 |
OMIM:612631 |
Orphanet:86817 |
hemolytic anemia due to adenylate kinase deficiency |
MONDO:0060577 |
OMIM:617709 |
- |
neurodevelopmental disorder with microcephaly, ataxia, and seizures |
MONDO:0012897 |
OMIM:612416 |
Orphanet:329 |
congenital factor XI deficiency |
MONDO:0010143 |
OMIM:275210 |
Orphanet:1662 |
lethal restrictive dermopathy |
MONDO:0012531 |
OMIM:610651 |
Orphanet:910 |
xeroderma pigmentosum group B |
MONDO:0013771 |
OMIM:614480 |
Orphanet:300293 |
transient infantile hypertriglyceridemia and hepatosteatosis |
MONDO:0020853 |
OMIM:618113 |
- |
encephalitis/encephalopathy, mild, with reversible myelin vacuolization |
MONDO:0008221 |
OMIM:170100 |
Orphanet:742 |
prolidase deficiency |
MONDO:0014015 |
OMIM:615030 |
Orphanet:320411 |
hereditary spastic paraplegia 56 |
MONDO:0014978 |
OMIM:617234 |
- |
preimplantation embryonic lethality 2 |
MONDO:0010820 |
OMIM:600116 |
Orphanet:2828 |
autosomal recessive juvenile Parkinson disease 2 |
MONDO:0010471 |
OMIM:300882 |
Orphanet:199 |
Cornelia de Lange syndrome 5 |
MONDO:0044723 |
OMIM:617248 |
Orphanet:505208 |
3-methylglutaconic aciduria type 8 |
MONDO:0054732 |
OMIM:618086 |
- |
spermatogenic failure 28 |
MONDO:0054764 |
OMIM:617917 |
- |
neurodegeneration with brain iron accumulation 8 |
OMIM:619575 |
OMIM:619575 |
- |
DEVELOPMENTAL DELAY WITH OR WITHOUT INTELLECTUAL IMPAIRMENT OR BEHAVIORAL ABNORMALITIES |
MONDO:0011038 |
OMIM:601338 |
Orphanet:1171 |
cerebellar ataxia-areflexia-pes cavus-optic atrophy-sensorineural hearing loss syndrome |
MONDO:0008333 |
OMIM:177850 |
Orphanet:758 |
pseudoxanthoma elasticum, forme fruste |
MONDO:0013695 |
OMIM:614331 |
Orphanet:144 |
colorectal cancer, hereditary nonpolyposis, type 6 |
MONDO:0014758 |
OMIM:616738 |
- |
radioulnar synostosis with amegakaryocytic thrombocytopenia 2 |
MONDO:0013301 |
OMIM:613546 |
Orphanet:91 |
aromatase deficiency |
MONDO:0018310 |
OMIM:604856 |
Orphanet:389 |
Langerhans cell histiocytosis |
MONDO:0011424 |
OMIM:604287 |
Orphanet:139411 |
Carney triad |
MONDO:0014495 |
OMIM:616108 |
Orphanet:436245 |
retinitis pigmentosa-juvenile cataract-short stature-intellectual disability syndrome |
MONDO:0016309 |
- |
Orphanet:216981 |
Niemann-Pick disease type C, juvenile neurologic onset |
MONDO:0013617 |
OMIM:614192 |
- |
obsolete overgrowth-macrocephaly-facial dysmorphism syndrome |
MONDO:0011156 |
OMIM:615878 |
Orphanet:79304 |
progressive familial intrahepatic cholestasis type 2 |
MONDO:0032780 |
OMIM:618493 |
- |
hypotonia, hypoventilation, impaired intellectual development, dysautonomia, epilepsy, and eye abnormalities |
MONDO:0014570 |
OMIM:616287 |
Orphanet:2680 |
lethal congenital contracture syndrome 8 |
MONDO:0015025 |
OMIM:617339 |
- |
developmental and epileptic encephalopathy, 51 |
MONDO:0013571 |
OMIM:614097 |
Orphanet:926 |
acatalasia |
MONDO:0016865 |
- |
Orphanet:261652 |
Kleefstra syndrome due to a point mutation |
MONDO:0014638 |
OMIM:616435 |
- |
Fanconi anemia complementation group T |
MONDO:0009902 |
OMIM:263700 |
Orphanet:79277 |
cutaneous porphyria |
MONDO:0032789 |
OMIM:618504 |
- |
intellectual developmental disorder, autosomal recessive 71 |
MONDO:0009562 |
OMIM:248510 |
Orphanet:118 |
beta-mannosidosis |
MONDO:0009665 |
OMIM:253260 |
Orphanet:79241 |
biotinidase deficiency |
MONDO:0012041 |
OMIM:608456 |
Orphanet:247798 |
MUTYH-related attenuated familial adenomatous polyposis |
MONDO:0034146 |
- |
Orphanet:557056 |
spastic ataxia-dysarthria due to glutaminase deficiency |
MONDO:0030006 |
OMIM:618835 |
Orphanet:570491 |
combined oxidative phosphorylation deficiency 40 |
MONDO:0005015 |
OMIM:612227 |
- |
diabetes mellitus |
MONDO:0007690 |
OMIM:139300 |
Orphanet:178345 |
aromatase excess syndrome |
MONDO:0012197 |
OMIM:614743 |
Orphanet:88 |
idiopathic aplastic anemia |
MONDO:0010898 |
OMIM:616461 |
Orphanet:101046 |
Autosomal dominant epilepsy with auditory features |
MONDO:0012891 |
OMIM:612390 |
Orphanet:2524 |
pontocerebellar hypoplasia type 2C |
MONDO:0020734 |
OMIM:612874 |
Orphanet:45 |
erythrocyte AMP deaminase deficiency |
MONDO:0008858 |
OMIM:210000 |
Orphanet:1239 |
Behr syndrome |
MONDO:0014109 |
OMIM:615273 |
Orphanet:404454 |
NGLY1-deficiency |
MONDO:0032705 |
OMIM:618367 |
Orphanet:597874 |
neurodevelopmental disorder with microcephaly, epilepsy, and hypomyelination |
MONDO:0011093 |
OMIM:601492 |
Orphanet:67041 |
mucopolysaccharidosis type 9 |
MONDO:0018759 |
- |
Orphanet:466921 |
childhood-onset progressive contractures-limb-girdle weakness-muscle dystrophy syndrome |
MONDO:0014644 |
OMIM:616451 |
Orphanet:468661 |
hereditary spastic paraplegia 74 |
MONDO:0014647 |
OMIM:616457 |
Orphanet:448010 |
developmental and epileptic encephalopathy, 50 |
MONDO:0009744 |
OMIM:610127 |
Orphanet:79264 |
neuronal ceroid lipofuscinosis 1 |
MONDO:0008788 |
OMIM:206200 |
Orphanet:209981 |
IRIDA syndrome |
MONDO:0010441 |
OMIM:300831 |
Orphanet:251383 |
CK syndrome |
MONDO:0006040 |
- |
- |
lactic acidosis |
MONDO:0011508 |
OMIM:605027 |
Orphanet:547 |
lymphoma, non-Hodgkin, familial |
MONDO:0014656 |
OMIM:616479 |
Orphanet:329336 |
progressive external ophthalmoplegia with mitochondrial DNA deletions, autosomal recessive 2 |
MONDO:0009345 |
OMIM:235800 |
Orphanet:2157 |
histidinemia |
MONDO:0017051 |
OMIM:248600 |
Orphanet:268145 |
classic maple syrup urine disease |
MONDO:0012091 |
OMIM:608653 |
- |
autosomal recessive nonsyndromic hearing loss 32 |
MONDO:0018266 |
- |
Orphanet:370109 |
ataxia - telangiectasia variant |
MONDO:0009260 |
OMIM:230500 |
Orphanet:79255 |
GM1 gangliosidosis type 1 |
MONDO:0011743 |
OMIM:606889 |
- |
Alzheimer disease 4 |
MONDO:0011198 |
OMIM:602111 |
Orphanet:93356 |
spondyloepimetaphyseal dysplasia, Missouri type |
MONDO:0009066 |
OMIM:219900 |
Orphanet:411634 |
juvenile nephropathic cystinosis |
MONDO:0016369 |
OMIM:268400 |
Orphanet:221016 |
Rothmund-Thomson syndrome type 2 |
MONDO:0011031 |
OMIM:601316 |
- |
autosomal dominant nonsyndromic hearing loss 10 |
MONDO:0014871 |
OMIM:617023 |
- |
retinitis pigmentosa 75 |
MONDO:0007576 |
OMIM:133239 |
Orphanet:99977 |
esophageal cancer |
MONDO:0013972 |
OMIM:614926 |
Orphanet:2855 |
Perrault syndrome 2 |
MONDO:0007646 |
OMIM:137200 |
Orphanet:324442 |
Gamstorp-Wohlfart syndrome |
MONDO:0017304 |
- |
Orphanet:284804 |
ocular albinism |
MONDO:0009296 |
OMIM:232900 |
- |
glycoprotein storage disease |
MONDO:0025351 |
OMIM:301056 |
- |
multiple congenital anomalies-neurodevelopmental syndrome, x-linked |
MONDO:0054680 |
OMIM:617719 |
- |
epiphyseal dysplasia, multiple, 7 |
MONDO:0014113 |
OMIM:615279 |
Orphanet:1340 |
cardiofaciocutaneous syndrome 3 |
MONDO:0017353 |
- |
Orphanet:289857 |
neonatal glycine encephalopathy |
MONDO:0015470 |
OMIM:615916 |
Orphanet:154 |
familial isolated dilated cardiomyopathy |
MONDO:0017939 |
OMIM:602771 |
Orphanet:324604 |
classic multiminicore myopathy |
MONDO:0015679 |
OMIM:612004 |
Orphanet:168629 |
autosomal thrombocytopenia with normal platelets |
MONDO:0010160 |
OMIM:276600 |
Orphanet:28378 |
tyrosinemia type II |
MONDO:0008895 |
OMIM:211800 |
Orphanet:289601 |
hereditary arterial and articular multiple calcification syndrome |
MONDO:0013076 |
OMIM:613003 |
- |
attention deficit-hyperactivity disorder, susceptibility to, 7 |
MONDO:0013371 |
OMIM:613694 |
Orphanet:154 |
dilated cardiomyopathy 1U |
MONDO:0012307 |
OMIM:609579 |
Orphanet:168624 |
familial scaphocephaly syndrome, McGillivray type |
MONDO:0020355 |
- |
Orphanet:98943 |
coloboma of eye lens |
MONDO:0020632 |
OMIM:618012 |
- |
epileptic encephalopathy, infantile or early childhood, 3 |
MONDO:0044657 |
OMIM:617017 |
Orphanet:497757 |
MME-related autosomal dominant Charcot Marie Tooth disease type 2 |
MONDO:0011346 |
OMIM:603592 |
Orphanet:93602 |
xanthinuria type II |
MONDO:0007492 |
OMIM:602554 |
Orphanet:256 |
early-onset generalized limb-onset dystonia |
MONDO:0019549 |
- |
Orphanet:90118 |
severe early-onset axonal neuropathy due to MFN2 deficiency |
MONDO:0012860 |
OMIM:612304 |
Orphanet:745 |
thrombophilia due to protein C deficiency, autosomal recessive |
MONDO:0009970 |
OMIM:267430 |
Orphanet:97369 |
renal tubular dysgenesis of genetic origin |
MONDO:0015275 |
OMIM:600309 |
Orphanet:1330 |
partial atrioventricular canal |
MONDO:0007738 |
OMIM:143095 |
Orphanet:263463 |
spondyloepiphyseal dysplasia with congenital joint dislocations |
MONDO:0013978 |
OMIM:614934 |
- |
autosomal recessive nonsyndromic hearing loss 70 |
MONDO:0032643 |
OMIM:618266 |
- |
pontocerebellar hypoplasia, type 12 |
MONDO:0024528 |
OMIM:157640 |
Orphanet:254892 |
progressive external ophthalmoplegia with mitochondrial DNA deletions, autosomal dominant 1 |
MONDO:0018996 |
OMIM:606002 |
Orphanet:64753 |
spinocerebellar ataxia, autosomal recessive, with axonal neuropathy 2 |
MONDO:0011740 |
OMIM:606864 |
Orphanet:97286 |
Carney-Stratakis syndrome |
MONDO:0015004 |
OMIM:617284 |
Orphanet:589618 |
dystonia 28, childhood-onset |
MONDO:0017831 |
- |
Orphanet:314918 |
mild Canavan disease |
MONDO:0011027 |
OMIM:601283 |
- |
diabetes mellitus, noninsulin-dependent, 1 |
MONDO:0033091 |
OMIM:617571 |
- |
ichthyosis, congenital, autosomal recessive 14 |
MONDO:0013728 |
OMIM:614390 |
- |
pregnancy loss, recurrent, susceptibility to, 2 |
MONDO:0019306 |
OMIM:615024 |
Orphanet:79394 |
congenital non-bullous ichthyosiform erythroderma |
MONDO:0019148 |
OMIM:278000 |
Orphanet:75233 |
Wolman disease |
MONDO:0014753 |
OMIM:617302 |
Orphanet:98676 |
autosomal recessive optic atrophy |
MONDO:0012581 |
OMIM:610915 |
Orphanet:666 |
osteogenesis imperfecta type 8 |
MONDO:0009609 |
OMIM:250940 |
Orphanet:622 |
methylcobalamin deficiency type cblG |
MONDO:0044332 |
- |
Orphanet:494541 |
childhood-onset benign chorea with striatal involvement |
MONDO:0009556 |
OMIM:248360 |
Orphanet:943 |
malonic aciduria |
MONDO:0010437 |
OMIM:300816 |
Orphanet:238329 |
severe X-linked mitochondrial encephalomyopathy |
MONDO:0014317 |
OMIM:615715 |
Orphanet:401764 |
pancytopenia-developmental delay syndrome |
MONDO:0060457 |
OMIM:617388 |
- |
autoinflammation with arthritis and dyskeratosis |
MONDO:0100062 |
OMIM:616341 |
Orphanet:1934 |
developmental and epileptic encephalopathy |
MONDO:0033669 |
OMIM:619087 |
- |
Noonan syndrome 13 |
MONDO:0008097 |
OMIM:163200 |
Orphanet:2612 |
linear nevus sebaceous syndrome |
MONDO:0011908 |
OMIM:607785 |
Orphanet:86834 |
juvenile myelomonocytic leukemia |
MONDO:0008842 |
OMIM:208920 |
Orphanet:1168 |
ataxia, early-onset, with oculomotor apraxia and hypoalbuminemia |
MONDO:0014902 |
OMIM:617075 |
- |
nasopharyngeal carcinoma, susceptibility to, 3 |
MONDO:0008099 |
OMIM:163500 |
Orphanet:215 |
congenital stationary night blindness autosomal dominant 2 |
MONDO:0033640 |
OMIM:619073 |
- |
vitamin D-dependent rickets, type 3 |
MONDO:0012345 |
OMIM:609796 |
Orphanet:263534 |
acral peeling skin syndrome |
MONDO:0018642 |
- |
Orphanet:447731 |
NIK deficiency |
MONDO:0008214 |
OMIM:169400 |
- |
Pelger-Huet anomaly |
MONDO:0005580 |
OMIM:133239 |
Orphanet:99977 |
esophageal squamous cell carcinoma |
MONDO:0005595 |
OMIM:275355 |
Orphanet:494550 |
laryngeal squamous cell carcinoma |
MONDO:0013633 |
OMIM:614212 |
Orphanet:263524 |
encephalopathy, acute, infection-induced, susceptibility to, 4 |
MONDO:0008276 |
OMIM:174900 |
Orphanet:329971 |
generalized juvenile polyposis/juvenile polyposis coli |
MONDO:0014648 |
OMIM:616459 |
- |
Al-Raqad syndrome |
MONDO:0005260 |
OMIM:209850 |
- |
autism |
MONDO:0008939 |
OMIM:213000 |
Orphanet:2246 |
isolated cerebellar hypoplasia/agenesis |
MONDO:0012612 |
OMIM:611090 |
- |
intellectual disability, autosomal recessive 12 |
MONDO:0014711 |
OMIM:616625 |
Orphanet:488333 |
autosomal dominant Charcot-Marie-Tooth disease type 2W |
MONDO:0014575 |
OMIM:616298 |
Orphanet:85191 |
Singleton-Merten syndrome 2 |
MONDO:0016364 |
OMIM:617121 |
Orphanet:220493 |
Joubert syndrome with ocular defect |
MONDO:0018614 |
OMIM:617166 |
Orphanet:442835 |
undetermined early-onset epileptic encephalopathy |
MONDO:0009245 |
- |
- |
obsolete Friedreich ataxia |
MONDO:0012160 |
OMIM:608940 |
Orphanet:85167 |
spondylometaphyseal dysplasia-cone-rod dystrophy syndrome |
MONDO:0007343 |
OMIM:119900 |
Orphanet:217059 |
isolated congenital digital clubbing |
MONDO:0014593 |
OMIM:616339 |
- |
developmental and epileptic encephalopathy, 29 |
MONDO:0060585 |
OMIM:617721 |
- |
neuronopathy, distal hereditary motor, type 9 |
MONDO:0014920 |
OMIM:617111 |
Orphanet:466718 |
patterned macular dystrophy 3 |
MONDO:0008742 |
OMIM:613107 |
Orphanet:486 |
autosomal dominant severe congenital neutropenia |
MONDO:0013187 |
OMIM:613225 |
Orphanet:331 |
factor XIII, A subunit, deficiency of |
MONDO:0014912 |
OMIM:617099 |
Orphanet:500062 |
infantile-onset periodic fever-panniculitis-dermatosis syndrome |
MONDO:0014970 |
OMIM:617214 |
- |
spermatogenic failure 17 |
MONDO:0008547 |
OMIM:187601 |
Orphanet:93274 |
thanatophoric dysplasia type 2 |
MONDO:0013584 |
OMIM:614116 |
Orphanet:456318 |
hereditary sensory neuropathy-deafness-dementia syndrome |
MONDO:0020492 |
- |
Orphanet:99802 |
hemimegalencephaly |
MONDO:0032604 |
OMIM:618220 |
- |
retinitis pigmentosa 84 |
MONDO:0011684 |
OMIM:606579 |
- |
vitiligo-associated multiple autoimmune disease susceptibility 1 |
MONDO:0010035 |
OMIM:270400 |
Orphanet:818 |
Smith-Lemli-Opitz syndrome |
MONDO:0011725 |
OMIM:606785 |
Orphanet:79235 |
Crigler-Najjar syndrome type 2 |
MONDO:0009068 |
OMIM:220110 |
Orphanet:254905 |
cytochrome-c oxidase deficiency disease |
MONDO:0021230 |
- |
- |
uterine cervix neoplasm |
MONDO:0008980 |
OMIM:215470 |
Orphanet:1180 |
ataxia-hypogonadism-choroidal dystrophy syndrome |
MONDO:0017333 |
- |
Orphanet:289494 |
obsolete hypomyelinating leukodystrophy with or without oligondontia and/or hypogonadism |
MONDO:0008692 |
OMIM:200100 |
Orphanet:14 |
abetalipoproteinemia |
MONDO:0007854 |
OMIM:148370 |
Orphanet:50943 |
keratolytic winter erythema |
MONDO:0017171 |
- |
Orphanet:276212 |
mucopolysaccharidosis type 6, rapidly progressing |
MONDO:0020356 |
OMIM:120200 |
Orphanet:98944 |
coloboma of iris |
MONDO:0009908 |
OMIM:264070 |
Orphanet:238583 |
pterin-4 alpha-carbinolamine dehydratase 1 deficiency |
MONDO:0014568 |
OMIM:616282 |
Orphanet:444099 |
hereditary spastic paraplegia 73 |
MONDO:0012687 |
OMIM:611543 |
Orphanet:464760 |
familial cavitary optic disc anomaly |
MONDO:0011534 |
OMIM:605285 |
Orphanet:99953 |
Charcot-Marie-Tooth disease type 4G |
MONDO:0012691 |
OMIM:611554 |
Orphanet:500 |
LEOPARD syndrome 2 |
MONDO:0010577 |
OMIM:304500 |
Orphanet:90625 |
hearing loss, X-linked 1 |
MONDO:0013587 |
OMIM:614128 |
Orphanet:284435 |
glycogen storage disease due to lactate dehydrogenase H-subunit deficiency |
MONDO:0012682 |
OMIM:611521 |
Orphanet:331226 |
immunodeficiency 35 |
MONDO:0013381 |
OMIM:613708 |
Orphanet:36386 |
neuropathy, hereditary sensory, type 1D |
MONDO:0010225 |
OMIM:310468 |
Orphanet:93622 |
Dent disease type 1 |
MONDO:0009737 |
OMIM:256540 |
Orphanet:351 |
galactosialidosis |
MONDO:0002911 |
- |
- |
brain stem glioma |
MONDO:0019314 |
- |
Orphanet:79455 |
cutaneous mastocytoma |
MONDO:0033853 |
- |
Orphanet:521432 |
congenital cataract-severe neonatal hepatopathy-global developmental delay syndrome |
MONDO:0007470 |
OMIM:126550 |
Orphanet:85192 |
calvarial doughnut lesions-bone fragility syndrome |
MONDO:0026777 |
OMIM:301054 |
Orphanet:596753 |
VEXAS syndrome |
MONDO:0012970 |
OMIM:612634 |
- |
microvascular complications of diabetes, susceptibility to, 6 |
MONDO:0012793 |
OMIM:612076 |
Orphanet:94088 |
hypouricemia, renal, 2 |
MONDO:0017728 |
- |
Orphanet:309239 |
Tay-Sachs disease, B1 variant |
MONDO:0008055 |
OMIM:160800 |
Orphanet:614 |
myotonia congenita, autosomal dominant |
MONDO:0008434 |
OMIM:182290 |
Orphanet:819 |
Smith-Magenis syndrome |
MONDO:0009113 |
OMIM:222800 |
Orphanet:714 |
hemolytic anemia due to diphosphoglycerate mutase deficiency |
MONDO:0030877 |
OMIM:619143 |
- |
cardioacrofacial dysplasia 2 |
MONDO:0017167 |
- |
Orphanet:276145 |
malignant epithelial tumor of salivary glands |
MONDO:0010519 |
OMIM:301040 |
Orphanet:847 |
alpha thalassemia-X-linked intellectual disability syndrome |
MONDO:0012495 |
OMIM:610442 |
Orphanet:168454 |
spondyloepimetaphyseal dysplasia, Genevieve type |
MONDO:0015522 |
- |
Orphanet:157769 |
situs ambiguus |
MONDO:0024266 |
OMIM:617039 |
Orphanet:466729 |
patent ductus arteriosus 3 |
MONDO:0007326 |
- |
- |
obsolete paroxysmal nonkinesigenic dyskinesia 1 |
MONDO:0013164 |
OMIM:613161 |
Orphanet:65287 |
beta-ureidopropionase deficiency |
MONDO:0005453 |
OMIM:615779 |
- |
congenital heart disease |
MONDO:0011798 |
OMIM:607236 |
Orphanet:157855 |
hypoprebetalipoproteinemia, acanthocytosis, retinitis pigmentosa, and pallidal degeneration |
MONDO:0009697 |
OMIM:254780 |
Orphanet:501 |
Lafora disease |
MONDO:0010489 |
OMIM:300928 |
- |
intellectual disability, X-linked 101 |
MONDO:0012381 |
OMIM:609968 |
Orphanet:263458 |
hyperinsulinism due to INSR deficiency |
MONDO:0010047 |
OMIM:270800 |
Orphanet:100986 |
hereditary spastic paraplegia 5A |
MONDO:0054837 |
OMIM:618050 |
- |
intellectual disability, autosomal dominant 57 |
MONDO:0040502 |
OMIM:617825 |
- |
glucocorticoid deficiency 5 |
MONDO:0010013 |
OMIM:269250 |
Orphanet:3144 |
schneckenbecken dysplasia |
MONDO:0033635 |
OMIM:619046 |
- |
mitochondrial complex 4 deficiency, nuclear type 3 |
MONDO:0033563 |
OMIM:619007 |
- |
retinitis pigmentosa 90 |
MONDO:0060702 |
OMIM:617974 |
- |
spondyloepimetaphyseal dysplasia, di rocco type |
MONDO:0013602 |
OMIM:614165 |
Orphanet:29072 |
paragangliomas 5 |
MONDO:0009372 |
OMIM:236800 |
Orphanet:79155 |
encephalopathy due to hydroxykynureninuria |
MONDO:0014132 |
OMIM:615330 |
Orphanet:363424 |
multiple mitochondrial dysfunctions syndrome 3 |
MONDO:0030072 |
OMIM:618959 |
- |
developmental and epileptic encephalopathy, 88 |
MONDO:0014595 |
OMIM:616341 |
Orphanet:3451 |
developmental and epileptic encephalopathy, 30 |
MONDO:0009643 |
OMIM:252150 |
Orphanet:99732 |
sulfite oxidase deficiency due to molybdenum cofactor deficiency type A |
MONDO:0009058 |
OMIM:219500 |
Orphanet:212 |
cystathioninuria |
MONDO:0008892 |
OMIM:211600 |
Orphanet:79306 |
progressive familial intrahepatic cholestasis type 1 |
MONDO:0014256 |
OMIM:615565 |
- |
retinitis pigmentosa 67 |
MONDO:0009903 |
OMIM:263750 |
Orphanet:246 |
postaxial acrofacial dysostosis |
MONDO:0011022 |
OMIM:601224 |
Orphanet:52022 |
Potocki-Shaffer syndrome |
MONDO:0007546 |
OMIM:131440 |
Orphanet:86830 |
myeloproliferative disorder, chronic, with eosinophilia |
MONDO:0044320 |
OMIM:617460 |
Orphanet:791 |
retinitis pigmentosa 79 |
MONDO:0014286 |
OMIM:615632 |
Orphanet:36386 |
neuropathy, hereditary sensory, type 1F |
MONDO:0017732 |
- |
Orphanet:309282 |
alpha-mannosidosis, infantile form |
MONDO:0010028 |
OMIM:604369 |
Orphanet:3166 |
sialuria |
MONDO:0018143 |
OMIM:266150 |
Orphanet:353320 |
pyruvate carboxylase deficiency, benign type |
MONDO:0011784 |
OMIM:607151 |
Orphanet:2573 |
Moyamoya disease 2 |
MONDO:0014571 |
OMIM:616289 |
- |
optic atrophy 9 |
MONDO:0012359 |
OMIM:609889 |
Orphanet:231154 |
combined immunodeficiency due to partial RAG1 deficiency |
MONDO:0010299 |
OMIM:300323 |
Orphanet:79233 |
hypoxanthine guanine phosphoribosyltransferase partial deficiency |
MONDO:0032927 |
OMIM:618805 |
- |
triokinase and FMN cyclase deficiency syndrome |
MONDO:0016002 |
OMIM:225400 |
Orphanet:1900 |
Ehlers-Danlos syndrome, kyphoscoliotic type 1 |
MONDO:0013409 |
OMIM:613761 |
- |
age related macular degeneration 5 |
MONDO:0060715 |
OMIM:617994 |
- |
tumoral calcinosis, hyperphosphatemic, familial, 3 |
MONDO:0013410 |
OMIM:613762 |
Orphanet:251510 |
46,XY sex reversal 6 |
MONDO:0013882 |
OMIM:614749 |
Orphanet:247262 |
hyperphosphatasia with intellectual disability syndrome 2 |
MONDO:0012690 |
OMIM:611553 |
Orphanet:648 |
Noonan syndrome 5 |
MONDO:0008840 |
OMIM:208910 |
Orphanet:100 |
ataxia telangiectasia |
MONDO:0024552 |
OMIM:309801 |
Orphanet:2556 |
linear skin defects with multiple congenital anomalies 1 |
MONDO:0020437 |
- |
Orphanet:99106 |
atrial septal defect, ostium primum type |
MONDO:0030008 |
OMIM:618839 |
- |
combined oxidative phosphorylation deficiency 42 |
MONDO:0017176 |
- |
Orphanet:276244 |
Machado-Joseph disease type 3 |
MONDO:0008747 |
OMIM:203290 |
Orphanet:79433 |
oculocutaneous albinism type 3 |
MONDO:0014877 |
OMIM:617030 |
- |
myopathy, distal, 5 |
MONDO:0017733 |
- |
Orphanet:309288 |
alpha-mannosidosis, adult form |
MONDO:0007356 |
OMIM:120435 |
Orphanet:144 |
Lynch syndrome 1 |
MONDO:0013156 |
OMIM:613152 |
Orphanet:370980 |
muscular dystrophy-dystroglycanopathy (congenital without intellectual disability), type B4 |
MONDO:0013570 |
OMIM:614096 |
Orphanet:319504 |
combined oxidative phosphorylation defect type 8 |
MONDO:0018113 |
OMIM:616602 |
Orphanet:35098 |
isolated plagiocephaly |
MONDO:0009262 |
OMIM:230650 |
Orphanet:79257 |
GM1 gangliosidosis type 3 |
MONDO:0009329 |
OMIM:234810 |
Orphanet:199241 |
pulmonary venoocclusive disease 2 |
MONDO:0013157 |
OMIM:613153 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A5 |
MONDO:0019642 |
OMIM:600785 |
Orphanet:93160 |
vitamin D-dependent rickets, type 2 |
MONDO:0011888 |
OMIM:607676 |
Orphanet:70592 |
immunodeficiency 67 |
MONDO:0008420 |
OMIM:182000 |
- |
seborrheic keratosis |
MONDO:0012414 |
OMIM:610127 |
Orphanet:79264 |
neuronal ceroid lipofuscinosis 10 |
MONDO:0009757 |
OMIM:257220 |
Orphanet:646 |
Niemann-Pick disease, type C1 |
MONDO:0033682 |
- |
Orphanet:508533 |
skeletal dysplasia-T-cell immunodeficiency-developmental delay syndrome |
MONDO:0010212 |
OMIM:278730 |
Orphanet:910 |
xeroderma pigmentosum group D |
MONDO:0009114 |
OMIM:222900 |
Orphanet:35122 |
congenital sucrase-isomaltase deficiency |
MONDO:0015339 |
OMIM:300100 |
Orphanet:139399 |
adrenomyeloneuropathy |
MONDO:0032579 |
OMIM:618175 |
- |
warburg-cinotti syndrome |
MONDO:0008294 |
OMIM:176000 |
Orphanet:79276 |
acute intermittent porphyria |
MONDO:0013531 |
OMIM:614023 |
Orphanet:79350 |
PSPH deficiency |
MONDO:0032884 |
OMIM:618727 |
- |
ectodermal dysplasia with facial dysmorphism and acral, ocular, and brain anomalies |
MONDO:0030917 |
OMIM:617788 |
- |
intellectual disability, autosomal dominant 51 |
MONDO:0007156 |
OMIM:108100 |
- |
arthritis, sacroiliac |
MONDO:0017999 |
- |
Orphanet:329308 |
fatty acid hydroxylase-associated neurodegeneration |
MONDO:0008327 |
OMIM:177650 |
Orphanet:529819 |
exfoliation syndrome |
MONDO:0013412 |
OMIM:613765 |
- |
hypertrophic cardiomyopathy 9 |
MONDO:0010432 |
OMIM:300807 |
- |
thrombophilia, X-linked, due to factor 9 defect |
MONDO:0012676 |
OMIM:611490 |
Orphanet:667 |
autosomal recessive osteopetrosis 4 |
MONDO:0030852 |
OMIM:619103 |
- |
neurodevelopmental disorder with dysmorphic facies, sleep disturbance, and brain abnormalities |
MONDO:0000455 |
OMIM:613093 |
Orphanet:1871 |
cone dystrophy |
MONDO:0033547 |
OMIM:618974 |
- |
Li-Ghorbani-Weisz-Hubshman syndrome |
MONDO:0012543 |
OMIM:610708 |
Orphanet:98673 |
optic atrophy 5 |
MONDO:0014954 |
OMIM:617174 |
- |
Ehlers-Danlos syndrome, periodontal type 2 |
MONDO:0010632 |
OMIM:308350 |
- |
developmental and epileptic encephalopathy, 1 |
MONDO:0011816 |
OMIM:607330 |
Orphanet:46059 |
lathosterolosis |
MONDO:0007507 |
OMIM:129200 |
Orphanet:1658 |
absence of fingerprints-congenital milia syndrome |
MONDO:0011152 |
OMIM:601815 |
Orphanet:79351 |
PHGDH deficiency |
MONDO:0009261 |
OMIM:230600 |
Orphanet:79256 |
GM1 gangliosidosis type 2 |
MONDO:0009015 |
OMIM:217400 |
Orphanet:1490 |
corneal dystrophy-perceptive deafness syndrome |
MONDO:0018322 |
OMIM:300438 |
Orphanet:391428 |
HSD10 disease, infantile type |
MONDO:0018197 |
- |
Orphanet:363534 |
mitochondrial DNA depletion syndrome, hepatocerebrorenal form |
MONDO:0060671 |
OMIM:617924 |
- |
epilepsy, juvenile myoclonic, susceptibility to, 10 |
MONDO:0017973 |
- |
Orphanet:325529 |
non-classic congenital lipoid adrenal hyperplasia due to STAR deficency |
MONDO:0009997 |
- |
Orphanet:3103 |
Roberts syndrome |
MONDO:0007087 |
OMIM:104290 |
Orphanet:2131 |
alternating hemiplegia of childhood 1 |
MONDO:0032568 |
OMIM:618158 |
- |
intellectual developmental disorder with macrocephaly, seizures, and speech delay |
MONDO:0014197 |
OMIM:615468 |
Orphanet:397964 |
combined immunodeficiency due to MALT1 deficiency |
MONDO:0008965 |
OMIM:214800 |
Orphanet:138 |
CHARGE syndrome |
MONDO:0011002 |
OMIM:601152 |
Orphanet:90120 |
neuropathy, hereditary motor and sensory, type 6A |
MONDO:0014169 |
OMIM:615402 |
Orphanet:241 |
dyschromatosis universalis hereditaria 3 |
MONDO:0018935 |
- |
Orphanet:58017 |
hairy cell leukemia |
MONDO:0005223 |
- |
Orphanet:98832 |
acute myeloid leukemia with minimal differentiation |
MONDO:0010555 |
OMIM:602497 |
Orphanet:79345 |
X-linked chondrodysplasia punctata 1 |
MONDO:0007369 |
OMIM:121300 |
Orphanet:79273 |
hereditary coproporphyria |
MONDO:0007522 |
- |
Orphanet:90309 |
Ehlers-Danlos syndrome, classic type |
MONDO:0007798 |
OMIM:146300 |
Orphanet:436 |
obsolete adult hypophosphatasia |
MONDO:0014307 |
OMIM:615696 |
Orphanet:79145 |
Dowling-Degos disease 4 |
MONDO:0003795 |
- |
Orphanet:370396 |
ovarian small cell carcinoma |
MONDO:0011369 |
OMIM:603776 |
- |
hypercholesterolemia, autosomal dominant, 3 |
MONDO:0054726 |
OMIM:617706 |
- |
spermatogenic failure 22 |
MONDO:0008818 |
OMIM:208050 |
Orphanet:3342 |
arterial tortuosity syndrome |
MONDO:0013867 |
OMIM:614707 |
Orphanet:97229 |
brown-Vialetto-van Laere syndrome 2 |
MONDO:0032762 |
OMIM:618457 |
- |
hearing loss, autosomal recessive 115 |
MONDO:0009025 |
OMIM:218030 |
Orphanet:320 |
apparent mineralocorticoid excess |
MONDO:0013595 |
OMIM:614156 |
Orphanet:276405 |
hyperbiliverdinemia |
MONDO:0010510 |
OMIM:300984 |
- |
intellectual disability, X-linked 105 |
MONDO:0023693 |
- |
- |
maple syrup urine disease type 2 |
MONDO:0007919 |
OMIM:153100 |
Orphanet:79452 |
lymphatic malformation 1 |
MONDO:0024498 |
OMIM:137800 |
Orphanet:182067 |
glioma susceptibility 1 |
MONDO:0009124 |
OMIM:223370 |
Orphanet:235 |
Dubowitz syndrome |
MONDO:0010008 |
OMIM:268900 |
Orphanet:3129 |
sarcosinemia |
MONDO:0020715 |
OMIM:146500 |
- |
multiple system atrophy 1, susceptibility to |
MONDO:0015011 |
OMIM:617302 |
- |
optic atrophy 11 |
MONDO:0014682 |
OMIM:616535 |
Orphanet:319487 |
thyroid cancer, nonmedullary, 5 |
MONDO:0014596 |
OMIM:616342 |
- |
lissencephaly 7 with cerebellar hypoplasia |
MONDO:0030047 |
OMIM:618891 |
- |
microcephaly, developmental delay, and brittle hair syndrome |
MONDO:0014995 |
OMIM:617268 |
- |
neurodevelopmental disorder with hypotonia, seizures, and absent language |
MONDO:0014137 |
OMIM:615346 |
Orphanet:759 |
precocious puberty, central, 2 |
MONDO:0012089 |
OMIM:608649 |
Orphanet:88621 |
ichthyosis prematurity syndrome |
MONDO:0007621 |
OMIM:136140 |
Orphanet:2044 |
floating-Harbor syndrome |
MONDO:0017295 |
OMIM:307030 |
Orphanet:284411 |
glycerol kinase deficiency, juvenile form |
MONDO:0023655 |
OMIM:619281 |
- |
immunodeficiency 14b, autosomal recessive |
MONDO:0029133 |
OMIM:618129 |
- |
muscular dystrophy, limb-girdle, autosomal dominant 4 |
MONDO:0014147 |
OMIM:615362 |
Orphanet:79262 |
neuronal ceroid lipofuscinosis 13 |
MONDO:0008992 |
OMIM:216100 |
Orphanet:2319 |
Juberg-Hayward syndrome |
MONDO:0011426 |
OMIM:604290 |
Orphanet:48818 |
aceruloplasminemia |
MONDO:0044204 |
OMIM:260400 |
Orphanet:811 |
Shwachman-Diamond syndrome 1 |
MONDO:0019086 |
- |
Orphanet:70482 |
carcinoma of esophagus |
MONDO:0010783 |
OMIM:502500 |
- |
Alzheimer disease, susceptibility to, mitochondrial |
MONDO:0014557 |
OMIM:616267 |
Orphanet:459033 |
ataxia - oculomotor apraxia type 4 |
MONDO:0013166 |
OMIM:613163 |
Orphanet:2066 |
GABA aminotransferase deficiency |
MONDO:0007041 |
OMIM:101200 |
Orphanet:87 |
apert syndrome |
MONDO:0010152 |
OMIM:275400 |
Orphanet:3363 |
trichomegaly-retina pigmentary degeneration-dwarfism syndrome |
MONDO:0013554 |
OMIM:614070 |
- |
psoriasis 13, susceptibility to |
MONDO:0015555 |
- |
Orphanet:158769 |
plaque-form urticaria pigmentosa |
MONDO:0014553 |
OMIM:616260 |
- |
Tenorio syndrome |
MONDO:0013461 |
OMIM:613850 |
Orphanet:319684 |
inosine triphosphatase deficiency |
MONDO:0009965 |
OMIM:267000 |
Orphanet:2849 |
Perlman syndrome |
MONDO:0017778 |
OMIM:613943 |
Orphanet:313 |
lamellar ichthyosis |
MONDO:0014047 |
OMIM:615108 |
Orphanet:201 |
Cowden syndrome 5 |
MONDO:0007471 |
OMIM:126700 |
Orphanet:75376 |
Doyne honeycomb retinal dystrophy |
MONDO:0033014 |
OMIM:617526 |
Orphanet:317 |
erythrokeratodermia variabilis et progressiva 4 |
MONDO:0024539 |
OMIM:215500 |
Orphanet:75377 |
choroidal dystrophy, central areolar, 1 |
MONDO:0009398 |
OMIM:239300 |
Orphanet:247262 |
hyperphosphatasia with intellectual disability syndrome 1 |
MONDO:0014466 |
OMIM:616038 |
Orphanet:2671 |
Neu-Laxova syndrome 2 |
MONDO:0012880 |
OMIM:612370 |
- |
hypogonadotropic hypogonadism 5 with or without anosmia |
MONDO:0013379 |
OMIM:613706 |
Orphanet:648 |
Noonan syndrome 7 |
MONDO:0019587 |
OMIM:616969 |
Orphanet:90635 |
autosomal dominant nonsyndromic hearing loss |
MONDO:0021100 |
- |
- |
breast neoplasm |
MONDO:0011450 |
OMIM:604370 |
Orphanet:227535 |
breast-ovarian cancer, familial, susceptibility to, 1 |
MONDO:0010914 |
OMIM:600649 |
Orphanet:228305 |
carnitine palmitoyl transferase II deficiency, severe infantile form |
MONDO:0014975 |
OMIM:617225 |
Orphanet:513436 |
autosomal recessive spastic paraplegia type 78 |
MONDO:0005486 |
OMIM:617073 |
Orphanet:99798 |
tooth agenesis |
MONDO:0005062 |
OMIM:605027 |
Orphanet:223735 |
lymphoma |
MONDO:0013766 |
OMIM:614468 |
Orphanet:300359 |
familial cold autoinflammatory syndrome 3 |
MONDO:0013788 |
OMIM:614504 |
Orphanet:886 |
Usher syndrome type 3B |
MONDO:0007872 |
OMIM:149730 |
Orphanet:2363 |
LADD syndrome |
MONDO:0009454 |
OMIM:242860 |
Orphanet:2268 |
immunodeficiency-centromeric instability-facial anomalies syndrome 1 |
MONDO:0034145 |
OMIM:618440 |
Orphanet:557003 |
oculocerebrodental syndrome |
MONDO:0012371 |
OMIM:609942 |
Orphanet:648 |
Noonan syndrome 3 |
MONDO:0002407 |
- |
- |
capillary hemangioma |
MONDO:0018141 |
OMIM:266150 |
Orphanet:353308 |
pyruvate carboxylase deficiency, infantile form |
MONDO:0010161 |
OMIM:276700 |
Orphanet:882 |
tyrosinemia type I |
MONDO:0032772 |
OMIM:618476 |
- |
brain abnormalities, neurodegeneration, and dysosteosclerosis |
MONDO:0011640 |
OMIM:606170 |
Orphanet:85201 |
genitopatellar syndrome |
MONDO:0011190 |
OMIM:602088 |
Orphanet:93591 |
nephronophthisis 2 |
MONDO:0007265 |
OMIM:115150 |
Orphanet:1340 |
cardiofaciocutaneous syndrome 1 |
MONDO:0013249 |
OMIM:613391 |
Orphanet:90636 |
autosomal recessive nonsyndromic hearing loss 84A |
MONDO:0032621 |
OMIM:618238 |
- |
mitochondrial complex 1 deficiency, nuclear type 16 |
MONDO:0100252 |
OMIM:211900 |
- |
tumoral calcinosis, hyperphosphatemic, familial, 1 |
MONDO:0019004 |
OMIM:616806 |
Orphanet:654 |
kidney Wilms tumor |
MONDO:0012892 |
OMIM:612394 |
Orphanet:300284 |
bone fragility with contractures, arterial rupture, and deafness |
MONDO:0017366 |
OMIM:614165 |
Orphanet:29072 |
hereditary pheochromocytoma-paraganglioma |
MONDO:0009759 |
OMIM:257300 |
- |
mosaic variegated aneuploidy syndrome 1 |
MONDO:0032839 |
OMIM:618624 |
- |
noonan syndrome 12 |
MONDO:0019570 |
OMIM:216400 |
Orphanet:90324 |
Cockayne syndrome type 2 |
MONDO:0013883 |
OMIM:614750 |
Orphanet:590 |
congenital myasthenic syndrome 13 |
MONDO:0034147 |
- |
Orphanet:557064 |
neonatal epileptic encephalopathy due to glutaminase deficiency |
MONDO:0012454 |
OMIM:610251 |
- |
alcohol sensitivity, acute |
MONDO:0015716 |
- |
Orphanet:169796 |
moderately severe hemophilia B |
MONDO:0021251 |
- |
- |
endometrium neoplasm |
MONDO:0013339 |
OMIM:613642 |
- |
dilated cardiomyopathy 1GG |
MONDO:0011871 |
OMIM:607616 |
Orphanet:99022 |
Niemann-Pick disease type B |
MONDO:0010216 |
OMIM:278780 |
Orphanet:910 |
xeroderma pigmentosum group G |
MONDO:0002049 |
OMIM:612004 |
Orphanet:852 |
thrombocytopenia |
MONDO:0100082 |
OMIM:151100 |
- |
LEOPARD syndrome 1 |
MONDO:0011274 |
OMIM:602849 |
Orphanet:53271 |
Muenke syndrome |
MONDO:0007288 |
OMIM:116600 |
Orphanet:98994 |
cataract 6 multiple types |
MONDO:0018618 |
- |
Orphanet:443090 |
obsolete 46,XY disorder of sexual development due to dihydrotestosterone backdoor pathway biosynthesis defect |
MONDO:0019118 |
- |
Orphanet:71862 |
inherited retinal dystrophy |
MONDO:0009885 |
OMIM:262890 |
Orphanet:806 |
Scott syndrome |
MONDO:0008428 |
OMIM:182230 |
Orphanet:95494 |
septooptic dysplasia |
MONDO:0012693 |
OMIM:611556 |
Orphanet:137625 |
glycogen storage disease due to muscle and heart glycogen synthase deficiency |
MONDO:0007700 |
OMIM:140350 |
Orphanet:2118 |
hawkinsinuria |
MONDO:0016089 |
- |
Orphanet:206436 |
infantile Krabbe disease |
MONDO:0018002 |
OMIM:616479 |
Orphanet:329336 |
adult-onset chronic progressive external ophthalmoplegia with mitochondrial myopathy |
MONDO:0008774 |
OMIM:245130 |
Orphanet:79154 |
2-aminoadipic 2-oxoadipic aciduria |
MONDO:0002135 |
- |
- |
optic nerve disorder |
MONDO:0007885 |
OMIM:150600 |
Orphanet:2380 |
Legg-Calve-Perthes disease |
MONDO:0017840 |
- |
Orphanet:315311 |
classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency, simple virilizing form |
MONDO:0010162 |
OMIM:276710 |
Orphanet:69723 |
tyrosinemia type III |
MONDO:0001187 |
OMIM:109800 |
Orphanet:157980 |
urinary bladder cancer |
MONDO:0009799 |
- |
- |
obsolete pachydermoperiostosis |
MONDO:0017696 |
OMIM:232500 |
Orphanet:308638 |
glycogen storage disease due to glycogen branching enzyme deficiency, non progressive hepatic form |
MONDO:0030918 |
OMIM:617796 |
- |
intellectual disability, autosomal dominant 52 |
MONDO:0014221 |
OMIM:615512 |
Orphanet:868 |
triosephosphate isomerase deficiency |
MONDO:0020748 |
OMIM:618666 |
- |
sitosterolemia 2 |
MONDO:0016305 |
- |
Orphanet:216873 |
atypical pantothenate kinase-associated neurodegeneration |
MONDO:0010457 |
OMIM:300855 |
Orphanet:276432 |
Ogden syndrome |
MONDO:0013818 |
OMIM:614602 |
Orphanet:84064 |
trichohepatoenteric syndrome 2 |
MONDO:0013310 |
OMIM:613571 |
Orphanet:95699 |
congenital adrenal hyperplasia due to cytochrome P450 oxidoreductase deficiency |
MONDO:0032860 |
OMIM:618665 |
- |
intellectual developmental disorder, autosomal recessive 72 |
MONDO:0011715 |
OMIM:606744 |
Orphanet:808 |
Seckel syndrome 2 |
MONDO:0010779 |
OMIM:500008 |
Orphanet:90641 |
mitochondrial non-syndromic sensorineural hearing loss |
MONDO:0012504 |
OMIM:610474 |
Orphanet:85164 |
camptodactyly-tall stature-scoliosis-hearing loss syndrome |
MONDO:0054731 |
OMIM:617965 |
- |
spermatogenic failure 27 |
MONDO:0016355 |
OMIM:610829 |
Orphanet:220386 |
semilobar holoprosencephaly |
MONDO:0016814 |
OMIM:256000 |
Orphanet:255210 |
maternally-inherited Leigh syndrome |
MONDO:0032918 |
OMIM:618792 |
- |
developmental and epileptic encephalopathy, 84 |
MONDO:0700089 |
OMIM:611147 |
Orphanet:98810 |
paroxysmal nonkinesigenic dyskinesia 1 |
MONDO:0005072 |
OMIM:616792 |
Orphanet:635 |
neuroblastoma |
MONDO:0014450 |
OMIM:616001 |
Orphanet:180188 |
breasts and/or nipples, aplasia or hypoplasia of, 2 |
MONDO:0008090 |
OMIM:162800 |
Orphanet:2686 |
cyclic hematopoiesis |
MONDO:0011913 |
OMIM:607822 |
- |
Alzheimer disease 3 |
MONDO:0010263 |
OMIM:300990 |
Orphanet:86818 |
Alport syndrome-intellectual disability-midface hypoplasia-elliptocytosis syndrome |
MONDO:0014754 |
OMIM:616733 |
- |
primary coenzyme Q10 deficiency 8 |
MONDO:0032786 |
OMIM:618499 |
- |
Noonan syndrome 11 |
MONDO:0019414 |
OMIM:308205 |
Orphanet:85284 |
BRESEK syndrome |
MONDO:0021040 |
- |
- |
pancreatic neoplasm |
MONDO:0013868 |
OMIM:614714 |
Orphanet:79152 |
porokeratosis 7, multiple types |
MONDO:0012316 |
OMIM:609628 |
Orphanet:77297 |
Majeed syndrome |
MONDO:0030258 |
OMIM:619301 |
- |
pontocerebellar hypoplasia, type 14 |
MONDO:0009636 |
OMIM:251880 |
Orphanet:279934 |
mitochondrial DNA depletion syndrome 3 |
MONDO:0008995 |
OMIM:216340 |
Orphanet:3472 |
Yunis-Varon syndrome |
MONDO:0018346 |
- |
Orphanet:397922 |
ferro-cerebro-cutaneous syndrome |
MONDO:0002009 |
OMIM:608691 |
- |
major depressive disorder |
MONDO:0012238 |
OMIM:609283 |
Orphanet:254892 |
progressive external ophthalmoplegia with mitochondrial DNA deletions, autosomal dominant 2 |
MONDO:0100165 |
OMIM:606176 |
- |
permanent neonatal diabetes mellitus 1 |
MONDO:0017244 |
- |
Orphanet:280794 |
pseudoxanthomatous diffuse cutaneous mastocytosis |
MONDO:0012465 |
OMIM:610293 |
Orphanet:83639 |
hypercoagulability syndrome due to glycosylphosphatidylinositol deficiency |
MONDO:0018750 |
- |
- |
obsolete class I glucose-6-phosphate dehydrogenase deficiency |
MONDO:0017094 |
- |
Orphanet:268950 |
cerebral cortical dysplasia |
MONDO:0015008 |
OMIM:617297 |
- |
amelogenesis imperfecta, type 1J |
MONDO:0013091 |
OMIM:613027 |
- |
glycogen storage disease IXc |
MONDO:0013768 |
OMIM:614473 |
Orphanet:51608 |
arterial calcification, generalized, of infancy, 2 |
MONDO:0013563 |
OMIM:614080 |
Orphanet:280633 |
multiple congenital anomalies-hypotonia-seizures syndrome 1 |
MONDO:0008285 |
OMIM:175510 |
- |
polyps, multiple and recurrent inflammatory fibroid, gastrointestinal |
MONDO:0019342 |
OMIM:616777 |
Orphanet:808 |
Seckel syndrome |
MONDO:0018495 |
- |
Orphanet:423479 |
X-linked intellectual disability-limb spasticity-retinal dystrophy-diabetes insipidus syndrome |
MONDO:0016557 |
OMIM:151600 |
Orphanet:2387 |
leukonychia totalis |
MONDO:0009253 |
OMIM:229850 |
Orphanet:2059 |
Fryns syndrome |
MONDO:0012990 |
OMIM:612712 |
- |
Leber congenital amaurosis 13 |
MONDO:0000819 |
OMIM:206500 |
Orphanet:1048 |
anencephaly |
MONDO:0014306 |
OMIM:615688 |
Orphanet:404553 |
vasculitis due to ADA2 deficiency |
MONDO:0013968 |
OMIM:614921 |
Orphanet:319646 |
PGM1-CDG |
MONDO:0013822 |
OMIM:614613 |
Orphanet:950 |
acrodysostosis 2 with or without hormone resistance |
MONDO:0012728 |
OMIM:611777 |
Orphanet:130 |
Brugada syndrome 2 |
MONDO:0023122 |
OMIM:601518 |
Orphanet:1331 |
familial prostate carcinoma |
MONDO:0018810 |
- |
Orphanet:480528 |
lethal hydranencephaly-diaphragmatic hernia syndrome |
MONDO:0014206 |
OMIM:615486 |
Orphanet:440427 |
severe early-onset pulmonary alveolar proteinosis due to MARS deficiency |
MONDO:0020320 |
- |
Orphanet:98834 |
acute myeloblastic leukemia with maturation |
MONDO:0017566 |
- |
Orphanet:295243 |
macrodactyly of toes, unilateral |
MONDO:0015168 |
- |
Orphanet:1037 |
arthrogryposis multiplex congenita |
MONDO:0017726 |
- |
Orphanet:309192 |
Tay-Sachs disease, b variant, adult form |
MONDO:0014922 |
OMIM:617114 |
- |
myofibrillar myopathy 7 |
MONDO:0009185 |
OMIM:226750 |
Orphanet:1946 |
amelocerebrohypohidrotic syndrome |
MONDO:0012753 |
OMIM:611895 |
Orphanet:803 |
amyotrophic lateral sclerosis type 9 |
MONDO:0009053 |
OMIM:219150 |
Orphanet:35664 |
ALDH18A1-related de Barsy syndrome |
MONDO:0017701 |
OMIM:232500 |
Orphanet:308712 |
glycogen storage disease due to glycogen branching enzyme deficiency, adult neuromuscular form |
MONDO:0031006 |
OMIM:619259 |
- |
neurodegeneration with ataxia and late-onset optic atrophy |
MONDO:0012071 |
OMIM:608594 |
Orphanet:528 |
congenital generalized lipodystrophy type 1 |
MONDO:0009824 |
OMIM:260000 |
Orphanet:93599 |
primary hyperoxaluria type 2 |
MONDO:0032647 |
OMIM:618272 |
- |
global developmental delay, lung cysts, overgrowth, and wilms tumor |
MONDO:0008791 |
OMIM:206500 |
Orphanet:1048 |
isolated anencephaly/exencephaly |
MONDO:0006547 |
- |
- |
exanthem |
MONDO:0012183 |
OMIM:609048 |
Orphanet:618 |
melanoma, cutaneous malignant, susceptibility to, 3 |
MONDO:0044324 |
OMIM:617694 |
- |
Al Kaissi syndrome |
MONDO:0024546 |
OMIM:259100 |
Orphanet:2796 |
hypertrophic osteoarthropathy, primary, autosomal recessive, 1 |
MONDO:0008974 |
OMIM:215140 |
Orphanet:1426 |
Greenberg dysplasia |
MONDO:0013987 |
OMIM:614947 |
Orphanet:319524 |
combined oxidative phosphorylation defect type 15 |
MONDO:0012656 |
OMIM:614915 |
Orphanet:137783 |
lethal congenital contracture syndrome 3 |
MONDO:0026768 |
OMIM:301052 |
- |
warfarin sensitivity, X-linked |
MONDO:0004994 |
- |
Orphanet:167848 |
cardiomyopathy |
MONDO:0016090 |
- |
Orphanet:206443 |
late-infantile/juvenile Krabbe disease |
MONDO:0017389 |
- |
Orphanet:293284 |
tetrahydrobiopterin-responsive hyperphenylalaninemia/phenylketonuria |
MONDO:0100354 |
OMIM:249210 |
Orphanet:2604 |
megacystis-microcolon-intestinal hypoperistalsis syndrome 1 |
MONDO:0016431 |
OMIM:606482 |
Orphanet:228179 |
autosomal dominant Charcot-Marie-Tooth disease type 2M |
MONDO:0011792 |
OMIM:607200 |
Orphanet:95716 |
thyroid dyshormonogenesis 6 |
MONDO:0020630 |
OMIM:617711 |
- |
epileptic encephalopathy, infantile or early childhood, 1 |
MONDO:0015253 |
OMIM:615909 |
Orphanet:124 |
Diamond-Blackfan anemia |
MONDO:0008178 |
OMIM:167320 |
Orphanet:52430 |
inclusion body myopathy with Paget disease of bone and frontotemporal dementia type 1 |
MONDO:0018733 |
- |
Orphanet:464311 |
intellectual disability syndrome due to a DYRK1A point mutation |
MONDO:0010088 |
OMIM:272200 |
Orphanet:585 |
mucosulfatidosis |
MONDO:0018872 |
- |
Orphanet:518 |
acute megakaryoblastic leukemia |
MONDO:0013322 |
OMIM:613608 |
Orphanet:86814 |
epilepsy, familial adult myoclonic, 3 |
MONDO:0009658 |
OMIM:252940 |
Orphanet:79272 |
Sanfilippo syndrome type D |
MONDO:0009022 |
OMIM:217990 |
- |
corpus callosum, agenesis of |
MONDO:0010621 |
OMIM:308050 |
Orphanet:139 |
CHILD syndrome |
MONDO:0016366 |
OMIM:261600 |
Orphanet:2209 |
maternal phenylketonuria |
MONDO:0016607 |
OMIM:146300 |
Orphanet:247685 |
odontohypophosphatasia |
MONDO:0010420 |
OMIM:300752 |
Orphanet:79278 |
X-linked erythropoietic protoporphyria |
MONDO:0014048 |
OMIM:615109 |
Orphanet:201 |
Cowden syndrome 6 |
MONDO:0009862 |
OMIM:261630 |
Orphanet:238583 |
dihydropteridine reductase deficiency |
MONDO:0009863 |
OMIM:261640 |
Orphanet:238583 |
BH4-deficient hyperphenylalaninemia A |
MONDO:0015018 |
OMIM:617320 |
- |
ichthyosis, congenital, autosomal recessive 12 |
MONDO:0009649 |
OMIM:252350 |
Orphanet:2573 |
moyamoya disease 1 |
MONDO:0014305 |
OMIM:615686 |
Orphanet:401805 |
hereditary spastic paraplegia 63 |
MONDO:0018577 |
- |
Orphanet:436274 |
pseudoxanthoma elasticum-like skin manifestations with retinitis pigmentosa |
MONDO:0014973 |
OMIM:617222 |
- |
sudden cardiac failure, infantile |
MONDO:0014391 |
OMIM:615897 |
Orphanet:420573 |
severe combined immunodeficiency due to CTPS1 deficiency |
MONDO:0013971 |
OMIM:614924 |
Orphanet:314051 |
leukoencephalopathy-thalamus and brainstem anomalies-high lactate syndrome |
MONDO:0014275 |
OMIM:615605 |
Orphanet:3337 |
Fanconi renotubular syndrome 3 |
MONDO:0007959 |
OMIM:155255 |
Orphanet:616 |
medulloblastoma |
MONDO:0013756 |
OMIM:614441 |
Orphanet:2796 |
hypertrophic osteoarthropathy, primary, autosomal recessive, 2 |
MONDO:0014162 |
OMIM:615395 |
Orphanet:352563 |
infantile hypertrophic cardiomyopathy due to MRPL44 deficiency |
MONDO:0011603 |
OMIM:617158 |
Orphanet:602 |
GNE myopathy |
MONDO:0017730 |
- |
Orphanet:309271 |
metachromatic leukodystrophy, adult form |
MONDO:0008726 |
OMIM:201750 |
Orphanet:63269 |
Antley-Bixler syndrome with genital anomalies and disordered steroidogenesis |
MONDO:0009676 |
OMIM:253601 |
Orphanet:268 |
autosomal recessive limb-girdle muscular dystrophy type 2B |
MONDO:0100095 |
OMIM:618170 |
- |
neurodegeneration, childhood-onset, stress-induced, with variable ataxia and seizures |
MONDO:0009383 |
OMIM:237900 |
Orphanet:2312 |
transient familial neonatal hyperbilirubinemia |
MONDO:0030059 |
OMIM:618916 |
- |
developmental and epileptic encephalopathy, 87 |
MONDO:0014290 |
OMIM:615643 |
Orphanet:397725 |
neurodegeneration with brain iron accumulation 6 |
MONDO:0018989 |
- |
Orphanet:64740 |
recurrent acute pancreatitis |
MONDO:0018653 |
OMIM:615083 |
Orphanet:447877 |
Polymerase proofreading-related adenomatous polyposis |
MONDO:0014566 |
OMIM:616280 |
Orphanet:397735 |
Charcot-Marie-Tooth disease axonal type 2U |
MONDO:0011860 |
OMIM:607572 |
Orphanet:548 |
leprosy, susceptibility to, 2 |
MONDO:0017403 |
OMIM:610193 |
Orphanet:293910 |
familial isolated arrhythmogenic ventricular dysplasia, right dominant form |
MONDO:0015052 |
- |
Orphanet:100049 |
obsolete primary interstitial lung disease specific to childhood due to pulmonary surfactant protein anomalies |
MONDO:0012986 |
OMIM:612691 |
Orphanet:268940 |
bilateral parasagittal parieto-occipital polymicrogyria |
MONDO:0000483 |
- |
- |
oculogyric crisis |
MONDO:0017173 |
OMIM:614822 |
Orphanet:276234 |
non-syndromic male infertility due to sperm motility disorder |
MONDO:0009265 |
OMIM:230800 |
Orphanet:77259 |
Gaucher disease type I |
MONDO:0009070 |
OMIM:220120 |
Orphanet:941 |
D-glyceric aciduria |
MONDO:0013561 |
OMIM:614078 |
Orphanet:280586 |
chondrodysplasia with joint dislocations, gPAPP type |
MONDO:0014563 |
OMIM:616277 |
Orphanet:506 |
mitochondrial short-chain Enoyl-Coa hydratase 1 deficiency |
MONDO:0012423 |
OMIM:610156 |
Orphanet:75858 |
MORM syndrome |
MONDO:0004183 |
- |
- |
axonal neuropathy |
MONDO:0017052 |
OMIM:615135 |
Orphanet:268162 |
intermediate maple syrup urine disease |
MONDO:0014881 |
OMIM:617044 |
Orphanet:488618 |
transketolase deficiency |
MONDO:0014101 |
OMIM:615249 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type a, 12 |
MONDO:0010256 |
OMIM:300143 |
- |
intellectual disability, X-linked 21 |
MONDO:0007793 |
OMIM:146000 |
Orphanet:429 |
hypochondroplasia |
MONDO:0014662 |
OMIM:616488 |
Orphanet:478664 |
congenital insensitivity to pain-hypohidrosis syndrome |
MONDO:0013307 |
OMIM:613561 |
Orphanet:2598 |
myopathy, lactic acidosis, and sideroblastic anemia 2 |
MONDO:0020785 |
OMIM:618196 |
- |
capillary malformation-arteriovenous malformation 2 |
MONDO:0008717 |
OMIM:201250 |
Orphanet:968 |
acromesomelic dysplasia 2C, Hunter-Thompson type |
MONDO:0018323 |
OMIM:300438 |
Orphanet:391457 |
HSD10 disease, neonatal type |
MONDO:0011953 |
OMIM:608033 |
Orphanet:88619 |
familial acute necrotizing encephalopathy |
MONDO:0024525 |
OMIM:134600 |
Orphanet:3337 |
Fanconi renotubular syndrome 1 |
MONDO:0060455 |
OMIM:301015 |
- |
X-linked congenital hemolytic anemia |
MONDO:0013242 |
OMIM:613375 |
Orphanet:552 |
maturity-onset diabetes of the young type 11 |
MONDO:0014457 |
OMIM:616025 |
Orphanet:247262 |
hyperphosphatasia with intellectual disability syndrome 5 |
MONDO:0005233 |
OMIM:211980 |
Orphanet:488201 |
non-small cell lung carcinoma |
MONDO:0009610 |
OMIM:250950 |
Orphanet:67046 |
3-methylglutaconic aciduria type 1 |
MONDO:0013743 |
OMIM:614420 |
Orphanet:300345 |
autosomal systemic lupus erythematosus type 16 |
MONDO:0030073 |
OMIM:618960 |
- |
Mitchell syndrome |
MONDO:0013000 |
OMIM:612740 |
Orphanet:100924 |
porphyria due to ALA dehydratase deficiency |
MONDO:0060555 |
OMIM:617661 |
- |
vertebral, cardiac, renal, and limb defects syndrome 2 |
MONDO:0008310 |
OMIM:176670 |
Orphanet:740 |
Hutchinson-Gilford progeria syndrome |
MONDO:0020788 |
OMIM:618314 |
- |
hypomagnesemia, seizures, and intellectual disability 2 |
MONDO:0012831 |
OMIM:612244 |
- |
inflammatory bowel disease 13 |
MONDO:0007272 |
OMIM:277350 |
Orphanet:199285 |
hereditary hypercarotenemia and vitamin A deficiency |
MONDO:0010799 |
OMIM:580000 |
Orphanet:168609 |
deafness, aminoglycoside-induced |
MONDO:0013685 |
OMIM:614320 |
Orphanet:1333 |
pancreatic cancer, susceptibility to, 4 |
MONDO:0011402 |
OMIM:604168 |
Orphanet:48431 |
congenital cataracts-facial dysmorphism-neuropathy syndrome |
MONDO:0012132 |
OMIM:608812 |
- |
colorectal cancer, susceptibility to, 1 |
MONDO:0014142 |
OMIM:615352 |
Orphanet:363623 |
autosomal recessive limb-girdle muscular dystrophy type 2T |
MONDO:0032733 |
OMIM:618412 |
- |
global developmental delay, progressive ataxia, and elevated glutamine |
MONDO:0012866 |
OMIM:612319 |
Orphanet:171629 |
hereditary spastic paraplegia 35 |
MONDO:0019828 |
- |
Orphanet:95496 |
pituitary stalk interruption syndrome |
MONDO:0021022 |
OMIM:614619 |
Orphanet:3197 |
hereditary hyperekplexia |
MONDO:0100218 |
OMIM:618947 |
- |
arthrogryposis multiplex congenita 5 |
MONDO:0032792 |
OMIM:618511 |
- |
neuropathy, hereditary motor and sensory, type VIc, with optic atrophy |
MONDO:0018995 |
- |
Orphanet:64749 |
Charcot-Marie-Tooth disease type 4 |
MONDO:0017893 |
OMIM:601626 |
Orphanet:319465 |
inherited acute myeloid leukemia |
MONDO:0011629 |
OMIM:606056 |
Orphanet:79330 |
MOGS-CDG |
MONDO:0032612 |
OMIM:618229 |
- |
mitochondrial complex 1 deficiency, nuclear type 7 |
MONDO:0013533 |
OMIM:614025 |
Orphanet:140905 |
hyperlipidemia due to hepatic triglyceride lipase deficiency |
MONDO:0014543 |
OMIM:616228 |
Orphanet:590 |
congenital myasthenic syndrome 14 |
MONDO:0024557 |
OMIM:604391 |
Orphanet:251347 |
ataxia-telangiectasia-like disorder 1 |
MONDO:0013493 |
OMIM:613933 |
- |
acetyl-coa carboxylase deficiency |
MONDO:0017575 |
OMIM:613662 |
Orphanet:298 |
mitochondrial neurogastrointestinal encephalomyopathy |
MONDO:0020777 |
OMIM:618324 |
- |
congenital disorder of glycosylation with defective fucosylation 2 |
MONDO:0015466 |
OMIM:259100 |
Orphanet:1525 |
cranio-osteoarthropathy |
MONDO:0008641 |
OMIM:192315 |
Orphanet:247691 |
retinal vasculopathy with cerebral leukoencephalopathy and systemic manifestations |
MONDO:0014375 |
OMIM:615863 |
Orphanet:329242 |
congenital diarrhea 7 with exudative enteropathy |
MONDO:0014551 |
OMIM:616255 |
- |
short stature with nonspecific skeletal abnormalities |
MONDO:0060532 |
OMIM:617602 |
- |
congenital heart defects and skeletal malformations syndrome |
MONDO:0010077 |
OMIM:271665 |
Orphanet:93358 |
spondyloepimetaphyseal dysplasia-short limb-abnormal calcification syndrome |
MONDO:0008546 |
OMIM:187600 |
Orphanet:2655 |
thanatophoric dysplasia type 1 |
MONDO:0009785 |
OMIM:258480 |
Orphanet:2746 |
opsismodysplasia |
MONDO:0010023 |
OMIM:269840 |
Orphanet:911 |
combined immunodeficiency due to ZAP70 deficiency |
MONDO:0018333 |
- |
Orphanet:394532 |
multiple acyl-CoA dehydrogenase deficiency, mild type |
MONDO:0020434 |
- |
Orphanet:99103 |
atrial septal defect, ostium secundum type |
MONDO:0033362 |
OMIM:617389 |
Orphanet:1934 |
developmental and epileptic encephalopathy, 53 |
MONDO:0009231 |
OMIM:609441 |
Orphanet:2639 |
acromesomelic dysplasia 2B |
MONDO:0033367 |
OMIM:617830 |
- |
developmental and epileptic encephalopathy, 58 |
MONDO:0012477 |
OMIM:610359 |
- |
retinitis pigmentosa 33 |
MONDO:0000141 |
OMIM:614114 |
Orphanet:1052 |
mosaic variegated aneuploidy syndrome |
MONDO:0011393 |
OMIM:604091 |
- |
hypoalphalipoproteinemia, primary, 1 |
MONDO:0012833 |
OMIM:612247 |
Orphanet:93262 |
Crouzon syndrome-acanthosis nigricans syndrome |
MONDO:0034092 |
- |
Orphanet:543470 |
optic atrophy-ataxia-peripheral neuropathy-global developmental delay syndrome |
MONDO:0008005 |
OMIM:157800 |
Orphanet:3238 |
cardiospondylocarpofacial syndrome |
MONDO:0013925 |
OMIM:614857 |
Orphanet:369955 |
methylmalonic acidemia with homocystinuria, type cblJ |
MONDO:0005138 |
OMIM:211980 |
- |
lung carcinoma |
MONDO:0019635 |
OMIM:200400 |
Orphanet:930 |
idiopathic achalasia |
MONDO:0001567 |
- |
- |
nephrocalcinosis |
MONDO:0014439 |
OMIM:615988 |
- |
Bardet-Biedl syndrome 11 |
MONDO:0009667 |
OMIM:253280 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A3 |
MONDO:0011658 |
OMIM:606324 |
Orphanet:2828 |
autosomal recessive early-onset Parkinson disease 7 |
MONDO:0010810 |
OMIM:600081 |
Orphanet:289157 |
vitamin D hydroxylation-deficient rickets, type 1B |
MONDO:0012136 |
OMIM:608836 |
Orphanet:228308 |
carnitine palmitoyl transferase II deficiency, neonatal form |
MONDO:0024309 |
OMIM:201300 |
Orphanet:970 |
neuropathy, hereditary sensory and autonomic, type 2A |
MONDO:0020628 |
OMIM:618097 |
Orphanet:508512 |
microcephaly, growth restriction, and increased sister chromatid exchange 2 |
MONDO:0013361 |
OMIM:613679 |
Orphanet:325 |
congenital prothrombin deficiency |
MONDO:0012368 |
OMIM:609924 |
Orphanet:137754 |
aminoacylase 1 deficiency |
MONDO:0016982 |
- |
Orphanet:263413 |
angiosarcoma |
MONDO:0014359 |
OMIM:615830 |
- |
pigmented nodular adrenocortical disease, primary, 4 |
MONDO:0100220 |
OMIM:619013 |
- |
Rajab interstitial lung disease with brain calcifications 2 |
MONDO:0019448 |
OMIM:615400 |
Orphanet:86814 |
benign adult familial myoclonic epilepsy |
MONDO:0021105 |
OMIM:613282 |
- |
NAFLD1 |
MONDO:0012407 |
OMIM:610090 |
Orphanet:79096 |
pyridoxal phosphate-responsive seizures |
MONDO:0017830 |
- |
Orphanet:314911 |
severe Canavan disease |
MONDO:0018144 |
OMIM:616228 |
Orphanet:353327 |
congenital myasthenic syndromes with glycosylation defect |
MONDO:0013158 |
OMIM:613154 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A6 |
MONDO:0011150 |
OMIM:601812 |
Orphanet:363665 |
acroosteolysis-keloid-like lesions-premature aging syndrome |
MONDO:0009916 |
OMIM:264300 |
Orphanet:752 |
46,XY disorder of sex development due to 17-beta-hydroxysteroid dehydrogenase 3 deficiency |
MONDO:0019046 |
- |
Orphanet:68356 |
leukodystrophy |
MONDO:0035363 |
- |
- |
obsolete IRF2BPL-related regressive neurodevelopmental disorder-dystonia-seizures syndrome |
MONDO:0010221 |
OMIM:280000 |
Orphanet:3474 |
CHIME syndrome |
MONDO:0008603 |
OMIM:190440 |
Orphanet:3366 |
trigonocephaly 1 |
MONDO:0010592 |
OMIM:305600 |
Orphanet:2092 |
focal dermal hypoplasia |
MONDO:0010487 |
OMIM:300919 |
- |
intellectual disability, X-linked 99 |
MONDO:0009529 |
OMIM:246900 |
Orphanet:765 |
pyruvate dehydrogenase E3 deficiency |
MONDO:0013469 |
OMIM:613862 |
- |
retinitis pigmentosa 38 |
MONDO:0018931 |
OMIM:252605 |
Orphanet:577 |
mucolipidosis type III |
MONDO:0010584 |
OMIM:305000 |
Orphanet:3322 |
dyskeratosis congenita, X-linked |
MONDO:0012500 |
OMIM:610448 |
Orphanet:90280 |
chilblain lupus 1 |
MONDO:0009856 |
OMIM:261540 |
Orphanet:709 |
Peters plus syndrome |
MONDO:0018114 |
OMIM:616602 |
Orphanet:35099 |
isolated brachycephaly |
MONDO:0008940 |
OMIM:213002 |
Orphanet:85186 |
endosteal sclerosis-cerebellar hypoplasia syndrome |
MONDO:0054862 |
OMIM:618096 |
- |
premature ovarian failure 15 |
MONDO:0013125 |
OMIM:613089 |
Orphanet:168984 |
CLAPO syndrome |
MONDO:0013588 |
OMIM:614129 |
Orphanet:2855 |
Perrault syndrome 3 |
MONDO:0018770 |
OMIM:617088 |
Orphanet:474 |
Jeune syndrome |
MONDO:0012012 |
OMIM:608323 |
Orphanet:100045 |
Charcot-Marie-Tooth disease dominant intermediate C |
MONDO:0032613 |
OMIM:618230 |
- |
mitochondrial complex 1 deficiency, nuclear type 8 |
MONDO:0009662 |
OMIM:253220 |
Orphanet:584 |
mucopolysaccharidosis type 7 |
MONDO:0014704 |
OMIM:616592 |
Orphanet:477831 |
skeletal overgrowth-craniofacial dysmorphism-hyperelastic skin-white matter lesions syndrome |
MONDO:0009910 |
OMIM:264090 |
Orphanet:3455 |
Wiedemann-Rautenstrauch syndrome |
MONDO:0007412 |
OMIM:123790 |
Orphanet:1555 |
Beare-Stevenson cutis gyrata syndrome |
MONDO:0009123 |
OMIM:223360 |
Orphanet:230 |
dopamine beta-hydroxylase deficiency |
MONDO:0010497 |
OMIM:300958 |
- |
intellectual disability, X-linked 102 |
MONDO:0008315 |
OMIM:614731 |
- |
prostate cancer |
MONDO:0008293 |
OMIM:175900 |
Orphanet:79152 |
porokeratosis 3, disseminated superficial actinic type |
MONDO:0013765 |
OMIM:614466 |
- |
coronary heart disease, susceptibility to, 6 |
MONDO:0010167 |
OMIM:276880 |
Orphanet:210128 |
urocanic aciduria |
MONDO:0017695 |
OMIM:232500 |
Orphanet:308621 |
glycogen storage disease due to glycogen branching enzyme deficiency, progressive hepatic form |
MONDO:0001056 |
OMIM:613659 |
Orphanet:63443 |
gastric cancer |
MONDO:0013129 |
OMIM:613093 |
Orphanet:49382 |
cone dystrophy 4 |
MONDO:0054833 |
OMIM:618036 |
Orphanet:521414 |
charcot-marie-tooth disease, axonal, type 2DD |
MONDO:0007749 |
- |
- |
obsolete autosomal recessive infantile hypercalcemia |
MONDO:0013836 |
OMIM:614650 |
Orphanet:280406 |
familial steroid-resistant nephrotic syndrome with sensorineural deafness |
MONDO:0033968 |
- |
Orphanet:529977 |
immune dysregulation-inflammatory bowel disease-arthritis-recurrent infections-lymphopenia syndrome |
MONDO:0013986 |
OMIM:614946 |
Orphanet:319519 |
combined oxidative phosphorylation defect type 14 |
MONDO:0014892 |
OMIM:617061 |
Orphanet:476126 |
micrognathia-recurrent infections-behavioral abnormalities-mild intellectual disability syndrome |
MONDO:0014057 |
OMIM:615135 |
Orphanet:511 |
maple syrup urine disease, mild variant |
MONDO:0007342 |
OMIM:119800 |
Orphanet:293150 |
clubfoot |
MONDO:0015717 |
- |
Orphanet:169799 |
mild hemophilia B |
MONDO:0008862 |
OMIM:210210 |
Orphanet:6 |
3-methylcrotonyl-CoA carboxylase 2 deficiency |
MONDO:0032820 |
OMIM:618577 |
- |
neurodevelopmental disorder with structural brain anomalies and dysmorphic facies |
MONDO:0033532 |
OMIM:618950 |
- |
Suleiman-El-Hattab syndrome |
MONDO:0007299 |
OMIM:117550 |
Orphanet:821 |
Sotos syndrome 1 |
MONDO:0011540 |
OMIM:605361 |
Orphanet:98763 |
spinocerebellar ataxia type 14 |
MONDO:0012466 |
OMIM:610297 |
Orphanet:2828 |
Parkinson disease 13, autosomal dominant, susceptibility to |
MONDO:0010637 |
OMIM:308800 |
Orphanet:2340 |
keratosis follicularis spinulosa decalvans, X-linked |
MONDO:0013549 |
OMIM:614063 |
- |
N-acetylaspartate deficiency |
MONDO:0021571 |
OMIM:126200 |
- |
multiple sclerosis, susceptibility to 1 |
MONDO:0032807 |
OMIM:618547 |
- |
neurodevelopmental disorder with visual defects and brain anomalies |
MONDO:0009865 |
OMIM:261670 |
Orphanet:97234 |
glycogen storage disease due to phosphoglycerate mutase deficiency |
MONDO:0009300 |
OMIM:233400 |
Orphanet:2855 |
Perrault syndrome 1 |
MONDO:0032673 |
OMIM:618317 |
- |
basal ganglia calcification, idiopathic, 7, autosomal recessive |
MONDO:0011758 |
OMIM:607014 |
Orphanet:93473 |
Hurler syndrome |
MONDO:0009161 |
OMIM:225410 |
Orphanet:1901 |
Ehlers-Danlos syndrome, dermatosparaxis type |
MONDO:0030913 |
OMIM:617751 |
Orphanet:500159 |
intellectual disability, autosomal dominant 48 |
MONDO:0013159 |
OMIM:613155 |
Orphanet:370968 |
muscular dystrophy-dystroglycanopathy (congenital with intellectual disability), type B1 |
MONDO:0018765 |
- |
Orphanet:468635 |
cryptogenic multifocal ulcerous stenosing enteritis |
MONDO:0008170 |
OMIM:607893 |
Orphanet:213500 |
ovarian cancer |
MONDO:0013489 |
OMIM:613916 |
Orphanet:90636 |
autosomal recessive nonsyndromic hearing loss 89 |
MONDO:0007924 |
OMIM:153480 |
Orphanet:109 |
Bannayan-Riley-Ruvalcaba syndrome |
MONDO:0009947 |
OMIM:266130 |
Orphanet:32 |
glutathione synthetase deficiency with 5-oxoprolinuria |
MONDO:0014882 |
OMIM:617046 |
Orphanet:466722 |
hereditary spastic paraplegia 77 |
MONDO:0009458 |
OMIM:242900 |
Orphanet:1830 |
Schimke immuno-osseous dysplasia |
MONDO:0017729 |
- |
Orphanet:309256 |
metachromatic leukodystrophy, late infantile form |
MONDO:0060568 |
OMIM:617682 |
Orphanet:529965 |
Pilarowski-Bjornsson syndrome |
MONDO:0014255 |
OMIM:615561 |
- |
complement factor b deficiency |
MONDO:0010644 |
OMIM:308990 |
Orphanet:93622 |
proteinuria, low molecular weight, with hypercalciuria and nephrocalcinosis |
MONDO:0007781 |
OMIM:145500 |
- |
essential hypertension, genetic |
MONDO:0014011 |
OMIM:615024 |
Orphanet:79394 |
autosomal recessive congenital ichthyosis 10 |
MONDO:0015015 |
OMIM:617308 |
- |
congenital bile acid synthesis defect 6 |
MONDO:0014904 |
OMIM:617082 |
- |
congenital disorder of glycosylation, type IAA |
MONDO:0015356 |
- |
Orphanet:140162 |
hereditary neoplastic syndrome |
MONDO:0014224 |
OMIM:615516 |
Orphanet:329195 |
developmental delay with autism spectrum disorder and gait instability |
MONDO:0008757 |
OMIM:610753 |
Orphanet:701 |
alopecia universalis congenita |
MONDO:0014719 |
OMIM:616647 |
Orphanet:457375 |
developmental and epileptic encephalopathy, 35 |
MONDO:0008918 |
OMIM:212138 |
Orphanet:159 |
carnitine-acylcarnitine translocase deficiency |
MONDO:0014767 |
OMIM:616777 |
- |
Seckel syndrome 9 |
MONDO:0004976 |
- |
Orphanet:803 |
amyotrophic lateral sclerosis |
MONDO:0017839 |
- |
Orphanet:315306 |
classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency, salt wasting form |
MONDO:0019087 |
OMIM:615619 |
Orphanet:70567 |
cholangiocarcinoma |
MONDO:0013767 |
OMIM:614470 |
Orphanet:268114 |
autoimmune lymphoproliferative syndrome type 4 |
MONDO:0032795 |
OMIM:618522 |
- |
intellectual developmental disorder 59 |
MONDO:0018332 |
- |
Orphanet:394529 |
multiple acyl-CoA dehydrogenase deficiency, severe neonatal type |
MONDO:0007648 |
OMIM:137215 |
Orphanet:26106 |
hereditary diffuse gastric adenocarcinoma |
MONDO:0030921 |
OMIM:617831 |
- |
intellectual disability, autosomal dominant 55, with seizures |
MONDO:0013380 |
OMIM:613707 |
Orphanet:500 |
LEOPARD syndrome 3 |
MONDO:0008048 |
OMIM:614408 |
Orphanet:169189 |
autosomal dominant centronuclear myopathy |
MONDO:0014511 |
OMIM:616155 |
Orphanet:443073 |
Charcot-Marie-Tooth disease axonal type 2S |
MONDO:0010683 |
OMIM:310400 |
Orphanet:596 |
X-linked centronuclear myopathy |
MONDO:0014636 |
OMIM:616430 |
Orphanet:447954 |
combined oxidative phosphorylation defect type 25 |
MONDO:0009612 |
OMIM:251000 |
Orphanet:79312 |
methylmalonic aciduria due to methylmalonyl-CoA mutase deficiency |
MONDO:0012481 |
OMIM:610377 |
Orphanet:29 |
mevalonic aciduria |
MONDO:0060596 |
OMIM:617755 |
Orphanet:528084 |
neurodevelopmental disorder with dysmorphic facies and distal limb anomalies |
MONDO:0007765 |
OMIM:144755 |
Orphanet:443098 |
hyperostosis cranialis interna |
MONDO:0022113 |
OMIM:618352 |
- |
central centrifugal cicatricial alopecia |
MONDO:0010379 |
OMIM:300615 |
Orphanet:3057 |
Brunner syndrome |
MONDO:0020684 |
OMIM:130080 |
- |
Ehlers-Danlos syndrome, periodontal type 1 |
MONDO:0007042 |
OMIM:101400 |
Orphanet:794 |
Saethre-Chotzen syndrome |
MONDO:0017809 |
OMIM:606693 |
Orphanet:314632 |
parkinsonism due to ATP13A2 deficiency |
MONDO:0034104 |
- |
Orphanet:544488 |
global developmental delay-alopecia-macrocephaly-facial dysmorphism-structural brain anomalies syndrome |
MONDO:0008815 |
OMIM:207900 |
Orphanet:23 |
argininosuccinic aciduria |
MONDO:0009849 |
OMIM:260920 |
Orphanet:343 |
hyperimmunoglobulinemia D with periodic fever |
MONDO:0014085 |
OMIM:615219 |
Orphanet:2185 |
hydrocephalus, nonsyndromic, autosomal recessive 2 |
MONDO:0012526 |
OMIM:610618 |
Orphanet:91378 |
hereditary angioedema type 3 |
MONDO:0017564 |
- |
Orphanet:295239 |
macrodactyly of fingers, unilateral |
MONDO:0008093 |
OMIM:162900 |
Orphanet:79414 |
nevus, epidermal |
MONDO:0017950 |
- |
Orphanet:324761 |
microcephalic primordial dwarfism |
MONDO:0014736 |
OMIM:616688 |
Orphanet:466768 |
Charcot-Marie-Tooth disease axonal type 2Z |
MONDO:0012984 |
OMIM:612674 |
Orphanet:171848 |
PHARC syndrome |
MONDO:0005144 |
OMIM:616437 |
- |
familial amyotrophic lateral sclerosis |
MONDO:0013944 |
OMIM:614878 |
Orphanet:324530 |
autoinflammation-PLCG2-associated antibody deficiency-immune dysregulation |
MONDO:0013224 |
OMIM:613325 |
Orphanet:69077 |
rhabdoid tumor predisposition syndrome 2 |
MONDO:0004989 |
- |
- |
breast carcinoma |
MONDO:0013161 |
OMIM:613157 |
Orphanet:206564 |
autosomal recessive limb-girdle muscular dystrophy type 2O |
MONDO:0018419 |
- |
Orphanet:401820 |
autosomal recessive spastic paraplegia type 67 |
MONDO:0032862 |
OMIM:618667 |
- |
hydrocephalus, congenital communicating, 1 |
MONDO:0014500 |
OMIM:616117 |
Orphanet:436242 |
atrial conduction disease |
MONDO:0014850 |
OMIM:616959 |
- |
retinitis pigmentosa and erythrocytic microcytosis |
MONDO:0010479 |
OMIM:300905 |
Orphanet:352675 |
Charcot-Marie-Tooth disease X-linked dominant 6 |
MONDO:0020729 |
OMIM:601495 |
Orphanet:33110 |
autosomal recessive agammaglobulinemia 1 |
MONDO:0012123 |
OMIM:608799 |
Orphanet:79322 |
congenital disorder of glycosylation type 1E |
MONDO:0034186 |
- |
Orphanet:562538 |
autosomal recessive extra-oral halitosis |
MONDO:0009267 |
OMIM:231000 |
Orphanet:77261 |
Gaucher disease type III |
MONDO:0014576 |
OMIM:616299 |
Orphanet:401862 |
lipoyl transferase 1 deficiency |
MONDO:0020682 |
OMIM:130070 |
- |
Ehlers-Danlos syndrome, spondylodysplastic type, 1 |
MONDO:0014489 |
OMIM:616094 |
Orphanet:445110 |
limb-girdle muscular dystrophy due to POMK deficiency |
MONDO:0009520 |
OMIM:246450 |
Orphanet:20 |
3-hydroxy-3-methylglutaric aciduria |
MONDO:0008436 |
OMIM:182410 |
Orphanet:820 |
Sneddon syndrome |
MONDO:0002629 |
OMIM:259500 |
Orphanet:668 |
bone osteosarcoma |
MONDO:0012204 |
OMIM:609153 |
Orphanet:90044 |
familial pseudohyperkalemia |
MONDO:0007963 |
OMIM:155600 |
Orphanet:618 |
melanoma, cutaneous malignant, susceptibility to, 1 |
MONDO:0044903 |
- |
- |
myelofibrosis |
MONDO:0032873 |
OMIM:618697 |
- |
retinitis pigmentosa 87 with choroidal involvement |
MONDO:0013808 |
OMIM:614569 |
Orphanet:163634 |
Maffucci syndrome |
MONDO:0008664 |
- |
- |
obsolete autosomal dominant neovascular inflammatory vitreoretinopathy |
MONDO:0012556 |
OMIM:610768 |
Orphanet:91131 |
DK1-CDG |
MONDO:0019682 |
- |
Orphanet:93400 |
congenital sialidosis type 2 |
MONDO:0013171 |
OMIM:613179 |
Orphanet:760 |
purine nucleoside phosphorylase deficiency |
MONDO:0014209 |
OMIM:615491 |
Orphanet:352654 |
early-onset progressive neurodegeneration-blindness-ataxia-spasticity syndrome |
MONDO:0007068 |
OMIM:103050 |
Orphanet:46 |
adenylosuccinate lyase deficiency |
MONDO:0011945 |
OMIM:608013 |
Orphanet:85212 |
Gaucher disease perinatal lethal |
MONDO:0009281 |
OMIM:231670 |
Orphanet:25 |
glutaryl-CoA dehydrogenase deficiency |
MONDO:0008267 |
OMIM:174300 |
Orphanet:2919 |
orofaciodigital syndrome V |
MONDO:0014935 |
OMIM:617137 |
- |
frontometaphyseal dysplasia 2 |
MONDO:0010461 |
OMIM:300860 |
Orphanet:163956 |
syndromic X-linked intellectual disability Nascimento type |
MONDO:0017401 |
OMIM:610193 |
Orphanet:293888 |
familial isolated arrhythmogenic ventricular dysplasia, left dominant form |
MONDO:0019258 |
- |
Orphanet:79253 |
mild phenylketonuria |
MONDO:0012419 |
OMIM:610149 |
- |
age related macular degeneration 7 |
MONDO:0014555 |
OMIM:616265 |
Orphanet:263548 |
peeling skin syndrome type A |
MONDO:0008817 |
OMIM:208000 |
Orphanet:51608 |
arterial calcification, generalized, of infancy, 1 |
MONDO:0030074 |
OMIM:618961 |
- |
spondylometaphyseal dysplasia with corneal dystrophy |
MONDO:0007979 |
OMIM:156250 |
Orphanet:2499 |
metachondromatosis |
MONDO:0007958 |
OMIM:155240 |
Orphanet:99361 |
familial medullary thyroid carcinoma |
MONDO:0032775 |
OMIM:618480 |
- |
neurodevelopmental disorder with seizures and speech and walking impairment |
MONDO:0007803 |
- |
Orphanet:102 |
multiple system atrophy |
MONDO:0009352 |
OMIM:236200 |
Orphanet:394 |
classic homocystinuria |
MONDO:0014407 |
OMIM:615937 |
Orphanet:83473 |
megalencephaly-polymicrogyria-polydactyly-hydrocephalus syndrome 2 |
MONDO:0013439 |
OMIM:613812 |
Orphanet:79302 |
congenital bile acid synthesis defect 3 |
MONDO:0010133 |
OMIM:274500 |
Orphanet:95716 |
thyroid dyshormonogenesis 2A |
MONDO:0009821 |
OMIM:259775 |
Orphanet:1832 |
lethal osteosclerotic bone dysplasia |
MONDO:0012282 |
OMIM:609465 |
Orphanet:2725 |
Al-Gazali syndrome |
MONDO:0010392 |
OMIM:300653 |
Orphanet:713 |
glycogen storage disease due to phosphoglycerate kinase 1 deficiency |
MONDO:0010427 |
OMIM:300799 |
- |
syndromic X-linked intellectual disability Raymond type |
MONDO:0012679 |
OMIM:611497 |
Orphanet:210110 |
autosomal recessive osteopetrosis 6 |
MONDO:0044299 |
OMIM:616224 |
Orphanet:590 |
myasthenic syndrome, congenital, 22 |
MONDO:0012980 |
OMIM:612651 |
Orphanet:199332 |
endocrine-cerebro-osteodysplasia syndrome |
MONDO:0015557 |
- |
Orphanet:158775 |
Smouldering systemic mastocytosis |
MONDO:0018348 |
- |
- |
obsolete polyglucosan body myopathy type 1 |
MONDO:0013404 |
OMIM:613752 |
Orphanet:88618 |
hypermethioninemia with deficiency of S-adenosylhomocysteine hydrolase |
MONDO:0033566 |
OMIM:619012 |
- |
combined oxidative phosphorylation deficiency 48 |
MONDO:0007064 |
OMIM:102700 |
Orphanet:277 |
severe combined immunodeficiency, autosomal recessive, T cell-negative, B cell-negative, NK cell-negative, due to adenosine deaminase deficiency |
MONDO:0032829 |
OMIM:618603 |
- |
neurodevelopmental disorder with hypotonia and variable intellectual and behavioral abnormalities |
MONDO:0019002 |
OMIM:158350 |
Orphanet:65285 |
Lhermitte-Duclos disease |
MONDO:0009945 |
OMIM:617290 |
Orphanet:3006 |
pyridoxine-dependent epilepsy |
MONDO:0032923 |
OMIM:618800 |
- |
spinocerebellar ataxia, autosomal recessive 28 |
MONDO:0006486 |
OMIM:606661 |
Orphanet:39044 |
uveal melanoma |
MONDO:0013800 |
OMIM:614557 |
Orphanet:300179 |
Ehlers-Danlos syndrome, kyphoscoliotic and deafness type |
MONDO:0012747 |
OMIM:611881 |
Orphanet:57 |
glycogen storage disease due to aldolase A deficiency |
MONDO:0008830 |
OMIM:208400 |
Orphanet:93 |
aspartylglucosaminuria |
MONDO:0013946 |
OMIM:614880 |
Orphanet:478 |
hypogonadotropic hypogonadism 15 with or without anosmia |
MONDO:0013997 |
OMIM:614974 |
Orphanet:398189 |
focal facial dermal dysplasia type IV |
MONDO:0013859 |
OMIM:614691 |
Orphanet:91492 |
cataract 38 |
MONDO:0014310 |
OMIM:615704 |
Orphanet:221043 |
hereditary sclerosing poikiloderma with tendon and pulmonary involvement |
MONDO:0011230 |
OMIM:602475 |
- |
ossification of the posterior longitudinal ligament of the spine |
MONDO:0017385 |
OMIM:616645 |
Orphanet:293181 |
malignant migrating partial seizures of infancy |
MONDO:0012444 |
OMIM:610217 |
Orphanet:35069 |
neurodegeneration with brain iron accumulation 2B |
MONDO:0018610 |
- |
Orphanet:441447 |
early-onset posterior subcapsular cataract |
MONDO:0017337 |
- |
Orphanet:289548 |
inherited isolated adrenal insufficiency due to partial CYP11A1 deficiency |
MONDO:0014886 |
OMIM:617051 |
Orphanet:488627 |
severe growth deficiency-strabismus-extensive dermal melanocytosis-intellectual disability syndrome |
MONDO:0008722 |
OMIM:201470 |
Orphanet:26792 |
short chain acyl-CoA dehydrogenase deficiency |
MONDO:0009891 |
OMIM:263300 |
Orphanet:729 |
acquired polycythemia vera |
MONDO:0007402 |
OMIM:123320 |
- |
creatine phosphokinase, elevated serum |
MONDO:0018155 |
OMIM:611637 |
Orphanet:35689 |
lateral sclerosis |
MONDO:0014824 |
OMIM:616901 |
Orphanet:459061 |
craniofacial dysplasia-short stature-ectodermal anomalies-intellectual disability syndrome |
MONDO:0011801 |
OMIM:607250 |
Orphanet:94124 |
spinocerebellar ataxia, autosomal recessive, with axonal neuropathy 1 |
MONDO:0010463 |
OMIM:300863 |
Orphanet:163966 |
X-linked dominant chondrodysplasia, Chassaing-Lacombe type |
MONDO:0014919 |
OMIM:617108 |
- |
sessile serrated polyposis cancer syndrome |
MONDO:0010447 |
OMIM:300844 |
Orphanet:777 |
intellectual disability, X-linked 19 |
MONDO:0032880 |
OMIM:618721 |
- |
developmental and epileptic encephalopathy, 82 |
MONDO:0020851 |
OMIM:618110 |
- |
spermatogenic failure 30 |
MONDO:0018006 |
- |
Orphanet:329478 |
adult-onset distal myopathy due to VCP mutation |
MONDO:0009583 |
OMIM:249620 |
Orphanet:2728 |
blepharophimosis - intellectual disability syndrome, Ohdo type |
MONDO:0009692 |
OMIM:254450 |
Orphanet:824 |
primary myelofibrosis |
MONDO:0016547 |
OMIM:130650 |
Orphanet:238613 |
Beckwith-Wiedemann syndrome due to NSD1 mutation |
MONDO:0030009 |
OMIM:618840 |
- |
alopecia-intellectual disability syndrome 4 |
MONDO:0019625 |
OMIM:617168 |
Orphanet:91387 |
familial thoracic aortic aneurysm and aortic dissection |
MONDO:0009255 |
OMIM:230200 |
Orphanet:79237 |
galactokinase deficiency |
MONDO:0009380 |
OMIM:237500 |
Orphanet:234 |
Dubin-Johnson syndrome |
MONDO:0007620 |
OMIM:136120 |
Orphanet:79292 |
fish eye disease |
MONDO:0009655 |
OMIM:252900 |
Orphanet:79269 |
Sanfilippo syndrome type A |
MONDO:0008021 |
OMIM:158350 |
Orphanet:65285 |
Cowden syndrome 1 |
MONDO:0007204 |
OMIM:112240 |
Orphanet:2050 |
Cole-Carpenter syndrome 1 |
MONDO:0016063 |
OMIM:616858 |
Orphanet:201 |
Cowden disease |
MONDO:0019200 |
OMIM:617123 |
Orphanet:791 |
retinitis pigmentosa |
MONDO:0014398 |
OMIM:615918 |
Orphanet:420733 |
combined oxidative phosphorylation defect type 21 |
MONDO:0013398 |
OMIM:613737 |
- |
acne inversa, familial, 3 |
MONDO:0010877 |
OMIM:600361 |
Orphanet:64751 |
Charcot-Marie-Tooth disease type 5 |
MONDO:0014545 |
OMIM:616230 |
Orphanet:424027 |
progressive myoclonic epilepsy type 8 |
MONDO:0017243 |
- |
Orphanet:280785 |
bullous diffuse cutaneous mastocytosis |
MONDO:0009252 |
OMIM:229800 |
Orphanet:2056 |
essential fructosuria |
MONDO:0032899 |
OMIM:618752 |
- |
neutropenia, severe congenital, 8, autosomal dominant |
MONDO:0012640 |
OMIM:611228 |
Orphanet:139515 |
Charcot-Marie-Tooth disease type 4J |
MONDO:0005375 |
- |
- |
nasopharyngeal neoplasm |
MONDO:0032905 |
OMIM:618768 |
- |
spastic paraplegia 81, autosomal recessive |
MONDO:0008647 |
OMIM:192600 |
- |
hypertrophic cardiomyopathy 1 |
MONDO:0009866 |
OMIM:261680 |
Orphanet:79316 |
phosphoenolpyruvate carboxykinase deficiency, cytosolic |
MONDO:0009009 |
OMIM:217090 |
Orphanet:722 |
hypoplasminogenemia |
MONDO:0003608 |
- |
Orphanet:98673 |
optic atrophy |
MONDO:0024519 |
OMIM:191830 |
Orphanet:411709 |
renal hypodysplasia/aplasia 1 |
MONDO:0010987 |
OMIM:601072 |
- |
autosomal recessive nonsyndromic hearing loss 8 |
MONDO:0030035 |
OMIM:618877 |
- |
leukoencephalopathy, developmental delay, and episodic neurologic regression syndrome |
MONDO:0014977 |
OMIM:617232 |
Orphanet:480682 |
autosomal recessive limb-girdle muscular dystrophy type 2Z |
MONDO:0011906 |
OMIM:607765 |
Orphanet:79301 |
congenital bile acid synthesis defect 1 |
MONDO:0008753 |
OMIM:203500 |
Orphanet:56 |
alkaptonuria |
MONDO:0020751 |
OMIM:618182 |
- |
orthostatic hypotension 2 |
MONDO:0024568 |
OMIM:615438 |
Orphanet:370088 |
infantile liver failure syndrome 1 |
MONDO:0012590 |
OMIM:610965 |
- |
XFE progeroid syndrome |
MONDO:0016647 |
OMIM:614284 |
Orphanet:250984 |
autosomal recessive Stickler syndrome |
MONDO:0013275 |
OMIM:613470 |
Orphanet:712 |
hemolytic anemia due to glucophosphate isomerase deficiency |
MONDO:0020667 |
OMIM:207410 |
- |
Antley-Bixler syndrome without genital anomalies or disordered steroidogenesis |
MONDO:0011362 |
OMIM:607569 |
Orphanet:34521 |
myopathy, myofibrillar, 9, with early respiratory failure |
MONDO:0033007 |
OMIM:617729 |
Orphanet:2065 |
Galloway-Mowat syndrome 3 |
MONDO:0014104 |
OMIM:615268 |
Orphanet:1766 |
cerebellar ataxia, intellectual disability, and dysequilibrium syndrome 4 |
MONDO:0008383 |
OMIM:604302 |
Orphanet:284130 |
rheumatoid arthritis |
MONDO:0014830 |
OMIM:616913 |
Orphanet:466806 |
platelet-type bleeding disorder 20 |
MONDO:0014598 |
OMIM:616346 |
Orphanet:2382 |
developmental and epileptic encephalopathy, 31 |
MONDO:0016589 |
OMIM:615851 |
Orphanet:247198 |
progressive cerebello-cerebral atrophy |
MONDO:0000208 |
OMIM:616033 |
- |
microcephaly, short stature, and impaired glucose metabolism 1 |
MONDO:0009515 |
OMIM:245900 |
Orphanet:79293 |
Norum disease |
MONDO:0013308 |
OMIM:613563 |
Orphanet:363972 |
CBL-related disorder |
MONDO:0008944 |
OMIM:213300 |
Orphanet:475 |
Joubert syndrome 1 |
MONDO:0014641 |
OMIM:616439 |
Orphanet:275872 |
frontotemporal dementia and/or amyotrophic lateral sclerosis 4 |
MONDO:0014234 |
OMIM:615537 |
Orphanet:178307 |
reticulate acropigmentation of Kitamura |
MONDO:0060666 |
OMIM:617915 |
- |
hypotonia, ataxia, developmental delay, and tooth enamel defect syndrome |
MONDO:0003441 |
- |
- |
dystonic disorder |
MONDO:0014112 |
OMIM:615278 |
Orphanet:1340 |
cardiofaciocutaneous syndrome 2 |
MONDO:0019660 |
- |
Orphanet:93259 |
Pfeiffer syndrome type 2 |
MONDO:0014510 |
OMIM:616154 |
Orphanet:438178 |
fatty acyl-CoA reductase 1 deficiency |
MONDO:0014944 |
OMIM:617157 |
Orphanet:464288 |
short stature-brachydactyly-obesity-global developmental delay syndrome |
MONDO:0007203 |
OMIM:112200 |
Orphanet:1059 |
blue rubber bleb nevus |
MONDO:0018298 |
OMIM:277950 |
Orphanet:371428 |
multicentric osteolysis-nodulosis-arthropathy spectrum |
MONDO:0032822 |
OMIM:618580 |
- |
developmental and epileptic encephalopathy, 80 |
MONDO:0044718 |
OMIM:617762 |
Orphanet:502444 |
alkaline ceramidase 3 deficiency |
MONDO:0009693 |
OMIM:254500 |
Orphanet:85443 |
plasma cell myeloma |
MONDO:0005578 |
- |
- |
arthritic joint disease |
MONDO:0030837 |
OMIM:619092 |
- |
neurodevelopmental disorder with microcephaly, impaired language, epilepsy, and gait abnormalities |
MONDO:0011541 |
OMIM:605362 |
Orphanet:217622 |
dilated cardiomyopathy 1J |
MONDO:0030036 |
OMIM:618878 |
- |
leukoencephalopathy, motor delay, spasticity, and dysarthria syndrome |
MONDO:0007747 |
OMIM:143860 |
Orphanet:542657 |
isolated hyperchlorhidrosis |
MONDO:0009661 |
OMIM:253200 |
Orphanet:583 |
mucopolysaccharidosis type 6 |
MONDO:0012172 |
OMIM:609015 |
Orphanet:746 |
mitochondrial trifunctional protein deficiency |
MONDO:0011365 |
OMIM:603736 |
Orphanet:3047 |
blepharophimosis - intellectual disability syndrome, SBBYS type |
MONDO:0007794 |
OMIM:146110 |
- |
hypogonadotropic hypogonadism 7 with or without anosmia |
MONDO:0009475 |
OMIM:243500 |
Orphanet:33 |
isovaleric acidemia |
MONDO:0008869 |
OMIM:210600 |
Orphanet:808 |
Seckel syndrome 1 |
MONDO:0018709 |
OMIM:300958 |
Orphanet:457260 |
X-linked intellectual disability-hypotonia-movement disorder syndrome |
MONDO:0009823 |
OMIM:259900 |
Orphanet:93598 |
primary hyperoxaluria type 1 |
MONDO:0033668 |
OMIM:619086 |
- |
hearing loss, autosomal dominant 79 |
MONDO:0014303 |
OMIM:615683 |
Orphanet:401810 |
hereditary spastic paraplegia 64 |
MONDO:0032842 |
OMIM:618635 |
- |
siddiqi syndrome |
MONDO:0007750 |
OMIM:143890 |
Orphanet:391665 |
hypercholesterolemia, familial, 1 |
MONDO:0017721 |
OMIM:268800 |
Orphanet:309155 |
Sandhoff disease, infantile form |
MONDO:0019799 |
OMIM:176100 |
Orphanet:95159 |
hepatoerythropoietic porphyria |
MONDO:0020769 |
OMIM:618333 |
- |
Menke-Hennekam syndrome 2 |
MONDO:0019311 |
OMIM:162900 |
Orphanet:79414 |
woolly hair nevus |
MONDO:0009689 |
OMIM:254210 |
Orphanet:98914 |
congenital myasthenic syndrome 6 |
MONDO:0019576 |
- |
Orphanet:90389 |
telangiectasia macularis eruptiva perstans |
MONDO:0013783 |
OMIM:614497 |
Orphanet:98938 |
microphthalmia, isolated, with coloboma 7 |
MONDO:0100340 |
OMIM:229300 |
- |
Friedreich ataxia 1 |
MONDO:0010687 |
OMIM:310468 |
Orphanet:93622 |
nephrolithiasis, X-linked recessive, with renal failure |
MONDO:0019182 |
OMIM:601665 |
Orphanet:77828 |
inherited obesity |
MONDO:0013843 |
OMIM:614665 |
Orphanet:314376 |
intestinal obstruction in the newborn due to guanylate cyclase 2C deficiency |
MONDO:0009339 |
OMIM:235555 |
Orphanet:79303 |
congenital bile acid synthesis defect 2 |
MONDO:0014991 |
OMIM:617253 |
- |
Seckel syndrome 10 |
MONDO:0012704 |
OMIM:611615 |
Orphanet:154 |
dilated cardiomyopathy 1X |
MONDO:0014843 |
OMIM:616946 |
- |
premature ovarian failure 11 |
MONDO:0016025 |
OMIM:616421 |
Orphanet:1942 |
myoclonic-astastic epilepsy |
MONDO:0018467 |
OMIM:219800 |
Orphanet:411629 |
nephropathic infantile cystinosis |
MONDO:0044325 |
OMIM:617784 |
- |
Fanconi anemia, complementation group W |
MONDO:0009400 |
OMIM:239500 |
Orphanet:419 |
hyperprolinemia type 1 |
MONDO:0007374 |
OMIM:121800 |
Orphanet:98967 |
Schnyder corneal dystrophy |
MONDO:0014832 |
OMIM:616917 |
Orphanet:488635 |
intellectual disability, autosomal recessive 53 |
MONDO:0011414 |
OMIM:612968 |
Orphanet:708 |
Peters anomaly |
MONDO:0018967 |
OMIM:307200 |
Orphanet:632 |
short stature due to isolated growth hormone deficiency with X-linked hypogammaglobulinemia |
MONDO:0012274 |
OMIM:609441 |
- |
acromesomelic dysplasia 3 |
MONDO:0014516 |
OMIM:616171 |
Orphanet:808 |
microcephaly and chorioretinopathy 2 |
MONDO:0009622 |
OMIM:251255 |
Orphanet:313795 |
Jawad syndrome |
MONDO:0012073 |
OMIM:608611 |
Orphanet:440706 |
ribose-5-P isomerase deficiency |
MONDO:0030966 |
OMIM:619194 |
- |
neurofacioskeletal syndrome with or without renal agenesis |
MONDO:0032837 |
OMIM:618620 |
- |
abdominal obesity-metabolic syndrome 4 |
MONDO:0014834 |
OMIM:616921 |
- |
dyskinesia, limb and orofacial, infantile-onset |
MONDO:0010826 |
OMIM:612269 |
Orphanet:64280 |
childhood absence epilepsy |
MONDO:0017723 |
OMIM:268800 |
Orphanet:309169 |
Sandhoff disease, adult form |
MONDO:0011066 |
OMIM:601382 |
Orphanet:99955 |
Charcot-Marie-Tooth disease type 4B1 |
MONDO:0014108 |
OMIM:615272 |
- |
Fanconi anemia complementation group Q |
MONDO:0014372 |
OMIM:615860 |
- |
cone-rod dystrophy 19 |
MONDO:0009973 |
OMIM:267500 |
Orphanet:33355 |
reticular dysgenesis |
MONDO:0033613 |
OMIM:619026 |
Orphanet:210141 |
neurodevelopmental disorder with progressive spasticity and brain white matter abnormalities |
MONDO:0000437 |
- |
Orphanet:102002 |
cerebellar ataxia |
MONDO:0010136 |
OMIM:274800 |
Orphanet:95716 |
thyroid dyshormonogenesis 4 |
MONDO:0005075 |
OMIM:188550 |
- |
thyroid gland papillary carcinoma |
MONDO:0032922 |
OMIM:618798 |
- |
Beck-Fahrner syndrome |
MONDO:0010665 |
OMIM:309585 |
Orphanet:3459 |
Wilson-Turner syndrome |
MONDO:0007429 |
OMIM:125250 |
Orphanet:1215 |
optic atrophy with or without deafness, ophthalmoplegia, myopathy, ataxia, and neuropathy |
MONDO:0013687 |
OMIM:614322 |
Orphanet:284282 |
autosomal recessive spinocerebellar ataxia 12 |
MONDO:0013108 |
OMIM:613065 |
Orphanet:513 |
leukemia, acute lymphocytic, susceptibility to, 1 |
MONDO:0011829 |
OMIM:607426 |
Orphanet:255249 |
coenzyme Q10 deficiency, primary, 1 |
MONDO:0014706 |
OMIM:616603 |
- |
cutis laxa, autosomal dominant 3 |
MONDO:0022435 |
- |
- |
Mauriac syndrome |
MONDO:0009894 |
OMIM:263520 |
Orphanet:93269 |
short-rib thoracic dysplasia 6 with or without polydactyly |
MONDO:0001595 |
OMIM:215450 |
Orphanet:1429 |
choreatic disease |
MONDO:0013619 |
OMIM:614196 |
- |
nephrotic syndrome, type 6 |
MONDO:0010703 |
OMIM:311250 |
Orphanet:664 |
ornithine carbamoyltransferase deficiency |
MONDO:0016310 |
- |
Orphanet:216986 |
Niemann-Pick disease type C, adult neurologic onset |
MONDO:0010172 |
OMIM:314390 |
Orphanet:3412 |
VACTERL with hydrocephalus |
MONDO:0023659 |
OMIM:619340 |
- |
developmental and epileptic encephalopathy 96 |
MONDO:0010222 |
OMIM:300000 |
Orphanet:306597 |
X-linked Opitz G/BBB syndrome |
MONDO:0060578 |
OMIM:617710 |
Orphanet:572798 |
neurodevelopmental disorder, mitochondrial, with abnormal movements and lactic acidosis, with or without seizures |
MONDO:0044339 |
OMIM:603932 |
- |
lumbar disc degenerative disorder |
MONDO:0009006 |
OMIM:217000 |
Orphanet:169147 |
complement component 2 deficiency |
MONDO:0018416 |
- |
Orphanet:401795 |
autosomal recessive spastic paraplegia type 59 |
MONDO:0032740 |
OMIM:618422 |
- |
hearing loss, autosomal recessive 100 |
MONDO:0017101 |
OMIM:607341 |
Orphanet:269001 |
isolated focal cortical dysplasia type IIa |
MONDO:0014174 |
OMIM:615415 |
Orphanet:294415 |
renal-hepatic-pancreatic dysplasia 2 |
MONDO:0007273 |
OMIM:115310 |
Orphanet:29072 |
paragangliomas 4 |
MONDO:0012991 |
OMIM:612713 |
Orphanet:168972 |
Kahrizi syndrome |
MONDO:0016304 |
- |
Orphanet:216866 |
classic pantothenate kinase-associated neurodegeneration |
MONDO:0009805 |
OMIM:259440 |
Orphanet:216820 |
osteogenesis imperfecta type 9 |
MONDO:0009796 |
OMIM:258870 |
Orphanet:414 |
ornithine aminotransferase deficiency |
MONDO:0013487 |
OMIM:613912 |
Orphanet:169467 |
recurrent Neisseria infections due to factor D deficiency |
MONDO:0014864 |
OMIM:617013 |
Orphanet:521406 |
hypermanganesemia with dystonia 2 |
MONDO:0011996 |
OMIM:608232 |
Orphanet:521 |
chronic myelogenous leukemia, BCR-ABL1 positive |
MONDO:0013042 |
OMIM:612924 |
Orphanet:93578 |
atypical hemolytic-uremic syndrome with B factor anomaly |
MONDO:0014120 |
OMIM:615287 |
Orphanet:899 |
muscular dystrophy-dystroglycanopathy (congenital with brain and eye anomalies), type A13 |
MONDO:0032730 |
OMIM:618404 |
- |
leukodystrophy, hypomyelinating, 18 |
MONDO:0018742 |
- |
Orphanet:464756 |
familial gastric type 1 neuroendocrine tumor |
MONDO:0016825 |
OMIM:251950 |
Orphanet:2597 |
mitochondrial myopathy-lactic acidosis-deafness syndrome |
MONDO:0014899 |
OMIM:617070 |
Orphanet:329314 |
adult-onset multiple mitochondrial DNA deletion syndrome due to DGUOK deficiency |
MONDO:0030043 |
OMIM:618885 |
- |
congenital disorder of glycosylation, type iit |
MONDO:0032599 |
OMIM:618204 |
- |
immunodeficiency 15a |
MONDO:0013580 |
OMIM:614111 |
Orphanet:765 |
pyruvate dehydrogenase E1-beta deficiency |
MONDO:8000013 |
OMIM:617068 |
- |
portal hypertension, noncirrhotic, 1 |
MONDO:0016306 |
- |
Orphanet:216972 |
Niemann-Pick disease type C, severe perinatal form |
MONDO:0017172 |
- |
Orphanet:276223 |
mucopolysaccharidosis type 6, slowly progressing |
MONDO:0030900 |
OMIM:619150 |
- |
intellectual developmental disorder with paroxysmal dyskinesia or seizures |
MONDO:0011091 |
OMIM:601472 |
Orphanet:99938 |
Charcot-Marie-Tooth disease type 2D |
MONDO:0019638 |
- |
Orphanet:93108 |
renal dysplasia |
MONDO:0015788 |
- |
Orphanet:177929 |
symptomatic form of hemophilia B in female carriers |
MONDO:0020763 |
OMIM:618332 |
- |
Menke-Hennekam syndrome 1 |
MONDO:0044303 |
OMIM:617364 |
- |
congenital heart defects and ectodermal dysplasia |
MONDO:0001561 |
- |
- |
pyloric stenosis |
MONDO:0032610 |
OMIM:618226 |
- |
mitochondrial complex 1 deficiency, nuclear type 5 |
MONDO:0007748 |
OMIM:143870 |
Orphanet:2197 |
hypercalciuria, absorptive, 2 |
MONDO:0032920 |
OMIM:618795 |
- |
juvenile arthritis due to defect in LACC1 |
MONDO:0018710 |
OMIM:617011 |
Orphanet:457359 |
megalencephaly-severe kyphoscoliosis-overgrowth syndrome |
MONDO:0014837 |
OMIM:616937 |
Orphanet:480851 |
thrombocytopenia 6 |
MONDO:0014225 |
OMIM:615517 |
Orphanet:447792 |
hemochromatosis type 5 |
MONDO:0100428 |
OMIM:211500 |
Orphanet:56965 |
progressive bulbar palsy of childhood |
MONDO:0012930 |
OMIM:612541 |
Orphanet:331176 |
autosomal recessive severe congenital neutropenia due to G6PC3 deficiency |
MONDO:0012349 |
OMIM:609813 |
Orphanet:2311 |
spondylocostal dysostosis 3, autosomal recessive |
MONDO:0014257 |
OMIM:615573 |
Orphanet:656 |
nephrotic syndrome, type 9 |
MONDO:0014189 |
OMIM:615439 |
- |
age related macular degeneration 13 |
MONDO:0017692 |
- |
Orphanet:308487 |
generalized galactose epimerase deficiency |
MONDO:0020344 |
OMIM:616720 |
Orphanet:98913 |
postsynaptic congenital myasthenic syndrome |
MONDO:0014998 |
OMIM:617272 |
- |
glaucoma 3, primary congenital, E |
MONDO:0011650 |
OMIM:606217 |
Orphanet:98722 |
atrioventricular septal defect, susceptibility to, 2 |
MONDO:0010359 |
OMIM:300555 |
Orphanet:93623 |
Dent disease type 2 |
MONDO:0018445 |
- |
Orphanet:404476 |
global developmental delay - lung cysts - overgrowth - Wilms tumor syndrome |
MONDO:0010361 |
OMIM:300558 |
Orphanet:777 |
intellectual disability, X-linked 30 |
MONDO:0019531 |
OMIM:618660 |
Orphanet:90030 |
hemolytic anemia due to glutathione reductase deficiency |
MONDO:0009607 |
OMIM:250850 |
Orphanet:168598 |
methionine adenosyltransferase deficiency |
MONDO:0008967 |
OMIM:614307 |
Orphanet:79095 |
congenital bile acid synthesis defect 4 |
MONDO:0013468 |
OMIM:613861 |
- |
retinitis pigmentosa 59 |
MONDO:0032774 |
OMIM:618479 |
- |
cerebellar, ocular, craniofacial, and genital syndrome |
MONDO:0020856 |
OMIM:618116 |
- |
bone marrow failure syndrome 4 |
MONDO:0008134 |
OMIM:610708 |
Orphanet:98673 |
autosomal dominant optic atrophy, classic form |
MONDO:0008045 |
OMIM:159950 |
Orphanet:2590 |
spinal muscular atrophy-progressive myoclonic epilepsy syndrome |
MONDO:0017884 |
OMIM:605074 |
Orphanet:47044 |
papillary renal cell carcinoma |
MONDO:0032935 |
OMIM:618821 |
- |
rhizomelic limb shortening with dysmorphic features |
MONDO:0015967 |
- |
Orphanet:183625 |
monogenic diabetes |
MONDO:0007610 |
OMIM:135400 |
Orphanet:2026 |
gingival fibromatosis-hypertrichosis syndrome |
MONDO:0032649 |
OMIM:618275 |
- |
hypotrichosis 14 |
MONDO:0014929 |
OMIM:617123 |
- |
retinitis pigmentosa 76 |
MONDO:0020603 |
OMIM:302960 |
Orphanet:35173 |
X-linked chondrodysplasia punctata 2 |
MONDO:0010532 |
OMIM:301830 |
Orphanet:1145 |
infantile-onset X-linked spinal muscular atrophy |
MONDO:0014673 |
OMIM:616509 |
Orphanet:98994 |
cataract 44 |
MONDO:0009369 |
OMIM:236750 |
Orphanet:363999 |
non-immune hydrops fetalis |
MONDO:0010298 |
OMIM:308950 |
Orphanet:510 |
Lesch-Nyhan syndrome |
MONDO:0012383 |
OMIM:609981 |
Orphanet:75391 |
primary immunodeficiency with natural-killer cell deficiency and adrenal insufficiency |
MONDO:0018129 |
- |
Orphanet:352641 |
autosomal recessive cerebellar ataxia with late-onset spasticity |
MONDO:0010150 |
OMIM:275355 |
Orphanet:67037 |
head and neck squamous cell carcinoma |
MONDO:0005272 |
- |
Orphanet:98826 |
refractory anemia |
MONDO:0010214 |
OMIM:278750 |
Orphanet:910 |
xeroderma pigmentosum variant type |
MONDO:0008464 |
OMIM:183600 |
Orphanet:2440 |
split hand-foot malformation 1 |
MONDO:0012301 |
OMIM:609560 |
Orphanet:254875 |
mitochondrial DNA depletion syndrome, myopathic form |
MONDO:0009578 |
OMIM:249400 |
Orphanet:2481 |
neurocutaneous melanocytosis |
MONDO:0012222 |
OMIM:609242 |
Orphanet:79280 |
alpha-N-acetylgalactosaminidase deficiency type 2 |
MONDO:0030897 |
OMIM:619149 |
- |
Lessel-Kreienkamp syndrome |
MONDO:0030924 |
OMIM:619175 |
- |
proteasome-associated autoinflammatory syndrome 5 |
MONDO:0014003 |
OMIM:615006 |
Orphanet:3451 |
developmental and epileptic encephalopathy, 15 |
MONDO:0009925 |
OMIM:264800 |
Orphanet:758 |
autosomal recessive inherited pseudoxanthoma elasticum |
MONDO:0032811 |
OMIM:618555 |
- |
night blindness, congenital stationary, type1i |
MONDO:0018337 |
OMIM:615595 |
Orphanet:397593 |
severe neonatal lactic acidosis due to NFS1-ISD11 complex deficiency |
MONDO:0032721 |
OMIM:618392 |
- |
spondyloepiphyseal dysplasia, kondo-fu type |
MONDO:0012714 |
OMIM:611705 |
Orphanet:289377 |
early-onset myopathy with fatal cardiomyopathy |
MONDO:0032592 |
OMIM:618189 |
- |
cardiomyopathy, dilated, 2c |
MONDO:0013505 |
OMIM:613958 |
Orphanet:399808 |
spermatogenic failure 9 |
MONDO:0007888 |
OMIM:150800 |
Orphanet:523 |
hereditary leiomyomatosis and renal cell cancer |
MONDO:0013315 |
OMIM:613582 |
Orphanet:791 |
retinitis pigmentosa 57 |
MONDO:0012803 |
OMIM:612119 |
Orphanet:103909 |
diarrhea-vomiting due to trehalase deficiency |
MONDO:0019438 |
OMIM:254500 |
Orphanet:85443 |
AL amyloidosis |
MONDO:0010486 |
OMIM:300918 |
Orphanet:659 |
Olmsted syndrome, X-linked |
MONDO:0013038 |
OMIM:612918 |
Orphanet:140944 |
CLOVES syndrome |
MONDO:0009770 |
OMIM:257920 |
Orphanet:293843 |
3MC syndrome 1 |
MONDO:0010083 |
OMIM:271980 |
Orphanet:22 |
succinic semialdehyde dehydrogenase deficiency |
MONDO:0014717 |
OMIM:616640 |
Orphanet:324290 |
early-onset Lafora body disease |
MONDO:0015085 |
OMIM:242300 |
Orphanet:100976 |
bathing suit ichthyosis |
MONDO:0012552 |
OMIM:610755 |
Orphanet:276152 |
multiple endocrine neoplasia type 4 |
MONDO:0011835 |
OMIM:613832 |
Orphanet:70595 |
sensory ataxic neuropathy, dysarthria, and ophthalmoparesis |
MONDO:0010594 |
OMIM:305690 |
- |
inherited genitourinary tract anomalies |
MONDO:0011120 |
OMIM:601634 |
Orphanet:823 |
neural tube defects, folate-sensitive |
MONDO:0032888 |
OMIM:618731 |
- |
neurodevelopmental disorder with brain anomalies and with or without vertebral or cardiac anomalies |
MONDO:0014746 |
OMIM:616721 |
Orphanet:468699 |
SLC39A8-CDG |
MONDO:0014080 |
OMIM:615198 |
Orphanet:500548 |
osteosclerotic metaphyseal dysplasia |
MONDO:0001071 |
- |
Orphanet:319658 |
intellectual disability |
MONDO:0011772 |
OMIM:607091 |
Orphanet:79332 |
B4GALT1-CDG |
MONDO:0010651 |
OMIM:309400 |
Orphanet:565 |
Menkes disease |
MONDO:0014298 |
OMIM:615668 |
Orphanet:439822 |
chromosome 5q12 deletion syndrome |
MONDO:0012382 |
OMIM:609975 |
Orphanet:71212 |
hyperinsulinemic hypoglycemia, familial, 4 |
MONDO:0013454 |
OMIM:613837 |
- |
Leber congenital amaurosis 11 |
MONDO:0010699 |
OMIM:311070 |
Orphanet:99014 |
Charcot-Marie-Tooth disease X-linked recessive 5 |
MONDO:0005044 |
OMIM:145500 |
- |
hypertensive disorder |
MONDO:0001150 |
OMIM:615219 |
Orphanet:2185 |
hydrocephalus |
MONDO:0009377 |
OMIM:237310 |
Orphanet:927 |
hyperammonemia due to N-acetylglutamate synthase deficiency |
MONDO:0011106 |
OMIM:601552 |
Orphanet:412022 |
facial dysmorphism-lens dislocation-anterior segment abnormalities-spontaneous filtering blebs syndrome |
MONDO:0030045 |
OMIM:618889 |
- |
Liberfarb syndrome |
MONDO:0014809 |
OMIM:616871 |
Orphanet:488647 |
DDX41-related hematologic malignancy predisposition syndrome |
MONDO:0006928 |
OMIM:193235 |
Orphanet:329211 |
proliferative vitreoretinopathy |
MONDO:0010909 |
OMIM:600630 |
Orphanet:178338 |
UV-sensitive syndrome 1 |
MONDO:0013231 |
OMIM:613341 |
Orphanet:791 |
Leber congenital amaurosis 14 |
MONDO:0009703 |
OMIM:255100 |
- |
myopathy with abnormal lipid metabolism |
MONDO:0014231 |
OMIM:615528 |
Orphanet:391411 |
juvenile onset Parkinson disease 19A |
MONDO:0032805 |
OMIM:618541 |
- |
hypopigmentation, organomegaly, and delayed myelination and development |
MONDO:0009806 |
OMIM:259450 |
Orphanet:2771 |
Bruck syndrome 1 |
MONDO:0054743 |
OMIM:617874 |
- |
polycystic liver disease 3 with or without kidney cysts |
MONDO:0010193 |
OMIM:277590 |
Orphanet:3447 |
Weaver syndrome |
MONDO:0015702 |
OMIM:608971 |
Orphanet:169157 |
T-B+ severe combined immunodeficiency due to CD45 deficiency |
MONDO:0009039 |
OMIM:218600 |
Orphanet:1225 |
Baller-Gerold syndrome |
MONDO:0008760 |
OMIM:203750 |
Orphanet:134 |
beta-ketothiolase deficiency |
MONDO:0054699 |
OMIM:617591 |
- |
proteasome-associated autoinflammatory syndrome 3 |
MONDO:0030058 |
OMIM:618915 |
- |
hearing loss, autosomal dominant 77 |
MONDO:0033657 |
OMIM:619071 |
- |
leukodystrophy, hypomyelinating, 20 |
MONDO:0011868 |
OMIM:607598 |
Orphanet:137783 |
lethal congenital contracture syndrome 2 |
MONDO:0009115 |
OMIM:223000 |
Orphanet:53690 |
congenital lactase deficiency |
MONDO:0011688 |
OMIM:606612 |
Orphanet:52428 |
muscular dystrophy-dystroglycanopathy type B5 |
MONDO:0010791 |
OMIM:550500 |
Orphanet:99845 |
myoglobinuria, recurrent |
MONDO:0011570 |
OMIM:605589 |
Orphanet:101101 |
Charcot-Marie-Tooth disease type 2B2 |
MONDO:0014151 |
OMIM:615371 |
- |
pulmonary hypertension, neonatal, susceptibility to |
MONDO:0030866 |
OMIM:619121 |
- |
neurodevelopmental disorder with cardiomyopathy, spasticity, and brain abnormalities |
MONDO:0024457 |
OMIM:610217 |
Orphanet:35069 |
neurodegeneration with brain iron accumulation 2A |
MONDO:0013117 |
OMIM:613077 |
Orphanet:254892 |
progressive external ophthalmoplegia with mitochondrial DNA deletions, autosomal dominant 5 |
MONDO:0024288 |
- |
- |
hyperbilirubinemia |
MONDO:0010200 |
OMIM:277900 |
Orphanet:905 |
Wilson disease |
MONDO:0014050 |
OMIM:615113 |
Orphanet:2542 |
isolated microphthalmia 8 |
MONDO:0010689 |
OMIM:310490 |
Orphanet:101078 |
Charcot-Marie-Tooth disease X-linked recessive 4 |
MONDO:0032794 |
OMIM:618513 |
- |
leber congenital amaurosis 19 |
MONDO:0012845 |
OMIM:612278 |
- |
inflammatory bowel disease 19 |
MONDO:0010543 |
OMIM:302060 |
Orphanet:111 |
Barth syndrome |
MONDO:0013116 |
OMIM:613076 |
Orphanet:330054 |
congenital cataract-progressive muscular hypotonia-hearing loss-developmental delay syndrome |
MONDO:0009998 |
OMIM:268305 |
Orphanet:3102 |
Richieri Costa-Pereira syndrome |
MONDO:0020681 |
OMIM:601776 |
- |
Ehlers-Danlos syndrome, musculocontractural type 1 |
MONDO:0005148 |
OMIM:616087 |
- |
type 2 diabetes mellitus |
MONDO:0013898 |
OMIM:614817 |
Orphanet:401996 |
karyomegalic interstitial nephritis |
MONDO:0060759 |
OMIM:618088 |
Orphanet:597623 |
neurodevelopmental disorder with regression, abnormal movements, loss of speech, and seizures |
MONDO:0009026 |
OMIM:218040 |
Orphanet:3071 |
Costello syndrome |
MONDO:0012764 |
OMIM:611943 |
Orphanet:420741 |
RIDDLE syndrome |
MONDO:0016642 |
OMIM:606190 |
Orphanet:2495 |
meningioma |
MONDO:0011806 |
OMIM:609143 |
Orphanet:488265 |
osteofibrous dysplasia |
MONDO:0001044 |
- |
- |
esophageal atresia |
MONDO:0014735 |
OMIM:616687 |
Orphanet:435387 |
Charcot-Marie-Tooth disease type 2Y |
MONDO:0010943 |
OMIM:600850 |
- |
schizophrenia 4 |
MONDO:0008171 |
OMIM:605990 |
- |
nephrolithiasis |
MONDO:0007893 |
OMIM:613707 |
Orphanet:500 |
Noonan syndrome with multiple lentigines |
MONDO:0019157 |
- |
Orphanet:75564 |
acquired idiopathic sideroblastic anemia |
MONDO:0019666 |
OMIM:612847 |
Orphanet:93282 |
spondyloepimetaphyseal dysplasia, PAPSS2 type |
MONDO:0005392 |
- |
- |
scoliosis |
MONDO:0013941 |
OMIM:614875 |
Orphanet:99646 |
metaphyseal chondromatosis with D-2-hydroxyglutaric aciduria |
MONDO:0007892 |
OMIM:151050 |
Orphanet:2658 |
Lenz-Majewski hyperostotic dwarfism |
MONDO:0007844 |
OMIM:147950 |
- |
hypogonadotropic hypogonadism 2 with or without anosmia |
MONDO:0014687 |
OMIM:616544 |
- |
retinitis pigmentosa 73 |
MONDO:0100003 |
OMIM:300909 |
- |
susceptibility to angioedema induced by ACE inhibitors |
MONDO:0012570 |
OMIM:610842 |
Orphanet:91135 |
body skin hyperlaxity due to vitamin K-dependent coagulation factor deficiency |
MONDO:0009306 |
OMIM:233650 |
Orphanet:157949 |
combined immunodeficiency with skin granulomas |
MONDO:0009376 |
OMIM:237300 |
Orphanet:147 |
carbamoyl phosphate synthetase I deficiency disease |
MONDO:0013869 |
OMIM:614723 |
Orphanet:976 |
adenine phosphoribosyltransferase deficiency |
MONDO:0013605 |
OMIM:614170 |
Orphanet:90354 |
brittle cornea syndrome 2 |
MONDO:0100133 |
- |
Orphanet:2609 |
mitochondrial complex I deficiency |
MONDO:0100215 |
OMIM:618007 |
Orphanet:178506 |
Rajab interstitial lung disease with brain calcifications 1 |
MONDO:0018997 |
OMIM:616564 |
Orphanet:648 |
Noonan syndrome |
MONDO:0012235 |
OMIM:609270 |
Orphanet:284324 |
autosomal recessive spinocerebellar ataxia 7 |
MONDO:0015353 |
OMIM:600794 |
Orphanet:139536 |
neuronopathy, distal hereditary motor, type 5A |
MONDO:0032798 |
OMIM:618527 |
- |
ichthyotic keratoderma, spasticity, hypomyelination, and dysmorphic facial features |
MONDO:0014017 |
OMIM:615032 |
- |
autism, susceptibility to, 18 |
MONDO:0020743 |
- |
Orphanet:530995 |
mixed phenotype acute leukemia |
MONDO:0017691 |
- |
Orphanet:308473 |
erythrocyte galactose epimerase deficiency |
MONDO:0032851 |
OMIM:618653 |
- |
intellectual developmental disorder with impaired language and dysmorphic facies |
MONDO:0007874 |
OMIM:150230 |
Orphanet:502 |
trichorhinophalangeal syndrome type II |
MONDO:0013999 |
OMIM:614979 |
Orphanet:313800 |
optic nerve edema-splenomegaly syndrome |
MONDO:0007726 |
OMIM:142669 |
Orphanet:2114 |
hip dysplasia, Beukes type |
MONDO:0008104 |
OMIM:163950 |
Orphanet:648 |
Noonan syndrome 1 |
MONDO:0008243 |
OMIM:172700 |
Orphanet:282 |
Pick disease |
MONDO:0032571 |
OMIM:618162 |
- |
spondyloepimetaphyseal dysplasia, Krakow type |
MONDO:0019597 |
OMIM:202110 |
Orphanet:90796 |
46,XY disorder of sex development due to isolated 17,20-lyase deficiency |
MONDO:0010378 |
OMIM:300614 |
Orphanet:139583 |
X-linked hereditary sensory and autonomic neuropathy with hearing loss |
MONDO:0011329 |
- |
- |
obsolete cerebral palsy, spastic quadriplegic, 1 |
MONDO:0013429 |
OMIM:613801 |
- |
retinitis pigmentosa 40 |
MONDO:0007236 |
OMIM:113650 |
Orphanet:107 |
branchiootorenal syndrome 1 |
MONDO:0013113 |
OMIM:613073 |
Orphanet:1040 |
metaphyseal anadysplasia 2 |
MONDO:0012205 |
OMIM:609161 |
- |
autosomal dominant striatal neurodegeneration type 1 |
MONDO:0018914 |
OMIM:615885 |
Orphanet:55654 |
hypotrichosis simplex |
MONDO:0010178 |
OMIM:277180 |
Orphanet:48 |
congenital bilateral aplasia of vas deferens from CFTR mutation |