MONDO:0008967 |
AMACR |
Q9UHK6 |
5.1.99.4
|
R-HSA-9033241
R-HSA-389887
R-HSA-389887
Reactome Name: Beta-oxidation of pristanoyl-CoA
See in Reactome
R-HSA-193368
R-HSA-193368
Reactome Name: Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol
See in Reactome
R-HSA-193775
R-HSA-193775
Reactome Name: Synthesis of bile acids and bile salts via 24-hydroxycholesterol
See in Reactome
|
R-HSA-194068
R-HSA-194068
Reactome Name: Bile acid and bile salt metabolism
See in Reactome
R-HSA-9609507
R-HSA-390918
R-HSA-1430728
R-HSA-8978868
R-HSA-192105
R-HSA-192105
Reactome Name: Synthesis of bile acids and bile salts
See in Reactome
R-HSA-556833
R-HSA-8957322
|
Protein localization
Metabolism
|
R-HSA-192056
(
R-HSA-193368
)
R-HSA-192056
Reaction Name: Isomerization of 25(R) THCA-CoA to 25(S) THCA-CoA
See in Reactome
R-HSA-193452
(
R-HSA-193368
)
R-HSA-193452
Reaction Name: Isomerization of 25(R) DHCA-CoA to 25(S) DHCA-CoA
See in Reactome
R-HSA-193736
(
R-HSA-193775
)
R-HSA-193736
Reaction Name: Isomerization of 3,7,24THCA-CoA to (24R, 25R) 3alpha,7alpha,24-trihydroxy-5beta-cholestanoyl-CoA
See in Reactome
R-HSA-193763
(
R-HSA-193775
)
R-HSA-193763
Reaction Name: Isomerization of 25(R) TetraHCA-CoA to (24R, 25R) 3alpha,7alpha,12alpha,24-tetrahydroxy-5beta-cholestanoyl-CoA
See in Reactome
R-HSA-389897
(
R-HSA-389887
)
R-HSA-389897
Reaction Name: Isomerization of (2R)-pristanoyl-CoA to (2S)-pristanoyl-CoA
See in Reactome
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
Reaction Name: PEX5S,L binds cargo proteins containing PTS1
See in Reactome
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
Reaction Name: Cargo of PEX5S,L translocates from the cytosol to the peroxisomal matrix
See in Reactome
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
Reaction Name: PEX5S,L:Cargo binds PEX13:PEX14:PEX2:PEX10:PEX12 (Docking and Translocation Module)
See in Reactome
|
MONDO:0009300 |
HSD17B4 |
P51659 |
1.1.1.n12
4.2.1.119
4.2.1.107
|
R-HSA-389887
R-HSA-389887
Reactome Name: Beta-oxidation of pristanoyl-CoA
See in Reactome
R-HSA-193368
R-HSA-193368
Reactome Name: Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol
See in Reactome
R-HSA-2046106
R-HSA-2046106
Reactome Name: alpha-linolenic acid (ALA) metabolism
See in Reactome
R-HSA-390247
R-HSA-390247
Reactome Name: Beta-oxidation of very long chain fatty acids
See in Reactome
R-HSA-9033500
R-HSA-9033500
Reactome Name: TYSND1 cleaves peroxisomal proteins
See in Reactome
R-HSA-9033241
|
R-HSA-194068
R-HSA-194068
Reactome Name: Bile acid and bile salt metabolism
See in Reactome
R-HSA-9609507
R-HSA-390918
R-HSA-2046104
R-HSA-2046104
Reactome Name: alpha-linolenic (omega3) and linoleic (omega6) acid metabolism
See in Reactome
R-HSA-1430728
R-HSA-8978868
R-HSA-192105
R-HSA-192105
Reactome Name: Synthesis of bile acids and bile salts
See in Reactome
R-HSA-556833
R-HSA-8957322
|
Protein localization
Metabolism
|
R-HSA-192331
(
R-HSA-193368
)
R-HSA-192331
Reaction Name: 3alpha,7alpha,12alpha-trihydroxy-5beta-cholest-24-enoyl-CoA (THCA-CoA) is hydrated to (24R, 25R) 3alpha,7alpha,12alpha,24-tetrahydroxy-5beta-cholestanoyl-CoA
See in Reactome
R-HSA-193455
(
R-HSA-193368
)
R-HSA-193455
Reaction Name: (24R, 25R) 3alpha,7alpha,12alpha,24-tetrahydroxy-5beta-cholestanoyl-CoA is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholest-24-one-CoA
See in Reactome
R-HSA-193508
(
R-HSA-193368
)
R-HSA-193508
Reaction Name: (24R, 25R) 3alpha,7alpha,24-trihydroxy-5beta-cholestanoyl-CoA is oxidized to 3alpha,7alpha-dihydroxy-5beta-cholest-24-one-CoA
See in Reactome
R-HSA-193535
(
R-HSA-193368
)
R-HSA-193535
Reaction Name: 25(S) 3alpha,7alpha-dihydroxy-5beta-cholest-24-enoyl-CoA is hydrated to (24R, 25R) 3alpha,7alpha,24-trihydroxy-5beta-cholestanoyl-CoA
See in Reactome
R-HSA-2066778
(
R-HSA-2046106
)
R-HSA-2066778
Reaction Name: Hydration of delta2-tetracosaheptaenoyl-CoA to 3-hydroxy tetracosahexaenoyl-CoA
See in Reactome
R-HSA-2066780
(
R-HSA-2046106
)
R-HSA-2066780
Reaction Name: Dehydrogenation of 3-hydroxy tetracosahexaenoyl-CoA
See in Reactome
R-HSA-389986
(
R-HSA-389887
)
R-HSA-389986
Reaction Name: trans-2,3-dehydropristanoyl-CoA + H2O => 3-hydroxypristanoyl-CoA
See in Reactome
R-HSA-389995
(
R-HSA-389887
)
R-HSA-389995
Reaction Name: 3-hydroxypristanoyl-CoA + NAD+ => 3-ketoxypristanoyl-CoA + NADH + H+
See in Reactome
R-HSA-390251
(
R-HSA-390247
)
R-HSA-390251
Reaction Name: HSD17B4 dehydrogenates 3-hydroxyhexacosanoyl-CoA
See in Reactome
R-HSA-390252
(
R-HSA-390247
)
R-HSA-390252
Reaction Name: HSD17B4 hydrates trans-2,3-dehydrohexacosanoyl-CoA
See in Reactome
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
Reaction Name: PEX5S,L binds cargo proteins containing PTS1
See in Reactome
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
Reaction Name: Cargo of PEX5S,L translocates from the cytosol to the peroxisomal matrix
See in Reactome
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
Reaction Name: PEX5S,L:Cargo binds PEX13:PEX14:PEX2:PEX10:PEX12 (Docking and Translocation Module)
See in Reactome
R-HSA-9033530
(
R-HSA-9033241;
R-HSA-9033500
)
|
MONDO:0009855 |
HSD17B4 |
P51659 |
1.1.1.n12
4.2.1.119
4.2.1.107
|
R-HSA-389887
R-HSA-389887
Reactome Name: Beta-oxidation of pristanoyl-CoA
See in Reactome
R-HSA-193368
R-HSA-193368
Reactome Name: Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol
See in Reactome
R-HSA-2046106
R-HSA-2046106
Reactome Name: alpha-linolenic acid (ALA) metabolism
See in Reactome
R-HSA-390247
R-HSA-390247
Reactome Name: Beta-oxidation of very long chain fatty acids
See in Reactome
R-HSA-9033500
R-HSA-9033500
Reactome Name: TYSND1 cleaves peroxisomal proteins
See in Reactome
R-HSA-9033241
|
R-HSA-194068
R-HSA-194068
Reactome Name: Bile acid and bile salt metabolism
See in Reactome
R-HSA-9609507
R-HSA-390918
R-HSA-2046104
R-HSA-2046104
Reactome Name: alpha-linolenic (omega3) and linoleic (omega6) acid metabolism
See in Reactome
R-HSA-1430728
R-HSA-8978868
R-HSA-192105
R-HSA-192105
Reactome Name: Synthesis of bile acids and bile salts
See in Reactome
R-HSA-556833
R-HSA-8957322
|
Protein localization
Metabolism
|
R-HSA-192331
(
R-HSA-193368
)
R-HSA-192331
Reaction Name: 3alpha,7alpha,12alpha-trihydroxy-5beta-cholest-24-enoyl-CoA (THCA-CoA) is hydrated to (24R, 25R) 3alpha,7alpha,12alpha,24-tetrahydroxy-5beta-cholestanoyl-CoA
See in Reactome
R-HSA-193455
(
R-HSA-193368
)
R-HSA-193455
Reaction Name: (24R, 25R) 3alpha,7alpha,12alpha,24-tetrahydroxy-5beta-cholestanoyl-CoA is oxidized to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholest-24-one-CoA
See in Reactome
R-HSA-193508
(
R-HSA-193368
)
R-HSA-193508
Reaction Name: (24R, 25R) 3alpha,7alpha,24-trihydroxy-5beta-cholestanoyl-CoA is oxidized to 3alpha,7alpha-dihydroxy-5beta-cholest-24-one-CoA
See in Reactome
R-HSA-193535
(
R-HSA-193368
)
R-HSA-193535
Reaction Name: 25(S) 3alpha,7alpha-dihydroxy-5beta-cholest-24-enoyl-CoA is hydrated to (24R, 25R) 3alpha,7alpha,24-trihydroxy-5beta-cholestanoyl-CoA
See in Reactome
R-HSA-2066778
(
R-HSA-2046106
)
R-HSA-2066778
Reaction Name: Hydration of delta2-tetracosaheptaenoyl-CoA to 3-hydroxy tetracosahexaenoyl-CoA
See in Reactome
R-HSA-2066780
(
R-HSA-2046106
)
R-HSA-2066780
Reaction Name: Dehydrogenation of 3-hydroxy tetracosahexaenoyl-CoA
See in Reactome
R-HSA-389986
(
R-HSA-389887
)
R-HSA-389986
Reaction Name: trans-2,3-dehydropristanoyl-CoA + H2O => 3-hydroxypristanoyl-CoA
See in Reactome
R-HSA-389995
(
R-HSA-389887
)
R-HSA-389995
Reaction Name: 3-hydroxypristanoyl-CoA + NAD+ => 3-ketoxypristanoyl-CoA + NADH + H+
See in Reactome
R-HSA-390251
(
R-HSA-390247
)
R-HSA-390251
Reaction Name: HSD17B4 dehydrogenates 3-hydroxyhexacosanoyl-CoA
See in Reactome
R-HSA-390252
(
R-HSA-390247
)
R-HSA-390252
Reaction Name: HSD17B4 hydrates trans-2,3-dehydrohexacosanoyl-CoA
See in Reactome
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
Reaction Name: PEX5S,L binds cargo proteins containing PTS1
See in Reactome
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
Reaction Name: Cargo of PEX5S,L translocates from the cytosol to the peroxisomal matrix
See in Reactome
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
Reaction Name: PEX5S,L:Cargo binds PEX13:PEX14:PEX2:PEX10:PEX12 (Docking and Translocation Module)
See in Reactome
R-HSA-9033530
(
R-HSA-9033241;
R-HSA-9033500
)
|
MONDO:0013391 |
SCP2 |
P22307 |
2.3.1.176
2.3.1.16
2.3.1.155
|
R-HSA-2046106
R-HSA-2046106
Reactome Name: alpha-linolenic acid (ALA) metabolism
See in Reactome
R-HSA-389887
R-HSA-389887
Reactome Name: Beta-oxidation of pristanoyl-CoA
See in Reactome
R-HSA-193368
R-HSA-193368
Reactome Name: Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol
See in Reactome
R-HSA-9033241
R-HSA-9033500
R-HSA-9033500
Reactome Name: TYSND1 cleaves peroxisomal proteins
See in Reactome
|
R-HSA-194068
R-HSA-194068
Reactome Name: Bile acid and bile salt metabolism
See in Reactome
R-HSA-9609507
R-HSA-390918
R-HSA-2046104
R-HSA-2046104
Reactome Name: alpha-linolenic (omega3) and linoleic (omega6) acid metabolism
See in Reactome
R-HSA-1430728
R-HSA-8978868
R-HSA-192105
R-HSA-192105
Reactome Name: Synthesis of bile acids and bile salts
See in Reactome
R-HSA-556833
R-HSA-8957322
|
Protein localization
Metabolism
|
R-HSA-2066781
(
R-HSA-2046106
)
R-HSA-2066781
Reaction Name: Formation of DHA-CoA catalysed by sterol carrier protein X (SCPx)
See in Reactome
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
Reaction Name: PEX5S,L binds cargo proteins containing PTS1
See in Reactome
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
Reaction Name: Cargo of PEX5S,L translocates from the cytosol to the peroxisomal matrix
See in Reactome
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
Reaction Name: PEX5S,L:Cargo binds PEX13:PEX14:PEX2:PEX10:PEX12 (Docking and Translocation Module)
See in Reactome
R-HSA-9033524
(
R-HSA-9033241;
R-HSA-9033500
)
|
MONDO:0015015 |
ACOX2 |
Q99424 |
1.17.99.3
|
R-HSA-9033241
R-HSA-389887
R-HSA-389887
Reactome Name: Beta-oxidation of pristanoyl-CoA
See in Reactome
R-HSA-193368
R-HSA-193368
Reactome Name: Synthesis of bile acids and bile salts via 7alpha-hydroxycholesterol
See in Reactome
|
R-HSA-194068
R-HSA-194068
Reactome Name: Bile acid and bile salt metabolism
See in Reactome
R-HSA-9609507
R-HSA-390918
R-HSA-1430728
R-HSA-8978868
R-HSA-192105
R-HSA-192105
Reactome Name: Synthesis of bile acids and bile salts
See in Reactome
R-HSA-556833
R-HSA-8957322
|
Protein localization
Metabolism
|
R-HSA-192335
(
R-HSA-193368
)
R-HSA-192335
Reaction Name: 25(S) THCA-CoA is dehydrogenated to 3alpha,7alpha,12alpha-trihydroxy-5beta-cholest-24-enoyl-CoA (THCA-CoA)
See in Reactome
R-HSA-193369
(
R-HSA-193368
)
R-HSA-193369
Reaction Name: 25(S) DHCA-CoA is dehydrogenated to 25(S) 3alpha,7alpha-dihydroxy-5beta-cholest-24-enoyl-CoA
See in Reactome
R-HSA-389889
(
R-HSA-389887
)
R-HSA-389889
Reaction Name: ACOX2:FAD, ACOXL:FAD oxidise (2S)-pristanoyl-CoA to trans-2,3-dehydropristanoyl-CoA
See in Reactome
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
Reaction Name: PEX5S,L binds cargo proteins containing PTS1
See in Reactome
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
Reaction Name: Cargo of PEX5S,L translocates from the cytosol to the peroxisomal matrix
See in Reactome
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
Reaction Name: PEX5S,L:Cargo binds PEX13:PEX14:PEX2:PEX10:PEX12 (Docking and Translocation Module)
See in Reactome
|
MONDO:0054764 |
CRAT |
P43155 |
2.3.1.137
2.3.1.7
|
R-HSA-9033241
R-HSA-389887
R-HSA-389887
Reactome Name: Beta-oxidation of pristanoyl-CoA
See in Reactome
|
R-HSA-556833
R-HSA-1430728
R-HSA-390918
R-HSA-9609507
R-HSA-8978868
|
Metabolism
Protein localization
|
R-HSA-390284
(
R-HSA-389887
)
R-HSA-390284
Reaction Name: propionyl-CoA + carnitine => propionylcarnitine + CoASH
See in Reactome
R-HSA-390291
(
R-HSA-389887
)
R-HSA-390291
Reaction Name: acetyl-CoA + carnitine => acetylcarnitine + CoASH
See in Reactome
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
(
R-HSA-9033241
)
R-HSA-9033233
Reaction Name: PEX5S,L binds cargo proteins containing PTS1
See in Reactome
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
(
R-HSA-9033241
)
R-HSA-9033235
Reaction Name: Cargo of PEX5S,L translocates from the cytosol to the peroxisomal matrix
See in Reactome
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
(
R-HSA-9033241
)
R-HSA-9033236
Reaction Name: PEX5S,L:Cargo binds PEX13:PEX14:PEX2:PEX10:PEX12 (Docking and Translocation Module)
See in Reactome
|